{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,11]],"date-time":"2025-09-11T17:52:15Z","timestamp":1757613135322,"version":"3.44.0"},"reference-count":15,"publisher":"BMJ","issue":"4","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["Pract Neurol"],"accepted":{"date-parts":[[2024,2,14]]},"published-print":{"date-parts":[[2024,8]]},"abstract":"<jats:p>Paroxysmal dysarthria ataxia syndrome presents with recurrent, brief, stereotyped events of dysarthria, limb clumsiness, unsteady gait and vertigo or dizziness that can occur in association with lesions in the midbrain. We describe a case of a woman presenting with paroxysmal dysarthria and ataxia secondary to a midbrain lesion, treated successfully with carbamazepine.<\/jats:p>","DOI":"10.1136\/pn-2023-004023","type":"journal-article","created":{"date-parts":[[2024,2,29]],"date-time":"2024-02-29T13:20:29Z","timestamp":1709212829000},"page":"310-312","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Paroxysmal dysarthria-ataxia syndrome"],"prefix":"10.1136","volume":"24","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-7793-271X","authenticated-orcid":false,"given":"Marija","family":"Cauchi","sequence":"first","affiliation":[{"name":"Department of Neurosciences, Mater Dei Hospital, Msida, Malta"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Janice","family":"Abela","sequence":"additional","affiliation":[{"name":"Department of Medicine, Mater Dei Hospital, Msida, Malta"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nicola","family":"Dingli","sequence":"additional","affiliation":[{"name":"Department of Neurosciences, Mater Dei Hospital, Msida, Malta"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Norbert","family":"Vella","sequence":"additional","affiliation":[{"name":"Department of Neurosciences, Mater Dei Hospital, Msida, Malta"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2024,2,29]]},"reference":[{"key":"2025090411170713000_24.4.310.1","first-page":"643","article-title":"Periodic ataxia","volume":"36","author":"Parker","year":"1946","journal-title":"Collect Pap Mayo Clin"},{"key":"2025090411170713000_24.4.310.2","doi-asserted-by":"crossref","first-page":"381","DOI":"10.1016\/j.jocn.2021.05.038","article-title":"Neuroinflammation preceding primary central nervous system lymphoma (PCNSL) \u2013 case reports and literature review","volume":"89","author":"Norrington","year":"2021","journal-title":"J Clin Neurosci"},{"key":"2025090411170713000_24.4.310.3","doi-asserted-by":"crossref","first-page":"345","DOI":"10.1212\/01.WNL.0000130252.69304.D2","article-title":"Paroxysmal dysarthria and ataxia after midbrain infarction","volume":"63","author":"Matsui","year":"2004","journal-title":"Neurology"},{"key":"2025090411170713000_24.4.310.4","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/98.2.189"},{"key":"2025090411170713000_24.4.310.5","doi-asserted-by":"crossref","first-page":"1369","DOI":"10.1007\/s00415-010-5534-3","article-title":"Symptomatic paroxysmal dysarthria-ataxia in demyelinating diseases","volume":"257","author":"Marcel","year":"2010","journal-title":"J Neurol"},{"key":"2025090411170713000_24.4.310.6","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.0b013e31827dec0f"},{"key":"2025090411170713000_24.4.310.7","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1016\/j.jns.2015.01.023","article-title":"Paroxysmal dysarthria-ataxia syndrome resolving after fingolimod treatment","volume":"350","author":"Rossi","year":"2015","journal-title":"J Neurol Sci"},{"key":"2025090411170713000_24.4.310.8","doi-asserted-by":"publisher","DOI":"10.1007\/BF00878879"},{"key":"2025090411170713000_24.4.310.9","doi-asserted-by":"crossref","first-page":"e2727","DOI":"10.1212\/WNL.0000000000007619","article-title":"Pearls & oy-sters: paroxysmal dysarthria-ataxia syndrome: acoustic analysis in a case of antiphospholipid syndrome","volume":"92","author":"Gessani","year":"2019","journal-title":"Neurology"},{"key":"2025090411170713000_24.4.310.10","doi-asserted-by":"crossref","DOI":"10.1136\/bcr-2013-200777","article-title":"Isolated paroxysmal dysarthria caused by a single demyelinating midbrain lesion","volume":"2013","author":"Codeluppi","year":"2013","journal-title":"BMJ Case Rep"},{"key":"2025090411170713000_24.4.310.11","doi-asserted-by":"crossref","first-page":"273","DOI":"10.1007\/s00415-010-5748-4","article-title":"Paroxysmal dysarthria and ataxia in multiple sclerosis and corresponding magnetic resonance imaging findings","volume":"258","author":"Li","year":"2011","journal-title":"J Neurol"},{"key":"2025090411170713000_24.4.310.12","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.38.2.191"},{"key":"2025090411170713000_24.4.310.13","doi-asserted-by":"crossref","first-page":"1349","DOI":"10.1007\/s00415-011-5901-8","article-title":"Lamotrigine therapy for paroxysmal dysarthria caused by multiple sclerosis: a case report","volume":"258","author":"Valentino","year":"2011","journal-title":"J Neurol"},{"key":"2025090411170713000_24.4.310.14","doi-asserted-by":"publisher","DOI":"10.1177\/1352458514546792"},{"key":"2025090411170713000_24.4.310.15","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1016\/j.msard.2016.09.003","article-title":"Successful treatment of paroxysmal ataxia and dysarthria in multiple sclerosis with levetiracetam","volume":"10","author":"Goodwin","year":"2016","journal-title":"Mult Scler Relat Disord"}],"container-title":["Practical Neurology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/pn-2023-004023","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,9,4]],"date-time":"2025-09-04T18:21:26Z","timestamp":1757010086000},"score":1,"resource":{"primary":{"URL":"https:\/\/pn.bmj.com\/lookup\/doi\/10.1136\/pn-2023-004023"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,2,29]]},"references-count":15,"journal-issue":{"issue":"4","published-online":{"date-parts":[[2024,7,16]]},"published-print":{"date-parts":[[2024,8]]}},"alternative-id":["10.1136\/pn-2023-004023"],"URL":"https:\/\/doi.org\/10.1136\/pn-2023-004023","relation":{},"ISSN":["1474-7758","1474-7766"],"issn-type":[{"type":"print","value":"1474-7758"},{"type":"electronic","value":"1474-7766"}],"subject":[],"published":{"date-parts":[[2024,2,29]]}}}