{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,26]],"date-time":"2026-03-26T04:58:20Z","timestamp":1774501100519,"version":"3.50.1"},"reference-count":48,"publisher":"American Society for Clinical Investigation","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. Clin. Invest."],"published-print":{"date-parts":[[2004,1,15]]},"DOI":"10.1172\/jci200420138","type":"journal-article","created":{"date-parts":[[2004,1,15]],"date-time":"2004-01-15T21:58:03Z","timestamp":1074203883000},"page":"231-242","source":"Crossref","is-referenced-by-count":254,"title":["Axonal degeneration in paraplegin-deficient mice is associated with abnormal mitochondria and impairment of axonal transport"],"prefix":"10.1172","volume":"113","author":[{"given":"Fatima","family":"Ferreirinha","sequence":"first","affiliation":[]},{"given":"Angelo","family":"Quattrini","sequence":"additional","affiliation":[]},{"given":"Marinella","family":"Pirozzi","sequence":"additional","affiliation":[]},{"given":"Valentina","family":"Valsecchi","sequence":"additional","affiliation":[]},{"given":"Giorgia","family":"Dina","sequence":"additional","affiliation":[]},{"given":"Vania","family":"Broccoli","sequence":"additional","affiliation":[]},{"given":"Alberto","family":"Auricchio","sequence":"additional","affiliation":[]},{"given":"Fiorella","family":"Piemonte","sequence":"additional","affiliation":[]},{"given":"Giulia","family":"Tozzi","sequence":"additional","affiliation":[]},{"given":"Laura","family":"Gaeta","sequence":"additional","affiliation":[]},{"given":"Giorgio","family":"Casari","sequence":"additional","affiliation":[]},{"given":"Andrea","family":"Ballabio","sequence":"additional","affiliation":[]},{"given":"Elena I.","family":"Rugarli","sequence":"additional","affiliation":[]}],"member":"232","reference":[{"key":"B1","doi-asserted-by":"publisher","DOI":"10.1038\/ng0794-351"},{"key":"B2","doi-asserted-by":"crossref","first-page":"1507","DOI":"10.1212\/WNL.46.6.1507","volume":"46","author":"Fink","year":"1996","journal-title":"Neurology."},{"key":"B3","journal-title":""},{"key":"B4","doi-asserted-by":"crossref","first-page":"313","DOI":"10.1097\/00019052-199708000-00006","volume":"10","author":"Fink","year":"1997","journal-title":"Curr. Opin. Neurol."},{"key":"B5","journal-title":""},{"key":"B6","doi-asserted-by":"publisher","DOI":"10.1016\/S0959-437X(00)00199-4"},{"key":"B7","doi-asserted-by":"publisher","DOI":"10.1016\/S0092-8674(00)81203-9"},{"key":"B8","doi-asserted-by":"publisher","DOI":"10.1016\/S0092-8674(00)81271-4"},{"key":"B9","doi-asserted-by":"publisher","DOI":"10.1002\/bies.950170710"},{"key":"B10","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1101\/gr.9.1.27","volume":"9","author":"Neuwald","year":"1999","journal-title":"Genome Res."},{"key":"B11","doi-asserted-by":"publisher","DOI":"10.1042\/BST0290431"},{"key":"B12","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1212\/WNL.56.4.467","volume":"56","author":"McDermott","year":"2001","journal-title":"Neurology."},{"key":"B13","doi-asserted-by":"publisher","DOI":"10.1086\/339935"},{"key":"B14","journal-title":""},{"key":"B15","doi-asserted-by":"crossref","first-page":"752","DOI":"10.1038\/jcbfm.1987.130","volume":"7","author":"Rosenthal","year":"1987","journal-title":"J. Cereb. Blood Flow Metab."},{"key":"B16","doi-asserted-by":"publisher","DOI":"10.1006\/abio.1999.4317"},{"key":"B17","doi-asserted-by":"publisher","DOI":"10.1203\/00006450-199011000-00027"},{"key":"B18","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.151.5.1035"},{"key":"B19","doi-asserted-by":"publisher","DOI":"10.1038\/85454"},{"key":"B20","journal-title":""},{"key":"B21","journal-title":""},{"key":"B22","doi-asserted-by":"publisher","DOI":"10.1016\/0168-0102(95)00895-9"},{"key":"B23","journal-title":""},{"key":"B24","doi-asserted-by":"publisher","DOI":"10.1016\/0006-8993(82)90244-X"},{"key":"B25","doi-asserted-by":"publisher","DOI":"10.1086\/344206"},{"key":"B26","doi-asserted-by":"publisher","DOI":"10.1093\/embo-reports\/kvf113"},{"key":"B27","doi-asserted-by":"publisher","DOI":"10.1016\/S0960-9822(01)00011-2"},{"key":"B28","doi-asserted-by":"publisher","DOI":"10.1038\/nature01633"},{"key":"B29","doi-asserted-by":"publisher","DOI":"10.1126\/science.283.5407.1493"},{"key":"B30","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200211046"},{"key":"B31","doi-asserted-by":"publisher","DOI":"10.1093\/emboj\/21.7.1616"},{"key":"B32","doi-asserted-by":"crossref","first-page":"d91","DOI":"10.2741\/A118","volume":"1","author":"Hollenbeck","year":"1996","journal-title":"Front. Biosci."},{"key":"B33","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.144.4.711"},{"key":"B34","doi-asserted-by":"publisher","DOI":"10.1038\/79944"},{"key":"B35","doi-asserted-by":"publisher","DOI":"10.1038\/79936"},{"key":"B36","doi-asserted-by":"publisher","DOI":"10.1126\/science.81524"},{"key":"B37","doi-asserted-by":"publisher","DOI":"10.1038\/81701"},{"key":"B38","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-510X(00)00422-6"},{"key":"B39","doi-asserted-by":"publisher","DOI":"10.1016\/S0092-8674(01)00244-6"},{"key":"B40","doi-asserted-by":"publisher","DOI":"10.1086\/302986"},{"key":"B41","doi-asserted-by":"publisher","DOI":"10.1086\/302962"},{"key":"B42","doi-asserted-by":"crossref","first-page":"101","DOI":"10.1242\/jcs.1993.Supplement_17.15","volume":"17","author":"Xu","year":"1993","journal-title":"J. Cell Sci. Suppl."},{"key":"B43","doi-asserted-by":"publisher","DOI":"10.1016\/S0896-6273(00)81108-3"},{"key":"B44","doi-asserted-by":"publisher","DOI":"10.1016\/0092-8674(83)90189-7"},{"key":"B45","doi-asserted-by":"publisher","DOI":"10.1038\/ng1123"},{"key":"B46","doi-asserted-by":"publisher","DOI":"10.1016\/S0896-6273(02)00696-7"},{"key":"B47","doi-asserted-by":"publisher","DOI":"10.1086\/344210"},{"key":"B48","doi-asserted-by":"publisher","DOI":"10.1126\/science.280.5369.1610"}],"container-title":["Journal of Clinical Investigation"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.jci.org\/articles\/view\/20138\/files\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,8,3]],"date-time":"2023-08-03T16:55:17Z","timestamp":1691081717000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.jci.org\/articles\/view\/20138"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2004,1,15]]},"references-count":48,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2004,1,15]]}},"URL":"https:\/\/doi.org\/10.1172\/jci200420138","relation":{},"ISSN":["0021-9738"],"issn-type":[{"value":"0021-9738","type":"print"}],"subject":[],"published":{"date-parts":[[2004,1,15]]}}}