{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,3]],"date-time":"2025-07-03T09:24:53Z","timestamp":1751534693598},"reference-count":60,"publisher":"Hindawi Limited","license":[{"start":{"date-parts":[[2014,1,1]],"date-time":"2014-01-01T00:00:00Z","timestamp":1388534400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/3.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Case Reports in Urology"],"published-print":{"date-parts":[[2014]]},"abstract":"<jats:p><jats:italic>Introduction<\/jats:italic>. Angiomyolipoma is a common benign renal tumor. It is associated with Tuberous Sclerosis Complex (TSC) in 20% of patients. Angiomyolipomas are classically multiple, bilateral, and growing; they may lead to complications such as Wunderlich syndrome or, in rare cases, to venous extension.<jats:italic>Observation<\/jats:italic>. a 74-year-old woman with TSC presented with an angiomyolipoma of the right kidney with inferior vena cava (IVC) fatty thrombus. She underwent partial nephrectomy and thrombectomy. After a 7-year follow-up there was no evidence of recurrence or metastasis and her renal function was preserved.<jats:italic>Review of Literature<\/jats:italic>. It is the 44th reported angiomyolipoma associated with IVC thrombus. The mean size of angiomyolipomas was 86.1\u2009mm and 67.4% of patients were symptomatic. Pulmonary embolism was found in 6 patients. There were 2 cases of recurrence\/metastatic outcome after radical nephrectomy and thrombectomy. They were associated with epithelioid form. The mean size of epithelioid tumors was significantly bigger than in classical angiomyolipomas (127.1\u2009mm versus 82.6\u2009mm,<mml:math xmlns:mml=\"http:\/\/www.w3.org\/1998\/Math\/MathML\" id=\"M1\"><mml:mrow><mml:mi>P<\/mml:mi><mml:mo>=<\/mml:mo><mml:mn>0.037<\/mml:mn><\/mml:mrow><\/mml:math>). With a median follow-up of 12 months, 91.3% of patients were recurrence and metastasis free, with 3 cases of nephron sparing surgery.<jats:italic>Conclusion<\/jats:italic>. Nephron sparing surgery for angiomyolipoma with IVC fatty thrombus can be safely performed in TSC, even in sporadic angiomyolipoma.<\/jats:p>","DOI":"10.1155\/2014\/285613","type":"journal-article","created":{"date-parts":[[2014,2,23]],"date-time":"2014-02-23T21:02:53Z","timestamp":1393189373000},"page":"1-8","source":"Crossref","is-referenced-by-count":7,"title":["Nephron Sparing Surgery for Renal Angiomyolipoma with Inferior Vena Cava Thrombus in Tuberous Sclerosis"],"prefix":"10.1155","volume":"2014","author":[{"given":"Adrien","family":"Riviere","sequence":"first","affiliation":[{"name":"H\u00f4pital Bic\u00eatre, 78 Rue du G\u00e9n\u00e9ral Leclerc, 94275 Le Kremlin-Bic\u00eatre, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas","family":"Bessede","sequence":"additional","affiliation":[{"name":"H\u00f4pital Bic\u00eatre, 78 Rue du G\u00e9n\u00e9ral Leclerc, 94275 Le Kremlin-Bic\u00eatre, 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