{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T12:09:11Z","timestamp":1756382951150},"reference-count":16,"publisher":"Hindawi Limited","license":[{"start":{"date-parts":[[2015,1,1]],"date-time":"2015-01-01T00:00:00Z","timestamp":1420070400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/3.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Case Reports in Critical Care"],"published-print":{"date-parts":[[2015]]},"abstract":"<jats:p><jats:italic>Ehlers-Danlos syndrome<\/jats:italic>(EDS) is a rare heterogeneous group of connective tissue disorders. The vascular type (vEDS) is an autosomal dominant disorder caused by heterozygous mutations in the<jats:italic>COL3A1<\/jats:italic>gene predisposing to premature arterial, intestinal, or uterine rupture. We report a case of a 38-year-old woman with a recent diagnosis of vEDS admitted in the Emergency Department with a suspicion of a pyelonephritis that evolved to a cardiopulmonary arrest. A fatal retroperitoneal hematoma related with a haemorrhagic dissection of the right renal artery was found after emergency surgery. This case highlights the need to be aware of the particular characteristics of vEDS, such as a severe vascular complication that can lead to a fatal outcome.<\/jats:p>","DOI":"10.1155\/2015\/804252","type":"journal-article","created":{"date-parts":[[2015,6,15]],"date-time":"2015-06-15T21:00:46Z","timestamp":1434402046000},"page":"1-4","source":"Crossref","is-referenced-by-count":3,"title":["Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome"],"prefix":"10.1155","volume":"2015","author":[{"given":"Filipa","family":"Pereira","sequence":"first","affiliation":[{"name":"Servi\u00e7o de Anestesiologia, Centro Hospitalar do Porto, Largo Professor Abel Salazar, 4099-001 Porto, Portugal"}]},{"given":"Teresa","family":"Cardoso","sequence":"additional","affiliation":[{"name":"Unidade de Cuidados Intensivos Polivalente, Centro Hospitalar do Porto, Largo Professor Abel Salazar, 4099-001 Porto, Portugal"}]},{"given":"Paula","family":"S\u00e1","sequence":"additional","affiliation":[{"name":"Servi\u00e7o de Anestesiologia, Centro Hospitalar do Porto, Largo Professor Abel Salazar, 4099-001 Porto, Portugal"}]}],"member":"98","reference":[{"key":"1","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.07.2370"},{"issue":"4, article 1","key":"2","volume":"17","year":"2011","journal-title":"Dermatology Online Journal"},{"key":"3","doi-asserted-by":"publisher","DOI":"10.1002\/(sici)1096-8628(19980428)77:1lt;31::aid-ajmg8x0003e;3.0.co;2-o"},{"key":"4","doi-asserted-by":"publisher","DOI":"10.1186\/1750-1172-2-32"},{"key":"5","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.34332"},{"key":"6","doi-asserted-by":"publisher","DOI":"10.1111\/j.1556-4029.2010.01521.x"},{"key":"7","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-0004.2012.01858.x"},{"key":"8","doi-asserted-by":"publisher","DOI":"10.1038\/ejhg.2015.32"},{"key":"9","doi-asserted-by":"publisher","DOI":"10.1016\/j.berh.2007.12.005"},{"key":"10","doi-asserted-by":"crossref","first-page":"95","DOI":"10.1007\/978-94-007-7893-1_7","volume":"802","year":"2014","journal-title":"Advances in Experimental Medicine and Biology"},{"key":"11","doi-asserted-by":"publisher","DOI":"10.3941\/jrcr.v8i2.1568"},{"key":"12","doi-asserted-by":"publisher","DOI":"10.1097\/sla.0b013e31829c7a59"},{"key":"13","doi-asserted-by":"publisher","DOI":"10.1016\/j.jvs.2005.03.053"},{"key":"15","doi-asserted-by":"publisher","DOI":"10.1186\/1750-1172-2-28"},{"key":"14","doi-asserted-by":"publisher","DOI":"10.1016\/j.jvs.2009.05.064"},{"key":"16","doi-asserted-by":"publisher","DOI":"10.1016\/s0140-6736(10)60960-9"}],"container-title":["Case Reports in Critical Care"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/downloads.hindawi.com\/journals\/cricc\/2015\/804252.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cricc\/2015\/804252.xml","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/downloads.hindawi.com\/journals\/cricc\/2015\/804252.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2017,6,23]],"date-time":"2017-06-23T13:47:07Z","timestamp":1498225627000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.hindawi.com\/journals\/cricc\/2015\/804252\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015]]},"references-count":16,"alternative-id":["804252","804252"],"URL":"https:\/\/doi.org\/10.1155\/2015\/804252","relation":{},"ISSN":["2090-6420","2090-6439"],"issn-type":[{"value":"2090-6420","type":"print"},{"value":"2090-6439","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015]]}}}