{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,18]],"date-time":"2026-02-18T16:05:26Z","timestamp":1771430726391,"version":"3.50.1"},"reference-count":12,"publisher":"BMJ","issue":"1","license":[{"start":{"date-parts":[[2026,2,18]],"date-time":"2026-02-18T00:00:00Z","timestamp":1771372800000},"content-version":"unspecified","delay-in-days":48,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["RMD Open"],"accepted":{"date-parts":[[2025,12,20]]},"published-print":{"date-parts":[[2026,1]]},"abstract":"<jats:sec>\n                    <jats:title>Introduction<\/jats:title>\n                    <jats:p>\n                      Familial Mediterranean fever (FMF) is the most common monogenic autoinflammatory disease. Colchicine is the first-line treatment, yet 5\u201310% of patients are resistant, increasing the risk of complications like amyloidosis. In 2023, Batu\n                      <jats:italic>et al<\/jats:italic>\n                      proposed the Turkish Paediatric Autoinflammatory Diseases (TURPAID) score to predict colchicine resistance in paediatric FMF at diagnosis. Its utility in broader populations is unknown. We assessed its performance in paediatric and adult FMF patients from the international Juvenile Inflammatory Rheumatism (JIR) cohort.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>\n                      We retrospectively analysed 236 genetically confirmed FMF patients treated with colchicine for \u22656 months. Patients were classified as colchicine-sensitive (CoS) or colchicine-resistant (CoR)\n                      <jats:italic>based on the initiation of biologic therapy<\/jats:italic>\n                      , which served as an operational definition of resistance, and matched for age and sex. The TURPAID score (range 0\u20134; resistance threshold \u22652) was retrospectively applied. Receiver operating characteristic (ROC) curves were used to assess predictive value.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>\n                      A TURPAID score \u22652 was observed in 89% of paediatric and 76% of adult CoS patients. Mean scores were significantly higher in paediatric-onset FMF. ROC analysis showed poor discrimination in both paediatric and adult groups (area under the curve=0.6). Clinical features and attack patterns varied by age. The genetic component (1.5 points for\n                      <jats:italic>MEFV<\/jats:italic>\n                      exon 10 mutations) contributed to overclassification, reducing predictive accuracy.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>The TURPAID score did not effectively predict colchicine resistance in the JIR cohort. Its limited generalisability may stem from age-related differences, recall bias and excessive genetic weighting. Genetic results should be a prerequisite and not a determinant of colchicine resistance prediction scores in FMF.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1136\/rmdopen-2025-006409","type":"journal-article","created":{"date-parts":[[2026,2,18]],"date-time":"2026-02-18T15:15:18Z","timestamp":1771427718000},"page":"e006409","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Colchicine resistance prediction criteria from the TURPAID cohort do not apply to the JIR cohort: a multicentre descriptive analysis"],"prefix":"10.1136","volume":"12","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-9781-7388","authenticated-orcid":false,"given":"Philippe","family":"Mertz","sequence":"first","affiliation":[{"name":"Department of Internal Medicine, Sorbonne University, DMU3ID, ERN RITA, H\u00f4pital Tenon, University, Assistance publique-h\u00f4pitaux de Paris (AP-HP), 4 rue de la Chine, 75020 Paris, France"},{"name":"Centre de r\u00e9f\u00e9rence des maladies autoinflammatoires et de l\u2019amylose (CEREMAIA), Paris, \u00cele-de-France, France"},{"name":"Service de p\u00e9diatrie, Centre hospitalier de Versailles, 78150 le Chesnay, France"},{"name":"Universit\u00e9 Paris Cit\u00e9, Institut Cochin, Inserm, CNRS, Paris, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9767-2262","authenticated-orcid":false,"given":"In\u00e8s","family":"Elhani","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Sorbonne University, DMU3ID, ERN RITA, H\u00f4pital Tenon, University, Assistance publique-h\u00f4pitaux de Paris (AP-HP), 4 rue de la Chine, 75020 Paris, France"},{"name":"Service de M\u00e9decine Interne, H\u00f4pital Jean Verdier, Bondy, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8939-5763","authenticated-orcid":false,"given":"Isabelle","family":"Kon\u00e9-Paut","sequence":"additional","affiliation":[{"name":"Centre de r\u00e9f\u00e9rence des maladies autoinflammatoires et de l\u2019amylose (CEREMAIA), Paris, \u00cele-de-France, France"},{"name":"Pediatric Rheumatology Department, Kremlin Bic\u00eatre Hospital, AP-HP, Le Kremlin Bic\u00eatre, University of Paris Saclay, Bic\u00e8tre, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Diana","family":"Dan","sequence":"additional","affiliation":[{"name":"Rheumatology Department, Lausanne University Hospital and University of Lausanne, Lausanne, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sandrine","family":"Roque","sequence":"additional","affiliation":[{"name":"Service de m\u00e9decine interne, CHU Nord, APHM, Marseille, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Katerina","family":"Theodoropoulou","sequence":"additional","affiliation":[{"name":"Paediatric Rheumatology and Immunology Unit, Department of Pediatrics, University Hospital of Lausanne (CHUV) and University of Lausanne (UNIL), Lausanne, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jana","family":"Pachlopnick Schmid","sequence":"additional","affiliation":[{"name":"Division of Immunology and Children\u2019s Research Center, University Children\u2019s Hospital, Zurich, Switzerland"},{"name":"Pediatric Immunology, Medical Faculty, University of Zurich, Zurich, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Brigitte","family":"Bader-Menier","sequence":"additional","affiliation":[{"name":"Department of Pediatric Immunology, Hematology and Rheumatology, Necker Hospital, AP-HP, National Reference Centre for Rheumatic and Autoimmune Diseases in Children, RAISE, Paris, \u00cele-de-France, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4902-5332","authenticated-orcid":false,"given":"Alexandre","family":"Belot","sequence":"additional","affiliation":[{"name":"National Referee Centre for Pediatric-Onset Rheumatism and Autoimmune Diseases, Hospices Civils de Lyon, Pediatric Nephrology, Rheumatology, Dermatology Unit, Mother and Children University Hospital, Lyon, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C\u00e9cile","family":"Dumaine","sequence":"additional","affiliation":[{"name":"General Paediatrics, Department of Infectious Disease and Internal Medicine, Robert Debr\u00e9 Mother-Child University Hospital, Reference Centre for Rheumatic, AutoImmune and Systemic Diseases in Children (RAISE), AP-HP, Paris, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Charlotte","family":"Kevorkian-Verguet","sequence":"additional","affiliation":[{"name":"Department of General Pediatrics, Grenoble Alpes University Hospital, Grenoble, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S\u00e9bastien","family":"Cavelot","sequence":"additional","affiliation":[{"name":"Centre de r\u00e9f\u00e9rence des maladies autoinflammatoires et de l\u2019amylose (CEREMAIA), Paris, \u00cele-de-France, France"},{"name":"Service de p\u00e9diatrie, Centre hospitalier de Versailles, 78150 le Chesnay, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6668-8854","authenticated-orcid":false,"given":"Sophie","family":"Georgin-Lavialle","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Sorbonne University, DMU3ID, ERN RITA, H\u00f4pital Tenon, University, Assistance publique-h\u00f4pitaux de Paris (AP-HP), 4 rue de la Chine, 75020 Paris, France"},{"name":"Centre de r\u00e9f\u00e9rence des maladies autoinflammatoires et de l\u2019amylose (CEREMAIA), Paris, \u00cele-de-France, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"V\u00e9ronique","family":"Hentgen","sequence":"additional","affiliation":[{"name":"Centre de r\u00e9f\u00e9rence des maladies autoinflammatoires et de l\u2019amylose (CEREMAIA), Paris, \u00cele-de-France, France"},{"name":"Service de p\u00e9diatrie, Centre hospitalier de Versailles, 78150 le Chesnay, France"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2026,2,18]]},"reference":[{"key":"2026021807151093000_12.1.e006409.1","doi-asserted-by":"crossref","first-page":"602","DOI":"10.1016\/j.revmed.2023.10.441","article-title":"French protocol for the diagnosis and management of familial Mediterranean fever","volume":"44","author":"Georgin-Lavialle","year":"2023","journal-title":"Rev 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