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According to the criteria introduced by Sillence, type I was the most common form of OI. Of the patients with normal hearing on audiometry, 17.1% reported subjective hearing loss, and 19.1% of the patients with impaired hearing did not recognize it. On audiometry, 57.9% of the patients had hearing loss, which was progressive, often of mixed type, and mostly bilateral, and began in the second to fourth decades of life. The frequency or severity of the hearing loss was not correlated with any other clinical features of OI. Hearing loss is common, affecting patients with all types of OI. Subjective misjudgment of hearing ability supports the need for repeated audiometry in all OI patients. A baseline study at the age of 10 years followed by audiograms every third year thereafter is recommended.<\/jats:p>","DOI":"10.1177\/000348940211101014","type":"journal-article","created":{"date-parts":[[2014,10,3]],"date-time":"2014-10-03T14:40:52Z","timestamp":1412347252000},"page":"939-946","source":"Crossref","is-referenced-by-count":113,"title":["Hearing Loss in Finnish Adults with Osteogenesis Imperfecta: A Nationwide Survey"],"prefix":"10.1177","volume":"111","author":[{"given":"Kaija","family":"Kuurila","sequence":"first","affiliation":[{"name":"Vaasa, Finland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Reijo","family":"Johansson","sequence":"additional","affiliation":[{"name":"Turku, Finland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ilkka","family":"Kaitila","sequence":"additional","affiliation":[{"name":"Helsinki, Finland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Reidar","family":"Gr\u00e9nman","sequence":"additional","affiliation":[{"name":"Turku, Finland"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2002,10]]},"reference":[{"key":"e_1_2_1_2_2","first-page":"317","volume-title":"Connective tissue and its heritable disorders: Molecular, genetic, and medical aspects","author":"Byers PH","year":"1993","unstructured":"Byers PH. 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