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Classic inner ear aplasias are discussed, including Michel, Mondini, Alexander and Scheibe. A case illustrating close resemblance between a genetically induced Scheibe malformation and rubella inner ear deformities is presented. A variety of ear disorders acquired during intrauterine or neonatal life, including cytomegalic inclusion disease, hypoxia, erythroblastosis fetalis and later-onset genetic disorders are also discussed. Illustrative case histories are presented as well as priorities for future investigations into the pathology of congenital and genetic hearing loss.<\/jats:p>","DOI":"10.1177\/00034894800890s511","type":"journal-article","created":{"date-parts":[[2017,1,6]],"date-time":"2017-01-06T07:32:21Z","timestamp":1483687941000},"page":"31-42","source":"Crossref","is-referenced-by-count":15,"title":["Pathology of Congenital Deafness"],"prefix":"10.1177","volume":"89","author":[{"given":"LaVonne","family":"Bergstrom","sequence":"first","affiliation":[{"name":"Los Angeles, 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