{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T08:04:36Z","timestamp":1772179476519,"version":"3.50.1"},"reference-count":38,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"8","content-domain":{"domain":["www.ahajournals.org"],"crossmark-restriction":true},"short-container-title":["JAHA"],"published-print":{"date-parts":[[2022,4,19]]},"abstract":"<jats:sec xml:lang=\"en\">\n            <jats:title>Background<\/jats:title>\n            <jats:p xml:lang=\"en\">Duchenne and Becker muscular dystrophy are progressive disorders associated with cardiac mortality. Guidelines recommend routine surveillance; we assess cardiac resource use and identify gaps in care delivery.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec xml:lang=\"en\">\n            <jats:title>Methods and Results<\/jats:title>\n            <jats:p xml:lang=\"en\">Male patients, aged 1 to 18\u00a0years, with Duchenne and Becker muscular dystrophy between January 2013 and December 2017 were identified in the IBM MarketScan Research Database. The cohort was divided into &lt;10 and 10 to 18\u00a0years of age. The primary outcome was rate of annual health care resource per person year. Resource use was assessed for place of service, cardiac testing, and medications. Adjusted incidence rate ratios (IRRs) were estimated using a Poisson regression model. Medication use was measured by proportion of days covered. There were 1386 patients with a median follow\u2010up time of 3.0\u00a0years (interquartile range, 1.9\u20134.7\u00a0years). Patients in the 10 to 18\u00a0years group had only 0.40 (95% CI, 0.35\u20130.45) cardiology visits per person year and 0.66 (95% CI, 0.62\u20130.70) echocardiography\/magnetic resonance imaging per person year. Older patients had higher rates of inpatient admissions (IRR, 1.46; 95% CI, 1.03\u20132.09), outpatient cardiology visits (IRR, 2.0; 95% CI, 1.66\u20132.40), cardiac imaging (IRR, 1.59; 95% CI, 1.40\u20131.80), and Holter monitoring (IRR, 3.33; 95% CI, 2.35\u20134.73). A proportion of days covered &gt;80% for angiotensin\u2010converting enzyme inhibitors\/angiotensin receptor blockers was observed in 13.6% (419\/3083) of total person years among patients in the 10 to 18\u00a0years group.<\/jats:p>\n          <\/jats:sec>\n          <jats:sec xml:lang=\"en\">\n            <jats:title>Conclusions<\/jats:title>\n            <jats:p xml:lang=\"en\">Children 10 to 18\u00a0years of age have higher rates of cardiac resource use compared with those &lt;10\u00a0years of age. However, rates in both age groups fall short of guidelines. Opportunities exist to identify barriers to resource use and optimize cardiac care for patients with Duchenne and Becker muscular dystrophy.<\/jats:p>\n          <\/jats:sec>","DOI":"10.1161\/jaha.121.024722","type":"journal-article","created":{"date-parts":[[2022,4,12]],"date-time":"2022-04-12T09:48:48Z","timestamp":1649756928000},"update-policy":"https:\/\/doi.org\/10.1161\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":4,"title":["Health Care Use of Cardiac Specialty Care in Children With Muscular Dystrophy in the United States"],"prefix":"10.1161","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-5777-9607","authenticated-orcid":false,"given":"Erika J.","family":"Mejia","sequence":"first","affiliation":[{"name":"Division of Cardiology Children\u2019s Hospital of PhiladelphiaUniversity of Pennsylvania Perelman School of Medicine Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1582-9797","authenticated-orcid":false,"given":"Kimberly Y.","family":"Lin","sequence":"additional","affiliation":[{"name":"Division of Cardiology Children\u2019s Hospital of PhiladelphiaUniversity of Pennsylvania Perelman School of Medicine Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Oluwatimilehin","family":"Okunowo","sequence":"additional","affiliation":[{"name":"Data Science &amp; 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