{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,16]],"date-time":"2026-10-16T16:09:25Z","timestamp":1792166965373,"version":"4.4.0"},"reference-count":13,"publisher":"Hindawi Limited","license":[{"start":{"date-parts":[[2015,1,1]],"date-time":"2015-01-01T00:00:00Z","timestamp":1420070400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/3.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Case Reports in Pulmonology"],"published-print":{"date-parts":[[2015]]},"abstract":"<jats:p>Short-rib polydactyly syndrome is an autosomal recessively inherited lethal skeletal dysplasia. The syndrome is characterized by marked narrow fetal thorax, short extremities, micromelia, cleft palate\/lip, polydactyly, cardiac and renal abnormalities, and genital malformations. In cases with pulmonary hypoplasia, persistent pulmonary hypertension of the newborn can develop. In this paper, we present a term newborn with persistent pulmonary hypertension of the newborn, which has developed secondary to short-rib polydactyly syndrome and was resistant to therapy with inhaled nitric oxide and oral sildenafil.<\/jats:p>","DOI":"10.1155\/2015\/274639","type":"journal-article","created":{"date-parts":[[2015,5,20]],"date-time":"2015-05-20T17:03:01Z","timestamp":1432141381000},"page":"1-3","source":"Crossref","is-referenced-by-count":4,"title":["A Rare Cause of Persistent Pulmonary Hypertension Resistant to Therapy in The Newborn: Short-Rib Polydactyly Syndrome"],"prefix":"10.1155","volume":"2015","author":[{"given":"Nihat","family":"Demir","sequence":"first","affiliation":[{"name":"Department of Pediatrics, Division of Neonatology, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Erdal","family":"Peker","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Division of Neonatology, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u0130brahim","family":"Ece","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Division of Cardiology, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sultan","family":"Kaba","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Division of Endocrinology, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kemal","family":"A\u011fengin","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"O\u011fuz","family":"Tuncer","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Division of Neonatology, Yuzuncu Yil University School of Medicine, 65080 Van, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"98","reference":[{"key":"1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajhg.2011.03.015"},{"key":"2","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajhg.2013.06.022"},{"key":"3","doi-asserted-by":"publisher","DOI":"10.1002\/uog.6147"},{"key":"4","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajhg.2013.06.022"},{"key":"5","doi-asserted-by":"publisher","DOI":"10.1111\/j.1447-0756.2010.01324.x"},{"key":"6","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcma.2011.12.004"},{"key":"7","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.31031"},{"key":"8","doi-asserted-by":"publisher","DOI":"10.1016\/j.jfma.2012.11.007"},{"key":"9","doi-asserted-by":"publisher","DOI":"10.1155\/2012\/818971"},{"key":"10","doi-asserted-by":"publisher","DOI":"10.1016\/j.bpa.2010.02.021"},{"key":"11","doi-asserted-by":"publisher","DOI":"10.1016\/j.ymgme.2014.01.001"},{"key":"12","doi-asserted-by":"publisher","DOI":"10.1038\/pr.2011.24"},{"key":"13","doi-asserted-by":"publisher","DOI":"10.1097\/MCD.0b013e3283079e68"}],"container-title":["Case Reports in Pulmonology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripu\/2015\/274639.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripu\/2015\/274639.xml","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripu\/2015\/274639.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2016,8,18]],"date-time":"2016-08-18T12:54:26Z","timestamp":1471524866000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.hindawi.com\/journals\/cripu\/2015\/274639\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015]]},"references-count":13,"alternative-id":["274639","274639"],"URL":"https:\/\/doi.org\/10.1155\/2015\/274639","relation":{},"ISSN":["2090-6846","2090-6854"],"issn-type":[{"value":"2090-6846","type":"print"},{"value":"2090-6854","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015]]}}}