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Endocrinology"],"published-print":{"date-parts":[[2019,8,1]]},"abstract":"<jats:p><jats:italic>Background<\/jats:italic>. The incidence of gastroenteropancreatic neuroendocrine neoplasms (GEP-NENs) has been increasing in the last five decades, but there is no large-scale data regarding these tumours in Portugal. We conducted a cross-sectional, multicentric study in main Portuguese centers to evaluate the clinical, pathological, and therapeutic profile of GEP-NENs. <jats:italic>Methods<\/jats:italic>. From November, 2012, to July, 2014, data from 293 patients diagnosed with GEP-NENs from 15 centers in Portugal was collected and registered in an online electronic platform. <jats:italic>Results<\/jats:italic>. Median age at diagnosis was 56.5 (range: 15-87) years with a preponderance of females (54.6%). The most frequent primary sites were the pancreas (31.1%), jejunum-ileum (24.2%), stomach (13.7%), and rectum (8.5%). Data regarding hormonal status was not available in most patients (82.3%). Stratified by the tumour grade (WHO 2010 classification), we observed 64.0% of NET G1, 24.7% of NET G2, and 11.3% of NEC. Poorly differentiated tumours occurred mainly in older patients (<mml:math xmlns:mml=\"http:\/\/www.w3.org\/1998\/Math\/MathML\" id=\"M1\"><mml:mi>p<\/mml:mi><mml:mo>=<\/mml:mo><mml:mn>0.017<\/mml:mn><\/mml:math>), were larger (<mml:math xmlns:mml=\"http:\/\/www.w3.org\/1998\/Math\/MathML\" id=\"M2\"><mml:mi>p<\/mml:mi><mml:mo>&lt;<\/mml:mo><mml:mn>0.001<\/mml:mn><\/mml:math>), and presented more vascular (<mml:math xmlns:mml=\"http:\/\/www.w3.org\/1998\/Math\/MathML\" id=\"M3\"><mml:mi>p<\/mml:mi><mml:mo>=<\/mml:mo><mml:mn>0.004<\/mml:mn><\/mml:math>) and lymphatic (<mml:math xmlns:mml=\"http:\/\/www.w3.org\/1998\/Math\/MathML\" id=\"M4\"><mml:mi>p<\/mml:mi><mml:mo>=<\/mml:mo><mml:mn>0.001<\/mml:mn><\/mml:math>) invasion. At the time of diagnosis, 44.4% of GEP-NENs presented metastatic disease. Surgery (79.6%) and somatostatin analogues (30.7%) were the most frequently used therapies of GEP-NENs with reported grading. <jats:italic>Conclusion<\/jats:italic>. In general, Portuguese patients with GEP-NENs presented similar characteristics to other populations described in the literature. This cross-sectional study represents the first step to establish a national database of GEP-NENs that may aid in understanding the clinical and epidemiological features of these tumours in Portugal.<\/jats:p>","DOI":"10.1155\/2019\/4518742","type":"journal-article","created":{"date-parts":[[2019,8,1]],"date-time":"2019-08-01T23:31:07Z","timestamp":1564702267000},"page":"1-10","source":"Crossref","is-referenced-by-count":5,"title":["Gastroenteropancreatic Neuroendocrine Neoplasia Characterization in Portugal: Results from the NETs Study Group of the Portuguese Society of Endocrinology, Diabetes and Metabolism"],"prefix":"10.1155","volume":"2019","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8896-305X","authenticated-orcid":true,"given":"A. P.","family":"Santos","sequence":"first","affiliation":[{"name":"Instituto Portugu\u00eas de Oncologia do Porto, Francisco Gentil (IPOPFG), 4200-162 Porto, Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0871-1427","authenticated-orcid":true,"given":"J.","family":"Vinagre","sequence":"additional","affiliation":[{"name":"Instituto de Investiga\u00e7\u00e3o e Inova\u00e7\u00e3o em Sa\u00fade (i3S), 4200-135 Porto, Portugal"},{"name":"Instituto de Patologia e Imunologia Molecular da Universidade do Porto (IPATIMUP), 4200-465 Porto, Portugal"},{"name":"Faculdade de Medicina da Universidade do Porto (FMUP), 4200-319 Porto, Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9607-6998","authenticated-orcid":true,"given":"P.","family":"Soares","sequence":"additional","affiliation":[{"name":"Instituto de Investiga\u00e7\u00e3o e Inova\u00e7\u00e3o em Sa\u00fade (i3S), 4200-135 Porto, Portugal"},{"name":"Instituto de Patologia e Imunologia Molecular da Universidade do Porto (IPATIMUP), 4200-465 Porto, Portugal"},{"name":"Centro Hospitalar de S\u00e3o Jo\u00e3o (CHSJ), 4200-319 Porto, Portugal"}]},{"given":"I.","family":"Claro","sequence":"additional","affiliation":[{"name":"Centro Hospitalar de Lisboa Ocidental (CHLO), 1349-019 Lisboa, Portugal"}]},{"given":"A. C.","family":"Sanches","sequence":"additional","affiliation":[{"name":"Instituto Portugu\u00eas de Oncologia do Porto, Francisco Gentil (IPOPFG), 4200-162 Porto, Portugal"}]},{"given":"L.","family":"Gomes","sequence":"additional","affiliation":[{"name":"Centro Hospitalar e Universit\u00e1rio de Coimbra (CHUC), 3000-075 Coimbra, Portugal"}]},{"given":"I.","family":"Fernandes","sequence":"additional","affiliation":[{"name":"Centro Hospitalar Lisboa Norte, EPE (CHLN), 1649-035 Lisboa, Portugal"},{"name":"Centro Acad\u00e9mico de Medicina de Lisboa (CAML), 1649-035 Lisboa, Portugal"}]},{"given":"A. L.","family":"Catarino","sequence":"additional","affiliation":[{"name":"Hospital da Luz, 1500-650 Lisboa, Portugal"}]},{"given":"J.","family":"Preto","sequence":"additional","affiliation":[{"name":"Faculdade de Medicina da Universidade do Porto (FMUP), 4200-319 Porto, Portugal"},{"name":"Centro Hospitalar de S\u00e3o Jo\u00e3o (CHSJ), 4200-319 Porto, Portugal"}]},{"given":"B. 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