{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,18]],"date-time":"2025-10-18T10:23:56Z","timestamp":1760783036299,"version":"build-2065373602"},"reference-count":12,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[1989,5,1]],"date-time":"1989-05-01T00:00:00Z","timestamp":609984000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Parenter Enteral Nutr"],"published-print":{"date-parts":[[1989,5]]},"abstract":"<jats:p>A 27\u2010yr\u2010old woman with the myopathic form of acid maltase deficiency (AMD) developed severe respiratory insufficiency after a crash diet resulting in a 6\u2010kg weight loss. While being maintained on home ventilation, an hypercaloric high\u2010protein, low\u2010carbohydrate diet (1800\u20132000 cal; 28% carbohydrates, 55% fat, 17% protein with 1.7 g protein\/kg body weight) was instituted. This ameliorated her condition up to a level where useful life was possible and ventilation could be diminished. (<jats:italic>Journal of Parenteral and Enteral Nutrition<\/jats:italic> <jats:bold>13:<\/jats:bold>321\u2013323, 1989)<\/jats:p>","DOI":"10.1177\/0148607189013003321","type":"journal-article","created":{"date-parts":[[2008,5,14]],"date-time":"2008-05-14T19:51:26Z","timestamp":1210794686000},"page":"321-323","source":"Crossref","is-referenced-by-count":15,"title":["Respiratory Insufficiency in Acid Maltase Deficiency: The Effect of High Protein Diet"],"prefix":"10.1002","volume":"13","author":[{"given":"H.E.","family":"Demey","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J.P.","family":"Van Meerbeeck","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.F.J.","family":"Vandewoude","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A.M.","family":"Prov\u00e9","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J.J.","family":"Martin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"L.L.","family":"Bossaert","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[1989,5]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(80)90157-6"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880060306"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.33.1.34"},{"key":"e_1_2_1_5_1","first-page":"328","article-title":"Acid maltase deficiency in an adult. Evidence for improvement in respiratory function with high\u2010protein dietary therapy","volume":"134","author":"Margolis ML","year":"1986","journal-title":"Am Rev Resp Dis"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.49.9.1011"},{"key":"e_1_2_1_7_1","first-page":"152","article-title":"Acid maltase deficiency. A study of five cases","volume":"86","author":"Lenders MB","year":"1986","journal-title":"Acta Neurol Belg"},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/108.4.845"},{"key":"e_1_2_1_9_1","doi-asserted-by":"publisher","DOI":"10.1097\/00007611-198702000-00016"},{"key":"e_1_2_1_10_1","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1016\/S0272-5231(21)00323-3","article-title":"Malnutrition and the respiratory muscles","volume":"7","author":"Rochester DF","year":"1986","journal-title":"Clin Chest Med"},{"key":"e_1_2_1_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(87)90377-9"},{"key":"e_1_2_1_12_1","first-page":"5","article-title":"Respiratory muscle strength and maximal voluntary ventilation in undernourished patients","volume":"126","author":"Arora NS","year":"1982","journal-title":"Am Rev Resp Dis"},{"key":"e_1_2_1_13_1","doi-asserted-by":"crossref","first-page":"64","DOI":"10.1152\/jappl.1982.52.1.64","article-title":"Effect of body weight and muscularity on human diaphragm muscle mass, thickness and area","volume":"52","author":"Arora NS","year":"1982","journal-title":"J Appl Physiol"}],"container-title":["Journal of Parenteral and Enteral Nutrition"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/aspenjournals.onlinelibrary.wiley.com\/doi\/pdf\/10.1177\/0148607189013003321","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,10,16]],"date-time":"2025-10-16T18:56:42Z","timestamp":1760641002000},"score":1,"resource":{"primary":{"URL":"https:\/\/aspenjournals.onlinelibrary.wiley.com\/doi\/10.1177\/0148607189013003321"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1989,5]]},"references-count":12,"journal-issue":{"issue":"3","published-print":{"date-parts":[[1989,5]]}},"alternative-id":["10.1177\/0148607189013003321"],"URL":"https:\/\/doi.org\/10.1177\/0148607189013003321","archive":["Portico"],"relation":{},"ISSN":["0148-6071","1941-2444"],"issn-type":[{"type":"print","value":"0148-6071"},{"type":"electronic","value":"1941-2444"}],"subject":[],"published":{"date-parts":[[1989,5]]}}}