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Only 22 cases had been published worldwide by 2008; nearly 80% of these cases were reported before 2007. In order to investigate the current clinical status of PEA, we search for relevant literatures with \u201cepididymis and adenocarcinoma\u201d and \u201cepididymal and adenocarcinoma\u201d as keywords published between January 1997 and November 2017 in PubMed. As a result, 17 cases are identified. We review these cases and summarize new and important perspectives about the clinicopathological characteristics, diagnosis, treatment, and prognosis of PEA in the present review.<\/jats:p>","DOI":"10.1155\/2017\/4126740","type":"journal-article","created":{"date-parts":[[2017,12,20]],"date-time":"2017-12-20T18:58:11Z","timestamp":1513796291000},"page":"1-9","source":"Crossref","is-referenced-by-count":6,"title":["Clinicopathological Characteristics, Treatment, and Prognosis of Rarely Primary Epididymal Adenocarcinoma: A Review and Update"],"prefix":"10.1155","volume":"2017","author":[{"given":"Zi-jun","family":"Zou","sequence":"first","affiliation":[{"name":"Institute of Urology, Department of Urology, West China Hospital, Sichuan University, Chengdu, Sichuan 610041, China"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ying-ming","family":"Xiao","sequence":"additional","affiliation":[{"name":"Department of Urology, Sichuan Cancer Hospital & Institute, Chengdu, 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