{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T05:47:53Z","timestamp":1790401673994,"version":"4.1.0"},"reference-count":188,"publisher":"American Physiological Society","issue":"6","funder":[{"DOI":"10.13039\/100000897","name":"Cystic Fibrosis Foundation (CFF)","doi-asserted-by":"publisher","award":["CLANCY09YO"],"award-info":[{"award-number":["CLANCY09YO"]}],"id":[{"id":"10.13039\/100000897","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"HHS | NIH | National Heart, Lung, and Blood Institute (NHBLI)","doi-asserted-by":"publisher","award":["R35HL135816"],"award-info":[{"award-number":["R35HL135816"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"HHS | NIH | National Heart, Lung, and Blood Institute (NHBLI)","doi-asserted-by":"publisher","award":["1 T32 HL134640 01 (PI Chad Steele)"],"award-info":[{"award-number":["1 T32 HL134640 01 (PI Chad Steele)"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000050","name":"HHS | NIH | National Heart, Lung, and Blood Institute (NHBLI)","doi-asserted-by":"publisher","award":["5 T32 HL105346 08 (PI Victor J. Thannickal)"],"award-info":[{"award-number":["5 T32 HL105346 08 (PI Victor J. Thannickal)"]}],"id":[{"id":"10.13039\/100000050","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000062","name":"HHS | NIH | National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK)","doi-asserted-by":"publisher","award":["DK072482"],"award-info":[{"award-number":["DK072482"]}],"id":[{"id":"10.13039\/100000062","id-type":"DOI","asserted-by":"publisher"}]},{"name":"NIH","award":["KL2"],"award-info":[{"award-number":["KL2"]}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["American Journal of Physiology-Lung Cellular and Molecular Physiology"],"published-print":{"date-parts":[[2018,6,1]]},"abstract":"<jats:p> The respiratory tract is lined with multiciliated epithelial cells that function to move mucus and trapped particles via the mucociliary transport apparatus. Genetic and acquired ciliopathies result in diminished mucociliary clearance, contributing to disease pathogenesis. Recent innovations in imaging technology have advanced our understanding of ciliary motion in health and disease states. Application of imaging modalities including transmission electron microscopy, high-speed video microscopy, and micron-optical coherence tomography could improve diagnostics and be applied for precision medicine. In this review, we provide an overview of ciliary motion, imaging modalities, and ciliopathic diseases of the respiratory system including primary ciliary dyskinesia, cystic fibrosis, chronic obstructive pulmonary disease, and idiopathic pulmonary fibrosis. <\/jats:p>","DOI":"10.1152\/ajplung.00556.2017","type":"journal-article","created":{"date-parts":[[2018,3,1]],"date-time":"2018-03-01T05:33:40Z","timestamp":1519882420000},"page":"L909-L921","source":"Crossref","is-referenced-by-count":30,"title":["Seeing cilia: imaging modalities for ciliary motion and clinical connections"],"prefix":"10.1152","volume":"314","author":[{"given":"Jacelyn E.","family":"Peabody","sequence":"first","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"},{"name":"Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7733-643X","authenticated-orcid":false,"given":"Ren-Jay","family":"Shei","sequence":"additional","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"},{"name":"Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Brent M.","family":"Bermingham","sequence":"additional","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Scott E.","family":"Phillips","sequence":"additional","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Brett","family":"Turner","sequence":"additional","affiliation":[{"name":"Departments of Pediatrics and Cell Developmental and Integrative Biology, University of Alabama at Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Steven M.","family":"Rowe","sequence":"additional","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"},{"name":"Departments of Pediatrics and Cell Developmental and Integrative Biology, University of Alabama at Birmingham, Alabama"},{"name":"Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3490-8474","authenticated-orcid":false,"given":"George M.","family":"Solomon","sequence":"additional","affiliation":[{"name":"Department of Medicine, University of Alabama at Birmingham, Alabama"},{"name":"Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"24","reference":[{"key":"B1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1084576"},{"key":"B2","doi-asserted-by":"publisher","DOI":"10.1016\/j.diff.2011.11.015"},{"key":"B3","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00176608"},{"key":"B4","doi-asserted-by":"publisher","DOI":"10.1016\/0092-8674(92)90155-6"},{"key":"B5","doi-asserted-by":"publisher","DOI":"10.1152\/ajplung.00395.2015"},{"key":"B6","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201404-0670OC"},{"key":"B7","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.066308"},{"key":"B8","doi-asserted-by":"publisher","DOI":"10.1042\/EBC20170032"},{"key":"B9","doi-asserted-by":"publisher","DOI":"10.1111\/eci.12254"},{"key":"B10","doi-asserted-by":"publisher","DOI":"10.1165\/ajrcmb.23.1.4070"},{"key":"B11","doi-asserted-by":"publisher","DOI":"10.1165\/rcmb.2011-0440OC"},{"key":"B12","doi-asserted-by":"publisher","DOI":"10.1101\/cshperspect.a028241"},{"key":"B13","doi-asserted-by":"publisher","DOI":"10.1016\/j.resp.2008.04.020"},{"key":"B14","doi-asserted-by":"publisher","DOI":"10.1126\/science.1223012"},{"key":"B15","doi-asserted-by":"publisher","DOI":"10.1126\/scisignal.2003755"},{"key":"B16","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0003316"},{"key":"B17","doi-asserted-by":"publisher","DOI":"10.1136\/thorax.55.4.314"},{"key":"B18","doi-asserted-by":"publisher","DOI":"10.1242\/dev.074666"},{"key":"B19","doi-asserted-by":"publisher","DOI":"10.1016\/B978-0-12-397944-5.00003-1"},{"key":"B20","doi-asserted-by":"publisher","DOI":"10.1364\/BOE.7.002494"},{"key":"B21","doi-asserted-by":"publisher","DOI":"10.4161\/auto.27641"},{"key":"B22","doi-asserted-by":"publisher","DOI":"10.1001\/jamaoto.2013.3917"},{"key":"B23","doi-asserted-by":"publisher","DOI":"10.1164\/ajrccm.150.4.7921471"},{"key":"B24","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201502-0396LE"},{"key":"B25","doi-asserted-by":"publisher","DOI":"10.1364\/OL.42.000867"},{"key":"B26","doi-asserted-by":"publisher","DOI":"10.2147\/TACG.S127129"},{"key":"B27","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201409-1672OC"},{"key":"B28","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa042976"},{"key":"B29","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.201408039"},{"key":"B30","doi-asserted-by":"publisher","DOI":"10.1186\/1465-9921-14-70"},{"key":"B31","doi-asserted-by":"publisher","DOI":"10.1211\/0022357055777"},{"key":"B32","doi-asserted-by":"publisher","DOI":"10.1080\/01913123.2017.1365990"},{"key":"B33","doi-asserted-by":"publisher","DOI":"10.1378\/chest.13-0274"},{"key":"B34","first-page":"37","volume":"20","author":"Dresdner RD","year":"1984","journal-title":"Biomed Sci Instrum"},{"key":"B35","doi-asserted-by":"publisher","DOI":"10.1113\/JP273996"},{"key":"B36","doi-asserted-by":"publisher","DOI":"10.1172\/jci.insight.88198"},{"key":"B37","doi-asserted-by":"publisher","DOI":"10.1016\/S0168-9525(03)00026-X"},{"key":"B38","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra0910061"},{"key":"B39","doi-asserted-by":"publisher","DOI":"10.1288\/00005537-195407000-00002"},{"key":"B40","first-page":"e50343","volume":"78","author":"Francis R","year":"2013","journal-title":"J Vis Exp"},{"key":"B41","doi-asserted-by":"publisher","DOI":"10.1038\/sj.neo.7900071"},{"key":"B42","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.201111146"},{"key":"B43","doi-asserted-by":"publisher","DOI":"10.1126\/science.149.3682.424"},{"key":"B44","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01181-2016"},{"key":"B45","doi-asserted-by":"publisher","DOI":"10.1136\/thx.2006.062836"},{"key":"B46","doi-asserted-by":"publisher","DOI":"10.1016\/j.otc.2010.02.007"},{"key":"B47","doi-asserted-by":"publisher","DOI":"10.1136\/thoraxjnl-2015-207588"},{"key":"B48","doi-asserted-by":"publisher","DOI":"10.1172\/JCI73469"},{"key":"B49","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0085453"},{"key":"B50","doi-asserted-by":"publisher","DOI":"10.1126\/science.1255825"},{"key":"B51","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa032158"},{"key":"B52","doi-asserted-by":"publisher","DOI":"10.1038\/pr.2013.200"},{"key":"B53","doi-asserted-by":"publisher","DOI":"10.1016\/j.prrv.2015.09.001"},{"key":"B54","doi-asserted-by":"publisher","DOI":"10.1126\/science.1957169"},{"key":"B55","doi-asserted-by":"publisher","DOI":"10.1378\/chest.127.4.1219"},{"key":"B56","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa1113354"},{"key":"B57","doi-asserted-by":"publisher","DOI":"10.1378\/chest.130.4.1102"},{"key":"B58","doi-asserted-by":"publisher","DOI":"10.1016\/S0091-679X(08)60815-8"},{"key":"B59","doi-asserted-by":"publisher","DOI":"10.2142\/biophysics.9.141"},{"key":"B60","doi-asserted-by":"publisher","DOI":"10.1101\/cshperspect.a028076"},{"key":"B61","doi-asserted-by":"publisher","DOI":"10.1186\/s13630-014-0012-7"},{"key":"B62","doi-asserted-by":"publisher","DOI":"10.1242\/dev.041129"},{"key":"B63","first-page":"1088","volume":"4","author":"Jain R","year":"2012","journal-title":"Front Biosci (Schol Ed)"},{"key":"B64","doi-asserted-by":"publisher","DOI":"10.1165\/rcmb.2009-0328OC"},{"key":"B65","doi-asserted-by":"publisher","DOI":"10.2307\/1538256"},{"key":"B66","doi-asserted-by":"publisher","DOI":"10.1038\/s41598-017-08968-x"},{"key":"B67","doi-asserted-by":"publisher","DOI":"10.1007\/BF02141468"},{"key":"B68","doi-asserted-by":"publisher","DOI":"10.1016\/j.chest.2016.09.015"},{"key":"B69","doi-asserted-by":"publisher","DOI":"10.1172\/JCI0215217"},{"key":"B70","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201301-0059CI"},{"key":"B71","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201311-2047OC"},{"key":"B72","doi-asserted-by":"publisher","DOI":"10.1016\/j.ccm.2016.04.008"},{"key":"B73","doi-asserted-by":"publisher","DOI":"10.1038\/nsmb.1555"},{"key":"B74","doi-asserted-by":"publisher","DOI":"10.1186\/1752-0509-5-143"},{"key":"B75","doi-asserted-by":"publisher","DOI":"10.1038\/pr.2016.263"},{"key":"B76","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00001010"},{"key":"B77","doi-asserted-by":"publisher","DOI":"10.1513\/AnnalsATS.201605-331PS"},{"key":"B78","doi-asserted-by":"publisher","DOI":"10.1172\/JCI69636"},{"key":"B79","doi-asserted-by":"publisher","DOI":"10.1016\/S0006-3495(99)76919-5"},{"key":"B80","doi-asserted-by":"publisher","DOI":"10.1186\/2046-2530-2-15"},{"key":"B81","doi-asserted-by":"publisher","DOI":"10.1038\/emboj.2009.405"},{"key":"B82","doi-asserted-by":"publisher","DOI":"10.1513\/AnnalsATS.201511-748OC"},{"key":"B83","doi-asserted-by":"publisher","DOI":"10.1016\/j.chest.2016.11.025"},{"key":"B84","doi-asserted-by":"publisher","DOI":"10.1097\/GIM.0b013e3181a53562"},{"key":"B85","doi-asserted-by":"publisher","DOI":"10.1097\/MOP.0b013e328329cddb"},{"key":"B86","doi-asserted-by":"publisher","DOI":"10.1002\/alr.21582"},{"key":"B87","doi-asserted-by":"publisher","DOI":"10.1002\/ppul.23840"},{"key":"B88","doi-asserted-by":"publisher","DOI":"10.1038\/ncb2939"},{"key":"B89","doi-asserted-by":"publisher","DOI":"10.1038\/ncomms6727"},{"key":"B90","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0054473"},{"key":"B91","doi-asserted-by":"publisher","DOI":"10.1038\/nm.2409"},{"key":"B92","doi-asserted-by":"publisher","DOI":"10.1165\/rcmb.2013-0499MA"},{"key":"B93","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01090-2016"},{"key":"B94","doi-asserted-by":"publisher","DOI":"10.1136\/archdischild-2013-304831"},{"key":"B95","doi-asserted-by":"publisher","DOI":"10.1165\/rcmb.2014-0078OC"},{"key":"B96","doi-asserted-by":"publisher","DOI":"10.1007\/s00405-009-1161-y"},{"key":"B97","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200106141"},{"key":"B98","doi-asserted-by":"publisher","DOI":"10.1016\/S0092-8674(00)81724-9"},{"key":"B99","doi-asserted-by":"publisher","DOI":"10.3389\/fped.2017.00135"},{"key":"B100","doi-asserted-by":"publisher","DOI":"10.1080\/01913123.2017.1370050"},{"key":"B101","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.2005.034868"},{"key":"B102","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbagen.2017.07.020"},{"key":"B103","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcf.2016.09.005"},{"key":"B104","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.31.6.493"},{"key":"B105","doi-asserted-by":"publisher","DOI":"10.1016\/j.devcel.2012.05.010"},{"key":"B106","doi-asserted-by":"publisher","DOI":"10.1016\/j.cell.2009.10.036"},{"key":"B107","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200303-365OC"},{"key":"B108","doi-asserted-by":"publisher","DOI":"10.1152\/ajplung.00364.2013"},{"key":"B109","doi-asserted-by":"publisher","DOI":"10.1136\/adc.2009.158493"},{"key":"B110","doi-asserted-by":"publisher","DOI":"10.1007\/s00232-002-1031-7"},{"key":"B111","doi-asserted-by":"publisher","DOI":"10.1093\/jmicro\/dfx018"},{"key":"B112","doi-asserted-by":"publisher","DOI":"10.1016\/j.jsb.2013.07.003"},{"key":"B113","doi-asserted-by":"publisher","DOI":"10.1146\/annurev-biochem-061516-044741"},{"key":"B114","doi-asserted-by":"publisher","DOI":"10.1152\/japplphysiol.00629.2010"},{"key":"B115","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajhg.2012.11.002"},{"key":"B116","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00046209"},{"key":"B117","doi-asserted-by":"publisher","DOI":"10.1016\/j.phrs.2004.07.006"},{"key":"B118","doi-asserted-by":"publisher","DOI":"10.1001\/archoto.2010.183"},{"key":"B119","doi-asserted-by":"publisher","DOI":"10.1126\/scitranslmed.aaa1233"},{"key":"B120","doi-asserted-by":"publisher","DOI":"10.1152\/ajplung.00039.2013"},{"key":"B121","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.2009-040GL"},{"key":"B122","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200602-163OC"},{"key":"B123","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00052014"},{"key":"B124","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201304-0733OC"},{"key":"B125","doi-asserted-by":"publisher","DOI":"10.1172\/jci.insight.87536"},{"key":"B126","doi-asserted-by":"publisher","DOI":"10.1165\/rcmb.2016-0226OC"},{"key":"B127","doi-asserted-by":"publisher","DOI":"10.1016\/j.ccm.2015.11.003"},{"key":"B128","doi-asserted-by":"publisher","DOI":"10.1038\/nrm952"},{"key":"B129","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra043184"},{"key":"B130","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.physiol.69.040705.141253"},{"key":"B131","doi-asserted-by":"publisher","DOI":"10.1091\/mbc.1.8.585"},{"key":"B132","doi-asserted-by":"publisher","DOI":"10.1002\/cm.970050402"},{"key":"B133","doi-asserted-by":"publisher","DOI":"10.1186\/s13630-017-0046-8"},{"key":"B134","doi-asserted-by":"publisher","DOI":"10.1002\/cm.970320203"},{"key":"B135","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.26.3.805"},{"key":"B136","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.39.1.77"},{"key":"B137","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.18.2.345"},{"key":"B138","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M110.113621"},{"key":"B139","doi-asserted-by":"publisher","DOI":"10.3762\/bjoc.4.34"},{"key":"B140","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0058658"},{"key":"B141","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa1013660"},{"key":"B142","doi-asserted-by":"publisher","DOI":"10.1126\/science.1173869"},{"key":"B143","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0712327105"},{"key":"B144","doi-asserted-by":"publisher","DOI":"10.1513\/AnnalsATS.201701-062SR"},{"key":"B145","doi-asserted-by":"publisher","DOI":"10.1002\/ppul.23304"},{"key":"B146","doi-asserted-by":"publisher","DOI":"10.1080\/01913123.2017.1365789"},{"key":"B147","doi-asserted-by":"publisher","DOI":"10.1136\/thoraxjnl-2012-202938"},{"key":"B148","doi-asserted-by":"publisher","DOI":"10.1016\/j.tcb.2009.04.002"},{"key":"B149","doi-asserted-by":"publisher","DOI":"10.1046\/j.1365-2818.2003.01209.x"},{"key":"B150","doi-asserted-by":"publisher","DOI":"10.1186\/2046-2530-1-14"},{"key":"B151","doi-asserted-by":"publisher","DOI":"10.1172\/jci.insight.91702"},{"key":"B152","doi-asserted-by":"publisher","DOI":"10.1016\/j.coph.2017.09.013"},{"key":"B153","first-page":"A7080","volume":"195","author":"Solomon GM","year":"2017","journal-title":"Am J Respir Crit Care Med"},{"key":"B154","doi-asserted-by":"publisher","DOI":"10.1016\/S2213-2600(16)30047-9"},{"key":"B155","doi-asserted-by":"publisher","DOI":"10.1513\/AnnalsATS.201509-601KV"},{"key":"B156","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M114.626556"},{"key":"B157","doi-asserted-by":"publisher","DOI":"10.1038\/nrm.2017.21"},{"key":"B158","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200903-0459OC"},{"key":"B159","doi-asserted-by":"publisher","DOI":"10.1038\/ng.267"},{"key":"B160","doi-asserted-by":"publisher","DOI":"10.1016\/S0006-3495(95)80292-4"},{"key":"B161","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M505832200"},{"key":"B162","doi-asserted-by":"publisher","DOI":"10.1529\/biophysj.106.094698"},{"key":"B163","doi-asserted-by":"publisher","DOI":"10.1007\/s10654-016-0132-z"},{"key":"B164","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00153308"},{"key":"B165","doi-asserted-by":"publisher","DOI":"10.1146\/annurev-physiol-021014-071931"},{"key":"B166","doi-asserted-by":"publisher","DOI":"10.1002\/lary.26720"},{"key":"B167","doi-asserted-by":"publisher","DOI":"10.1586\/17476348.2015.1067609"},{"key":"B168","doi-asserted-by":"crossref","first-page":"A2506","DOI":"10.1164\/rccm.201508-1633OC","volume":"193","author":"Turner B","year":"2016","journal-title":"Am J Respir Crit Care Med"},{"key":"B169","doi-asserted-by":"publisher","DOI":"10.1152\/ajplung.00324.2015"},{"key":"B170","doi-asserted-by":"publisher","DOI":"10.1002\/cm.21180"},{"key":"B171","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0904709106"},{"key":"B172","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pgen.1003019"},{"key":"B173","doi-asserted-by":"publisher","DOI":"10.1513\/pats.200602-019TK"},{"key":"B174","doi-asserted-by":"publisher","DOI":"10.1101\/cshperspect.a018325"},{"key":"B175","doi-asserted-by":"publisher","DOI":"10.1172\/jci.insight.88027"},{"key":"B176","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201701-0218PP"},{"key":"B177","doi-asserted-by":"publisher","DOI":"10.1007\/BF00231506"},{"key":"B178","doi-asserted-by":"publisher","DOI":"10.1091\/mbc.E12-12-0863"},{"key":"B179","doi-asserted-by":"publisher","DOI":"10.1136\/thoraxjnl-2013-203928"},{"key":"B180","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.03.00305503"},{"key":"B181","doi-asserted-by":"publisher","DOI":"10.1172\/JCI0213870"},{"key":"B182","doi-asserted-by":"publisher","DOI":"10.3390\/cells5040040"},{"key":"B183","doi-asserted-by":"publisher","DOI":"10.1016\/j.rmed.2012.04.001"},{"key":"B184","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200601-062OC"},{"key":"B185","doi-asserted-by":"publisher","DOI":"10.1038\/ng.263"},{"key":"B186","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0104090"},{"key":"B187","doi-asserted-by":"publisher","DOI":"10.2500\/ajra.2011.25.3643"},{"key":"B188","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0033667"}],"container-title":["American Journal of Physiology-Lung Cellular and Molecular Physiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.physiology.org\/doi\/pdf\/10.1152\/ajplung.00556.2017","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,9,24]],"date-time":"2019-09-24T04:50:54Z","timestamp":1569300654000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.physiology.org\/doi\/10.1152\/ajplung.00556.2017"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,6,1]]},"references-count":188,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2018,6,1]]}},"alternative-id":["10.1152\/ajplung.00556.2017"],"URL":"https:\/\/doi.org\/10.1152\/ajplung.00556.2017","relation":{},"ISSN":["1040-0605","1522-1504"],"issn-type":[{"value":"1040-0605","type":"print"},{"value":"1522-1504","type":"electronic"}],"subject":[],"published":{"date-parts":[[2018,6,1]]}}}