{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T04:26:59Z","timestamp":1777868819743,"version":"3.51.4"},"reference-count":0,"publisher":"S. Karger AG","license":[{"start":{"date-parts":[[2017,8,11]],"date-time":"2017-08-11T00:00:00Z","timestamp":1502409600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/karger.com\/pages\/terms-and-conditions"},{"start":{"date-parts":[[2017,8,11]],"date-time":"2017-08-11T00:00:00Z","timestamp":1502409600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/karger.com\/pages\/terms-and-conditions"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Enzymol Biol Clin"],"abstract":"<jats:p>An abnormal type of G6PD which\ndoes not cause spontaneous hemolysis was\ncharacterized in a single subject of Sicilian\nancestry. Numerous abnormal characteristics\nwere found. The pattern of abnormalities\ndiffers from that displayed by the other G6PD\nvariants previously described, particularly in the Mediterranean basin. This variant\nwas named G6PD Port-Royal. On the basis of immunological reactivity this enzyme\nwas found to have a half normal specific activity. It is likely that the number of\nenzyme molecules per cell is normal.<\/jats:p>","DOI":"10.1159\/000459511","type":"journal-article","created":{"date-parts":[[2017,8,11]],"date-time":"2017-08-11T17:12:59Z","timestamp":1502471579000},"page":"25-32","source":"Crossref","is-referenced-by-count":7,"title":["A New Glucose-6-phosphate Dehydrogenase Variant\n(G6PD Port-Royal)"],"prefix":"10.1159","author":[{"given":"J.-C.","family":"Kaplan","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A.","family":"Hanzlickova-Leroux","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A.-M.","family":"Nicolas","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R.","family":"Rosa","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C.","family":"Weiler","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"G.","family":"Lepercq","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"127","published-online":{"date-parts":[[2017,8,11]]},"container-title":["Enzymologia biologica et clinica"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/karger.com\/article-pdf\/doi\/10.1159\/000459511","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,4,30]],"date-time":"2026-04-30T12:44:29Z","timestamp":1777553069000},"score":1,"resource":{"primary":{"URL":"https:\/\/karger.com\/article\/doi\/10.1159\/000459511"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,8,11]]},"references-count":0,"URL":"https:\/\/doi.org\/10.1159\/000459511","archive":["Portico"],"relation":{},"ISSN":["0425-1423","2504-2572"],"issn-type":[{"value":"0425-1423","type":"print"},{"value":"2504-2572","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,8,11]]}}}