{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,5]],"date-time":"2026-10-05T21:56:03Z","timestamp":1791237363735,"version":"4.1.0"},"reference-count":35,"publisher":"American Society for Clinical Investigation","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. Clin. Invest."],"published-print":{"date-parts":[[2014,3,3]]},"DOI":"10.1172\/jci71919","type":"journal-article","created":{"date-parts":[[2014,2,2]],"date-time":"2014-02-02T06:00:42Z","timestamp":1391320842000},"page":"1144-1157","source":"Crossref","is-referenced-by-count":80,"title":["Chemical chaperone ameliorates pathological protein aggregation in plectin-deficient muscle"],"prefix":"10.1172","volume":"124","author":[{"given":"Lilli","family":"Winter","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ilona","family":"Staszewska","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eva","family":"Mihailovska","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Irmgard","family":"Fischer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Wolfgang H.","family":"Goldmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rolf","family":"Schr\u00f6der","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gerhard","family":"Wiche","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"232","published-online":{"date-parts":[[2014,2,3]]},"reference":[{"key":"B1","doi-asserted-by":"publisher","DOI":"10.1017\/S1462399408000793"},{"key":"B2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1750-3639.2009.00289.x"},{"key":"B3","doi-asserted-by":"publisher","DOI":"10.1007\/s00401-012-1026-0"},{"key":"B4","doi-asserted-by":"publisher","DOI":"10.4161\/bioa.1.1.14630"},{"key":"B5","doi-asserted-by":"publisher","DOI":"10.1007\/s00418-013-1102-0"},{"key":"B6","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/8.13.2461"},{"key":"B7","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200604179"},{"key":"B8","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200711058"},{"key":"B9","doi-asserted-by":"publisher","DOI":"10.1101\/gad.11.23.3143"},{"key":"B10","doi-asserted-by":"publisher","DOI":"10.1016\/j.yexcr.2009.07.005"},{"key":"B11","doi-asserted-by":"publisher","DOI":"10.1016\/0092-8674(95)90049-7"},{"key":"B12","doi-asserted-by":"publisher","DOI":"10.1111\/j.1742-4658.2005.04708.x"},{"key":"B13","doi-asserted-by":"crossref","first-page":"297","DOI":"10.1007\/s00401-002-0559-z","volume":"104","author":"Fischer","year":"2002","journal-title":"Acta Neuropathol."},{"key":"B14","doi-asserted-by":"crossref","first-page":"2099","DOI":"10.1242\/jcs.112.13.2099","volume":"112","author":"Perng","year":"1999","journal-title":"J Cell Sci."},{"key":"B15","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1007\/978-1-61737-967-3_3","volume":"705","author":"de Marco","year":"2011","journal-title":"Methods Mol Biol."},{"key":"B16","doi-asserted-by":"crossref","first-page":"1684","DOI":"10.1038\/jid.2011.93","volume":"131","author":"Chamcheu","year":"2011","journal-title":"J Invest Dermatol."},{"key":"B17","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbrc.2012.02.083"},{"key":"B18","doi-asserted-by":"crossref","first-page":"316","DOI":"10.1016\/j.bbrc.2013.03.048","volume":"434","author":"Soltow","year":"2013","journal-title":"Biochem Biophys Res Commun."},{"key":"B19","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1007\/s00401-012-1057-6","volume":"125","author":"Clemen","year":"2013","journal-title":"Acta Neuropathol."},{"key":"B20","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200605172"},{"key":"B21","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M608473200"},{"key":"B22","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/aws200"},{"key":"B23","doi-asserted-by":"publisher","DOI":"10.1111\/j.1750-3639.2009.00288.x"},{"key":"B24","doi-asserted-by":"publisher","DOI":"10.1016\/j.biocel.2012.05.024"},{"key":"B25","doi-asserted-by":"publisher","DOI":"10.1101\/gad.1657108"},{"key":"B26","first-page":"997","volume":"16","author":"Gong","year":"2010","journal-title":"Mol Vis."},{"key":"B27","doi-asserted-by":"crossref","first-page":"1491","DOI":"10.1111\/j.1471-4159.2006.04440.x","volume":"101","author":"Inden","year":"2007","journal-title":"J Neurochem."},{"key":"B28","doi-asserted-by":"publisher","DOI":"10.1164\/ajrccm.157.2.9706088"},{"key":"B29","doi-asserted-by":"publisher","DOI":"10.1124\/mol.104.001339"},{"key":"B30","doi-asserted-by":"publisher","DOI":"10.1126\/science.1128294"},{"key":"B31","doi-asserted-by":"publisher","DOI":"10.1038\/npp.2008.229"},{"key":"B32","doi-asserted-by":"publisher","DOI":"10.1016\/j.parkreldis.2009.03.002"},{"key":"B33","doi-asserted-by":"publisher","DOI":"10.1016\/j.ymgme.2010.03.014"},{"key":"B34","doi-asserted-by":"publisher","DOI":"10.1016\/j.cell.2008.05.049"},{"key":"B35","doi-asserted-by":"crossref","first-page":"261","DOI":"10.1016\/S0091-679X(08)60382-9","volume":"52","author":"Rando","year":"1997","journal-title":"Methods Cell Biol."}],"container-title":["Journal of Clinical Investigation"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.jci.org\/articles\/view\/71919\/files\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,8,3]],"date-time":"2023-08-03T13:25:54Z","timestamp":1691069154000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.jci.org\/articles\/view\/71919"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014,2,3]]},"references-count":35,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2014,3,3]]}},"URL":"https:\/\/doi.org\/10.1172\/jci71919","relation":{"has-review":[{"id-type":"doi","id":"10.3410\/f.718262109.793548163","asserted-by":"object"}]},"ISSN":["0021-9738"],"issn-type":[{"value":"0021-9738","type":"print"}],"subject":[],"published":{"date-parts":[[2014,2,3]]}}}