{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,26]],"date-time":"2025-10-26T21:03:46Z","timestamp":1761512626426},"reference-count":17,"publisher":"Oxford University Press (OUP)","issue":"786","license":[{"start":{"date-parts":[[1991,4,1]],"date-time":"1991-04-01T00:00:00Z","timestamp":670464000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/pages\/standard-publication-reuse-rights"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[1991,4,1]]},"abstract":"<jats:title>Summary<\/jats:title>\n               <jats:p>A 19 year old Mauritian male presented with episodic nausea, abdominal discomfort and jaundice. Unconjugated hyperbilirubinaemia and erythroid hyperplasia without dyserythropoiesis led to the diagnosis of primary shunt hyperbilirubinaemia. The similarity between congenital dyserythropoietic anaemia and this entity suggests that patients with these lesions can be considered within a single spectrum of disorders, characterized as congenital ineffective erythropoiesis.<\/jats:p>","DOI":"10.1136\/pgmj.67.786.396","type":"journal-article","created":{"date-parts":[[2008,12,29]],"date-time":"2008-12-29T21:01:03Z","timestamp":1230584463000},"page":"396-398","source":"Crossref","is-referenced-by-count":10,"title":["Primary shunt hyperbilirubinaemia: a variant of the congenital dyserythropoietic anaemias"],"prefix":"10.1093","volume":"67","author":[{"given":"A R","family":"Bird","sequence":"first","affiliation":[{"name":"University of Cape Town Leukaemia Centre and Department of Haematology, Groote Schuur Hospital, Observatory , Cape, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E","family":"Knottenbelt","sequence":"additional","affiliation":[{"name":"University of Cape Town Leukaemia Centre and Department of Haematology, Groote Schuur Hospital, Observatory , Cape, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P","family":"Jacobs","sequence":"additional","affiliation":[{"name":"University of Cape Town Leukaemia Centre and Department of Haematology, Groote Schuur Hospital, Observatory , Cape, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J","family":"Maigrot","sequence":"additional","affiliation":[{"name":"Rue Lees, Curepipe, Mauritius"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[1991,4,1]]},"reference":[{"key":"ref_1","first-page":"1","article-title":"The bilirubin shunt and shunt hyperbilirubinemia","volume-title":"Progress in Liver Disease. 11. Grune and Stratton, Inc","author":"Israels, L.G.","year":"1970","unstructured":"Israels, L.G. The bilirubin shunt and shunt hyperbilirubinemia. In: Popper, H. & Schaffner, F (eds). Progress in Liver Disease. 11. Grune and Stratton, Inc., New York, 1970, pp. 1-12."},{"key":"ref_2","first-page":"99","article-title":"Dyserythropoiesis and dyserythropoietic anemias","volume-title":"Progress in Hematology","author":"Lewis, S.M.; Verwilghen, R.L.","year":"1973","unstructured":"Lewis, S.M. & Verwilghen, R.L. Dyserythropoiesis and dyserythropoietic anemias. In: Brown, E.B. (ed.) Progress in Hematology 1973, pp. 99-129."},{"key":"ref_3","doi-asserted-by":"crossref","first-page":"210","DOI":"10.1016\/S0022-3476(75)80581-6","article-title":"Congenital dyserythropoietic anemia-type IV","volume":"87","author":"Benjamin, J.T.; Rosse, W.F.; Daldorf, F.G.; McMillan, C.W.","year":"1975","unstructured":"Benjamin, J.T., Rosse, W.F., Daldorf, F.G. & McMillan, C.W. Congenital dyserythropoietic anemia-type IV. J Pediatr 1975, 87: 210-216.","journal-title":"J Pediatr"},{"key":"ref_4","doi-asserted-by":"crossref","first-page":"184","DOI":"10.1136\/jcp.30.2.184","article-title":"Congenital dyserythropoietic anaemia: response to splenectomy and quantitation of ineffective erythropoiesis","volume":"30","author":"Samson, D.; Halliday, D.; Chanarin, I.","year":"1977","unstructured":"Samson, D., Halliday, D. & Chanarin, I. Congenital dyserythropoietic anaemia: response to splenectomy and quantitation of ineffective erythropoiesis. J Clin Pathol 1977, 30: 184-190.","journal-title":"J Clin Pathol"},{"key":"ref_5","doi-asserted-by":"crossref","first-page":"537","DOI":"10.1111\/j.1365-2141.1978.tb03623.x","article-title":"A new type of congenital dyserythropoietic anaemia","volume":"39","author":"Sansone, G.","year":"1978","unstructured":"Sansone, G. A new type of congenital dyserythropoietic anaemia. 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