{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,4,5]],"date-time":"2022-04-05T14:15:14Z","timestamp":1649168114937},"reference-count":13,"publisher":"Hindawi Limited","license":[{"start":{"date-parts":[[2014,1,1]],"date-time":"2014-01-01T00:00:00Z","timestamp":1388534400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/3.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Case Reports in Dentistry"],"published-print":{"date-parts":[[2014]]},"abstract":"<jats:p>Ectodermal dysplasia and sickle cell anaemia are inherited disorders that affect, respectively, the tissues derived from the embryonic ectoderm and the production of erythrocytes by the bone marrow. The simultaneous occurrence of both disorders is extremely rare. This is a case of both ectodermal dysplasia and sickle cell anaemia reported in a 6-year-old. The patient had been diagnosed with sickle cell anaemia for only six months when he sought treatment presenting with the following: hypotrichosis, dry skin, periocular hyperpigmentation, protruding lips, hypodontia, and morphologically altered teeth. The clinical features combined with his medical history led to the diagnosis of ectodermal dysplasia. Dentists should be prepared to recognise patterns that escape normality to aid in the diagnosis of systemic changes, even in patients with other previous diagnoses.<\/jats:p>","DOI":"10.1155\/2014\/314391","type":"journal-article","created":{"date-parts":[[2014,9,29]],"date-time":"2014-09-29T21:13:13Z","timestamp":1412025193000},"page":"1-3","source":"Crossref","is-referenced-by-count":0,"title":["Ectodermal Dysplasia Associated with Sickle Cell Disease"],"prefix":"10.1155","volume":"2014","author":[{"given":"Luiz Evaristo Ricci","family":"Volpato","sequence":"first","affiliation":[{"name":"Department of Post-Graduation, Master Program in Integrated Dentistry Science, University of Cuiab\u00e1, Avenida Manoel Jos\u00e9 de Arruda No. 3.100, 78050-000 Cuiab\u00e1, MT, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Maria Carmen Palma Faria","family":"Volpato","sequence":"additional","affiliation":[{"name":"Department of Post-Graduation, Master Program in Integrated Dentistry Science, University of Cuiab\u00e1, Avenida Manoel Jos\u00e9 de Arruda No. 3.100, 78050-000 Cuiab\u00e1, MT, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Artur Aburad","family":"de Carvalhosa","sequence":"additional","affiliation":[{"name":"Department of Post-Graduation, Master Program in Integrated Dentistry Science, University of Cuiab\u00e1, Avenida Manoel Jos\u00e9 de Arruda No. 3.100, 78050-000 Cuiab\u00e1, MT, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vinicius Canavarros","family":"Palma","sequence":"additional","affiliation":[{"name":"Department of Post-Graduation, Master Program in Integrated Dentistry Science, University of Cuiab\u00e1, Avenida Manoel Jos\u00e9 de Arruda No. 3.100, 78050-000 Cuiab\u00e1, MT, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"\u00c1lvaro Henrique","family":"Borges","sequence":"additional","affiliation":[{"name":"Department of Post-Graduation, Master Program in Integrated Dentistry Science, University of Cuiab\u00e1, Avenida Manoel Jos\u00e9 de Arruda No. 3.100, 78050-000 Cuiab\u00e1, MT, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"98","reference":[{"key":"1","doi-asserted-by":"publisher","DOI":"10.4103\/0378-6323.37060"},{"key":"2","year":"2004"},{"issue":"4","key":"3","first-page":"285","volume":"26","year":"1995","journal-title":"Quintessence International"},{"issue":"5","key":"4","first-page":"524","volume":"16","year":"1995","journal-title":"Compendium of Continuing Education in Dentistry"},{"issue":"11","key":"5","first-page":"525","volume":"32","year":"2010","journal-title":"Revista Brasileira de Ginecologia e Obstetricia"},{"issue":"1","key":"6","first-page":"29","volume":"3","year":"2010","journal-title":"Stem Cells and Cloning"},{"key":"7","doi-asserted-by":"publisher","DOI":"10.3109\/13816810.2010.497529"},{"issue":"12","key":"8","first-page":"976","volume":"51","year":"2010","journal-title":"Singapore Medical Journal"},{"issue":"2","key":"9","first-page":"113","volume":"4","year":"2008","journal-title":"Revista de Cl\u00ednica e Pesquisa Odontol\u00f3gica"},{"key":"10","doi-asserted-by":"publisher","DOI":"10.4103\/0976-9668.117012"},{"key":"11","doi-asserted-by":"publisher","DOI":"10.4103\/0976-9668.136253"},{"key":"12","doi-asserted-by":"publisher","DOI":"10.5005\/jp-journals-10005-1207"},{"issue":"3","key":"13","first-page":"108","volume":"6","year":"2012","journal-title":"Journal of Dental Research, Dental Clinics, Dental Prospects"}],"container-title":["Case Reports in Dentistry"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/downloads.hindawi.com\/journals\/crid\/2014\/314391.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/crid\/2014\/314391.xml","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/crid\/2014\/314391.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2016,8,18]],"date-time":"2016-08-18T16:52:36Z","timestamp":1471539156000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.hindawi.com\/journals\/crid\/2014\/314391\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014]]},"references-count":13,"alternative-id":["314391","314391"],"URL":"https:\/\/doi.org\/10.1155\/2014\/314391","relation":{},"ISSN":["2090-6447","2090-6455"],"issn-type":[{"value":"2090-6447","type":"print"},{"value":"2090-6455","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014]]}}}