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The other individual is also profoundly hearing impaired, but has well-developed speech, vestibular areflexia, and retinitis pigmentosa sine pigmento (RPSP). These findings suggest that Usher syndrome type III can be clinically misdiagnosed as either Usher type I or II; that Usher syndrome patients who are profoundly hearing impaired and have normal vestibular function should be tested for USH3 mutations; and that RPA and RPSP can occur as fundoscopic manifestations of pigmentary retinopathy in Usher syndrome.<\/jats:p>","DOI":"10.1177\/000348940311200608","type":"journal-article","created":{"date-parts":[[2014,10,3]],"date-time":"2014-10-03T14:40:52Z","timestamp":1412347252000},"page":"525-530","source":"Crossref","is-referenced-by-count":26,"title":["Usher Syndrome Type III Can Mimic other Types of Usher Syndrome"],"prefix":"10.1177","volume":"112","author":[{"given":"Ronald J. 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