{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,4]],"date-time":"2026-11-04T22:22:51Z","timestamp":1793830971684,"version":"4.6.1"},"reference-count":25,"publisher":"BMJ","issue":"1","license":[{"start":{"date-parts":[[2024,2,29]],"date-time":"2024-02-29T00:00:00Z","timestamp":1709164800000},"content-version":"unspecified","delay-in-days":28,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["RMD Open"],"accepted":{"date-parts":[[2024,2,12]]},"published-print":{"date-parts":[[2024,2]]},"abstract":"<jats:sec>\n                  <jats:title>Objective<\/jats:title>\n                  <jats:p>Although airway disease associated with Sj\u00f6gren\u2019s disease (Sjo-AD) is common, it is poorly studied compared with interstitial lung disease (ILD). In this study, we aimed to assess factors associated with Sjo-AD, the characteristics and prognosis of this manifestation.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Methods<\/jats:title>\n                  <jats:p>We performed a retrospective multicentric study involving nine centres. We included Sjo-AD patients confirmed by at least one clinician and one CT scan report. Clinical and biological data, pulmonary function test (PFT), and CT scans were collected. A single radiologist specialist in thoracic diseases reviewed CT scans. Sjo-AD patients were compared with Sjo controls without pulmonary involvement, randomly selected after matching for age and disease duration.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Results<\/jats:title>\n                  <jats:p>We included 31 Sjo-AD and 62 Sjo controls without pulmonary history. Sjo-AD had a higher disease activity (ESSDAI) compared with controls, even when excluding the pulmonary domain of the score (7 vs 3.8, p&lt;0.05), mainly due to the biological activity. Sjo-AD was multilobar (72%) and associated with signs of both bronchiectasis and bronchiolitis (60%). Obstructive lung disease occurred in 32% at the time of Sjo-AD diagnosis. Overall, PFT was stable after 8.7\u00b17 years follow-up but repeated CT scans showed extended lesions in 41% of cases within 6\u00b13.2 years. No patient developed Sjo-ILD. Sjo-AD progression was independent of the global disease activity.<\/jats:p>\n               <\/jats:sec>\n               <jats:sec>\n                  <jats:title>Conclusions<\/jats:title>\n                  <jats:p>Sjo-AD preferentially affects Sjo patients with higher biological activity. It is often characterised as a diffuse disease, affecting both proximal and distal airways, with a slow evolution over time and no progression to Sjo-ILD.<\/jats:p>\n               <\/jats:sec>","DOI":"10.1136\/rmdopen-2023-003866","type":"journal-article","created":{"date-parts":[[2024,2,29]],"date-time":"2024-02-29T23:15:16Z","timestamp":1709248516000},"page":"e003866","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":6,"title":["Characterisation of airway disease associated with Sj\u00f6gren disease"],"prefix":"10.1136","volume":"10","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6322-8801","authenticated-orcid":false,"given":"Lo\u00efc","family":"Meudec","sequence":"first","affiliation":[{"name":"Department of Rheumatology, Universit\u00e9 Paris-Saclay, H\u00f4pital Bic\u00eatre, Assistance Publique-H\u00f4pitaux de Paris, Le Kremlin Bic\u00eatre, France"},{"name":"Center for Immunology of Viral Infections and Auto-immune Diseases (IMVA), INSERM UMR 1184, Universit\u00e9 Paris-Saclay, Le Kremlin Bic\u00eatre, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marie-Pierre","family":"Debray","sequence":"additional","affiliation":[{"name":"Department of Radiology, H\u00f4pital Bichat Claude-Bernard, Assistance Publique-H\u00f4pitaux de Paris, Paris, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Antoine","family":"Beurnier","sequence":"additional","affiliation":[{"name":"Department of Functional Explorations, H\u00f4pital Bicetre, Assistance Publique-H\u00f4pitaux de Paris, Le Kremlin-Bicetre, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cindy","family":"Marques","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Universit\u00e9 Paris-Saclay, H\u00f4pital Bic\u00eatre, Assistance Publique-H\u00f4pitaux de Paris, Le Kremlin Bic\u00eatre, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3766-9600","authenticated-orcid":false,"given":"Pierre-Antoine","family":"Juge","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, H\u00f4pital Bichat Claude-Bernard, Assistance Publique-H\u00f4pitaux de Paris, Paris, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robin","family":"Dhote","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, H\u00f4pital Avicenne, Assistance Publique-H\u00f4pitaux de Paris, Bobigny, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Claire","family":"Larroche","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, H\u00f4pital Avicenne, Assistance Publique-H\u00f4pitaux de Paris, Bobigny, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anne Laure","family":"Fauchais","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Centre Hospitalier Universitaire de Limoges, Limoges, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Emanuelle","family":"Dernis","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Centre Hospitalier Le Mans, Le Mans, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Olivier","family":"Vittecoq","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, CHU Rouen Normandie, Rouen, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8454-7067","authenticated-orcid":false,"given":"Alain","family":"Saraux","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, CHU Brest, and Brest University, INSERM UMR 1227, Brest, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9469-946X","authenticated-orcid":false,"given":"Jacques-Eric","family":"Gottenberg","sequence":"additional","affiliation":[{"name":"Department of Rheumatology, Strasbourg University Hospital, Strasbourg, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7432-847X","authenticated-orcid":false,"given":"Eric","family":"Hachulla","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine and Clinical Immunology, Lille University Hospital, Lille, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V\u00e9ronique","family":"Le Guern","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine 1, Hopital Universitaire Pitie Salpetriere, Paris, 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