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MV was applied via a tracheostomy in 80 participants (67.2%) and non-invasive interfaces in 39 participants (32.8%), including 28 participants (71.8%) with daytime mouthpiece ventilation. HRQoL was rated good or excellent by 81 participants (68.1%), independently from age, diagnosis or respiratory autonomy. On multivariate analysis, time since MV initiation, independence from family member(s), residence in a rural area, ability to go outdoors with MV and tracheostomy were associated with better HRQoL.<\/jats:p>","DOI":"10.1136\/thorax-2022-219211","type":"journal-article","created":{"date-parts":[[2022,9,1]],"date-time":"2022-09-01T17:20:48Z","timestamp":1662052848000},"page":"92-96","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":13,"title":["Quality of life in patients with slowly progressive neuromuscular disorders dependent on mechanical ventilation"],"prefix":"10.1136","volume":"78","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-8506-2021","authenticated-orcid":false,"given":"Mathieu","family":"Delorme","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian","family":"Reveillere","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian","family":"Devaux","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandrine","family":"Segovia-Kueny","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fr\u00e9d\u00e9ric","family":"Lofaso","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ghilas","family":"Boussaid","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2022,9,1]]},"reference":[{"key":"2024051320320734000_78.1.92.1","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201210-1804CI"},{"key":"2024051320320734000_78.1.92.2","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00182208"},{"key":"2024051320320734000_78.1.92.3","doi-asserted-by":"publisher","DOI":"10.1016\/j.chest.2021.05.075"},{"key":"2024051320320734000_78.1.92.4","doi-asserted-by":"publisher","DOI":"10.1016\/S0895-4356(03)00088-X"},{"key":"2024051320320734000_78.1.92.5","doi-asserted-by":"publisher","DOI":"10.1002\/mus.25598"},{"key":"2024051320320734000_78.1.92.6","doi-asserted-by":"publisher","DOI":"10.1183\/23120541.00911-2020"},{"key":"2024051320320734000_78.1.92.7","doi-asserted-by":"publisher","DOI":"10.1378\/chest.104.6.1702"},{"key":"2024051320320734000_78.1.92.8","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200201-026OC"},{"key":"2024051320320734000_78.1.92.9","doi-asserted-by":"publisher","DOI":"10.1016\/j.nmd.2010.05.009"},{"key":"2024051320320734000_78.1.92.10","doi-asserted-by":"publisher","DOI":"10.1016\/j.rehab.2021.101552"}],"container-title":["Thorax"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/thorax-2022-219211","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,5,14]],"date-time":"2024-05-14T03:47:54Z","timestamp":1715658474000},"score":1,"resource":{"primary":{"URL":"https:\/\/thorax.bmj.com\/lookup\/doi\/10.1136\/thorax-2022-219211"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,9,1]]},"references-count":10,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2022,12,16]]},"published-print":{"date-parts":[[2023,1]]}},"alternative-id":["10.1136\/thorax-2022-219211"],"URL":"https:\/\/doi.org\/10.1136\/thorax-2022-219211","relation":{},"ISSN":["0040-6376","1468-3296"],"issn-type":[{"value":"0040-6376","type":"print"},{"value":"1468-3296","type":"electronic"}],"subject":[],"published":{"date-parts":[[2022,9,1]]}}}