{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,17]],"date-time":"2026-06-17T12:53:03Z","timestamp":1781700783262,"version":"3.54.5"},"reference-count":31,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[2026,5,12]],"date-time":"2026-05-12T00:00:00Z","timestamp":1778544000000},"content-version":"vor","delay-in-days":131,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"},{"start":{"date-parts":[[2026,1,1]],"date-time":"2026-01-01T00:00:00Z","timestamp":1767225600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1.1"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Case Reports in Hepatology"],"published-print":{"date-parts":[[2026,1]]},"abstract":"<jats:sec>\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>Desmoid tumor is a locally aggressive fibroblastic\/myofibroblastic neoplasm frequently arising in deep soft tissues. Although it can be well circumscribed, a desmoid tumor generally infiltrates surrounding tissues and tends to recur locally without metastasizing. While commonly arising in the extremities and abdominal wall, primary hepatic involvement is exceedingly uncommon.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Case Report<\/jats:title>\n                    <jats:p>We report the case of a 20\u2010year\u2010old woman presenting with progressive jaundice, pruritus, weight loss, and abdominal pain. Imaging revealed a 3\u2009\u00d7\u20093\u2009cm hepatic hilar mass with bile duct dilation, initially suggestive of cholangiocarcinoma. Histopathological examination following a tru\u2010cut biopsy demonstrated features consistent with desmoid\u2010type fibromatosis, confirmed by nuclear \u03b2\u2010catenin positivity. Due to clinical deterioration, the patient underwent a left hemihepatectomy. The postoperative course was uneventful. Adjuvant tamoxifen therapy was administered, and follow\u2010up imaging showed no recurrence. Despite the hormonal changes of a subsequent pregnancy, no disease progression was observed.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>This report highlights an extremely rare presentation of desmoid tumor in the hepatic hilum, mimicking malignancy. It underscores the importance of histopathological confirmation, multidisciplinary management, and individualized follow\u2010up strategies, especially in women of reproductive age.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1155\/crhe\/1253334","type":"journal-article","created":{"date-parts":[[2026,5,12]],"date-time":"2026-05-12T11:31:37Z","timestamp":1778585497000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Desmoid Tumor of the Porta Hepatis: A Rare Location With Unusual Clinical Presentation"],"prefix":"10.1155","volume":"2026","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2743-930X","authenticated-orcid":false,"given":"Adila","family":"Adilli","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1314-6642","authenticated-orcid":false,"given":"Altay","family":"Aliyev","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3748-2085","authenticated-orcid":false,"given":"Y\u0131ld\u0131r\u0131m","family":"Karsl\u0131o\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9680-4510","authenticated-orcid":false,"given":"Gulen Bulbul","family":"Dogusoy","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5818-0946","authenticated-orcid":false,"given":"Eldar","family":"Ahmadov","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0009-6958-0051","authenticated-orcid":false,"given":"Parvana","family":"Asgarova","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0002-2496-1941","authenticated-orcid":false,"given":"Farida","family":"Agayarl\u0131","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0004-8400-1867","authenticated-orcid":false,"given":"Iqbal","family":"Babazade","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5527-4434","authenticated-orcid":false,"given":"Arturan","family":"Ibrahimli","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0321-7585","authenticated-orcid":false,"given":"Gunel","family":"Ziyadova","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2026,5,12]]},"reference":[{"key":"e_1_2_10_1_2","doi-asserted-by":"publisher","DOI":"10.1155\/2012\/245671"},{"key":"e_1_2_10_2_2","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.v13.i45.5985"},{"key":"e_1_2_10_3_2","doi-asserted-by":"publisher","DOI":"10.32074\/1591-951x-213"},{"key":"e_1_2_10_4_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.suronc.2007.07.009"},{"key":"e_1_2_10_5_2","article-title":"Desmoid Tumors Complicating Familial Adenomatous Polyposis: A Meta-Analysis Mutation Spectrum of Affected Individuals","volume":"15","author":"Nieuwenhuis M. 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