{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,1]],"date-time":"2026-10-01T18:25:48Z","timestamp":1790879148936,"version":"4.1.0"},"reference-count":24,"publisher":"Wiley","license":[{"start":{"date-parts":[[2020,10,29]],"date-time":"2020-10-29T00:00:00Z","timestamp":1603929600000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Case Reports in Pediatrics"],"published-print":{"date-parts":[[2020,10,29]]},"abstract":"<jats:p>Introduction. Hepatopulmonary fusion is a very rare finding associated with right-sided congenital diaphragmatic hernia. With less than 50 reported cases, management and outcomes of hepatopulmonary fusion are poorly understood. This report highlights that clinical presentation is not a reliable indicator of outcomes in this rare disease. Case Presentation. A term neonate admitted for tachypnea and complete opacification of the right hemithorax was diagnosed with right-sided congenital diaphragmatic hernia. Preoperative respiratory support was minimal, and the only symptom exhibited was tachypnea. During surgical repair, fusion of the lung and liver were noted, consistent with a diagnosis of hepatopulmonary fusion. Postoperatively, the patient\u2019s pulmonary hypertension worsened and required extracorporeal membrane oxygenation. Conclusions. Many patients with hepatopulmonary fusion and only mild symptoms die postoperatively from severe pulmonary hypertension and progressive respiratory failure. Preoperative clinical status is not indicative of postoperative outcomes, and literature suggests that patients who require less support preoperatively have high mortality rates. The availability of ECMO for postoperative complications may be necessary in patients requiring repair of hepatopulmonary fusion.<\/jats:p>","DOI":"10.1155\/2020\/8851341","type":"journal-article","created":{"date-parts":[[2020,10,29]],"date-time":"2020-10-29T22:05:09Z","timestamp":1604009109000},"page":"1-6","source":"Crossref","is-referenced-by-count":1,"title":["Right-Sided Congenital Diaphragmatic Hernia Caused by Hepatopulmonary Fusion"],"prefix":"10.1155","volume":"2020","author":[{"given":"Sonal","family":"Patel","sequence":"first","affiliation":[{"name":"Department of Pediatrics, Division of Neonatology, University of New Mexico, Albuquerque, NM, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6175-7926","authenticated-orcid":true,"given":"Jennifer","family":"Rael","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Division of Neonatology, University of New Mexico, Albuquerque, NM, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","reference":[{"issue":"18","key":"1","first-page":"1420","article-title":"National population-based estimates for major birth defects","volume":"111","author":"C. T. Mai","year":"2019","journal-title":"2010\u20132014. Birth Defects Research"},{"issue":"1","key":"2","doi-asserted-by":"crossref","first-page":"24","DOI":"10.5603\/GP.a2017.0005","article-title":"Congenital diaphragmatic hernia: pathogenesis, prenatal diagnosis and management\u2014literature review","volume":"88","author":"P. Kosi\u0144ski","year":"2017","journal-title":"Ginekologia Polska"},{"key":"3","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2019.09.037"},{"issue":"1","key":"4","first-page":"17","article-title":"Pseudosequestration","volume":"28","author":"R. I. Macpherson","year":"1977","journal-title":"Journal of Canadian Association of Radiologists"},{"key":"5","doi-asserted-by":"publisher","DOI":"10.1016\/s0022-3468(98)90214-7"},{"key":"6","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.180.2.1800438"},{"issue":"1","key":"7","first-page":"95","article-title":"Hepatic pulmonary fusion: a rare association of right-sided congenital diaphragmatic hernia","volume":"26","author":"K. Saurabh","year":"2013","journal-title":"Annals of Gastroenterology"},{"key":"8","doi-asserted-by":"publisher","DOI":"10.1055\/s-0032-1324695"},{"issue":"3","key":"9","doi-asserted-by":"crossref","first-page":"417","DOI":"10.1007\/s10029-012-1042-y","article-title":"Hepatopulmonary fusion in a newborn. An uncommon intraoperatory finding during right congenital diaphragmatic hernia surgery: case description and review of literature","volume":"18","author":"D. Olenik","year":"2014","journal-title":"Hernia"},{"issue":"3","key":"10","doi-asserted-by":"crossref","DOI":"10.21699\/jns.v5i3.370","article-title":"Right congenital diaphragmatic hernia associated with hepatic pulmonary fusion: a case report","volume":"5","author":"R. Laamiri","year":"2016","journal-title":"Journal of Neonatal Surgery"},{"key":"11","doi-asserted-by":"publisher","DOI":"10.1136\/bcr-2016-218227"},{"key":"12","doi-asserted-by":"publisher","DOI":"10.1177\/0300060518759892"},{"key":"13","doi-asserted-by":"publisher","DOI":"10.1080\/00015458.2018.1496568"},{"key":"14","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2006.02.031"},{"key":"15","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2005.10.066"},{"key":"16","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2009.10.090"},{"key":"17","doi-asserted-by":"publisher","DOI":"10.4103\/0189-6725.59357"},{"key":"18","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2010.11.032"},{"key":"19","doi-asserted-by":"publisher","DOI":"10.3109\/15513815.2012.659406"},{"key":"20","doi-asserted-by":"publisher","DOI":"10.1007\/s00247-012-2379-1"},{"key":"21","doi-asserted-by":"publisher","DOI":"10.15537\/smj.2019.9.24378"},{"key":"22","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.174.1.1740229"},{"key":"23","doi-asserted-by":"publisher","DOI":"10.15761\/bdj.1000104"},{"key":"24","doi-asserted-by":"publisher","DOI":"10.1016\/j.clinimag.2009.07.005"}],"container-title":["Case Reports in Pediatrics"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripe\/2020\/8851341.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripe\/2020\/8851341.xml","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cripe\/2020\/8851341.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,10,29]],"date-time":"2020-10-29T22:05:11Z","timestamp":1604009111000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.hindawi.com\/journals\/cripe\/2020\/8851341\/"}},"subtitle":[],"editor":[{"given":"Anselm Chi Wai","family":"Lee","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"editor"}]}],"short-title":[],"issued":{"date-parts":[[2020,10,29]]},"references-count":24,"alternative-id":["8851341","8851341"],"URL":"https:\/\/doi.org\/10.1155\/2020\/8851341","relation":{},"ISSN":["2090-6811","2090-6803"],"issn-type":[{"value":"2090-6811","type":"electronic"},{"value":"2090-6803","type":"print"}],"subject":[],"published":{"date-parts":[[2020,10,29]]}}}