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Karger AG","issue":"3","license":[{"start":{"date-parts":[[2023,8,10]],"date-time":"2023-08-10T00:00:00Z","timestamp":1691625600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"},{"start":{"date-parts":[[2023,8,10]],"date-time":"2023-08-10T00:00:00Z","timestamp":1691625600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["GE Port J Gastroenterol"],"published-print":{"date-parts":[[2024]]},"abstract":"<jats:p>Common variable immunodeficiency enteropathy is a sprue-like disease, which may manifest as a severe malabsorption syndrome with nutritional deficits and cachexia. The authors report a case of a 33-year-old Afghan man, who presented to the emergency department due to chronic watery diarrhea and severe malnourishment. He had been previously misdiagnosed with celiac disease in his early adulthood; however, this was based on inconclusive findings. After a thorough diagnostic workup, the final diagnosis of common variable immunodeficiency enteropathy with symptomatic &lt;i&gt;norovirus&lt;\/i&gt; infection of the gut was obtained during his prolonged hospitalization. A slow but progressive improvement was observed with immunoglobulin replacement therapy, corticotherapy, and ribavirin treatment. This is a noteworthy case of a rare malabsorption disorder, and it reviews important aspects concerning the differential diagnosis of small bowel villous atrophy of unknown etiology, as well as gastrointestinal manifestations of common variable immunodeficiency disorder. <\/jats:p>","DOI":"10.1159\/000531396","type":"journal-article","created":{"date-parts":[[2023,8,10]],"date-time":"2023-08-10T21:01:16Z","timestamp":1691701276000},"page":"196-202","source":"Crossref","is-referenced-by-count":0,"title":["Small Bowel Villous Atrophy in a Young Patient: A Challenging Diagnosis"],"prefix":"10.1159","volume":"31","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-1956-2428","authenticated-orcid":false,"given":"Jo\u00e3o","family":"Correia","sequence":"first","affiliation":[]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0566-6720","authenticated-orcid":false,"given":"Andreia","family":"Freitas","sequence":"additional","affiliation":[]},{"given":"Ant\u00f3nio","family":"Marinho","sequence":"additional","affiliation":[]},{"given":"Ana","family":"Ponte","sequence":"additional","affiliation":[]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2169-1982","authenticated-orcid":false,"given":"Edgar","family":"Afecto","sequence":"additional","affiliation":[]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7171-0139","authenticated-orcid":false,"given":"Manuela","family":"Estevinho","sequence":"additional","affiliation":[]}],"member":"127","published-online":{"date-parts":[[2023,8,10]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.18176\/jiaci.0388"},{"key":"ref2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jim.2022.113342"},{"key":"ref3","doi-asserted-by":"publisher","DOI":"10.1080\/1744666X.2021.2008241"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaip.2015.07.025"},{"key":"ref5","doi-asserted-by":"publisher","DOI":"10.1177\/2050640619844125"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.17235\/reed.2018.5269\/2017"},{"key":"ref7","doi-asserted-by":"publisher","DOI":"10.1136\/bmjgast-2021-000630"},{"key":"ref8","doi-asserted-by":"publisher","DOI":"10.3389\/fimmu.2019.00033"},{"key":"ref9","doi-asserted-by":"publisher","DOI":"10.1038\/ajg.2010.214"},{"key":"ref10","doi-asserted-by":"publisher","DOI":"10.3390\/pediatric13030055"},{"key":"ref11","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.v27.i19.2251"},{"key":"ref12","doi-asserted-by":"publisher","DOI":"10.1016\/j.clim.2020.108362"},{"key":"ref13","doi-asserted-by":"publisher","DOI":"10.1016\/j.cgh.2013.02.024"},{"key":"ref14","doi-asserted-by":"publisher","DOI":"10.3904\/kjim.2014.29.2.256"},{"key":"ref15","doi-asserted-by":"publisher","DOI":"10.1159\/000486448"},{"key":"ref16","doi-asserted-by":"publisher","DOI":"10.37201\/req\/s03.14.2022"},{"key":"ref17","doi-asserted-by":"publisher","DOI":"10.1111\/cei.12600"},{"key":"ref18","doi-asserted-by":"publisher","DOI":"10.1038\/ajg.2014.432"},{"key":"ref19","doi-asserted-by":"publisher","DOI":"10.1111\/cei.12884"},{"key":"ref20","doi-asserted-by":"publisher","DOI":"10.1136\/bcr-2021-241752"},{"key":"ref21","doi-asserted-by":"publisher","DOI":"10.1016\/j.clnu.2016.09.004"},{"key":"ref22","doi-asserted-by":"publisher","DOI":"10.3390\/nu11081888"},{"key":"ref23","doi-asserted-by":"publisher","DOI":"10.3390\/ijerph19159157"}],"container-title":["GE - Portuguese Journal of Gastroenterology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/karger.com\/pjg\/article-pdf\/31\/3\/196\/4236247\/000531396.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/karger.com\/pjg\/article-pdf\/31\/3\/196\/4236247\/000531396.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,4,23]],"date-time":"2025-04-23T15:34:22Z","timestamp":1745422462000},"score":1,"resource":{"primary":{"URL":"https:\/\/karger.com\/article\/doi\/10.1159\/000531396"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,8,10]]},"references-count":23,"journal-issue":{"issue":"3","published-online":{"date-parts":[[2024,6,4]]}},"URL":"https:\/\/doi.org\/10.1159\/000531396","archive":["Portico"],"relation":{},"ISSN":["2341-4545","2387-1954"],"issn-type":[{"type":"print","value":"2341-4545"},{"type":"electronic","value":"2387-1954"}],"subject":[],"published":{"date-parts":[[2023,8,10]]}}}