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These predominantly characteristic, small round-cell tumors include Ewing\u2019s sarcoma of the bone and soft tissue, as well as primitive neuroectodermal tumors (PNETs) involving the bone, soft tissue, and thoracopulmonary region (Askin\u2019s tumor). Extraosseous ESFTs are extremely rare, especially in the head and neck region, where literature to date consists of sporadic case reports and very small series. We hereby present a review of the literature published on ESFTs reported in the maxilla and maxillary sinus region from 1968 to 2016.<\/jats:p>","DOI":"10.1155\/2016\/3872768","type":"journal-article","created":{"date-parts":[[2016,6,16]],"date-time":"2016-06-16T20:27:55Z","timestamp":1466108875000},"page":"1-15","source":"Crossref","is-referenced-by-count":17,"title":["Multimodality Treatment in Ewing\u2019s Sarcoma Family Tumors of the Maxilla and Maxillary Sinus: Review of the Literature"],"prefix":"10.1155","volume":"2016","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-7966-0711","authenticated-orcid":true,"given":"David","family":"Thorn","sequence":"first","affiliation":[{"name":"Division of Medical Oncology, Cantonal Hospital Aarau, 5001 Aarau, Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christoph","family":"Mamot","sequence":"additional","affiliation":[{"name":"Division of Medical Oncology, Cantonal Hospital Aarau, 5001 Aarau, 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