{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T12:40:58Z","timestamp":1760964058618,"version":"build-2065373602"},"reference-count":23,"publisher":"Wiley","issue":"3P1","license":[{"start":{"date-parts":[[2016,11,8]],"date-time":"2016-11-08T00:00:00Z","timestamp":1478563200000},"content-version":"vor","delay-in-days":8104,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["aao-hnsfjournals.onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Otolaryngol.--head neck surg."],"published-print":{"date-parts":[[1994,9]]},"abstract":"<jats:p>Townes\u2010Brocks syndrome is an autosomal dominant syndrome consisting of anomalies affecting the ear, hand, foot, anus, and kidney. Anomalies affecting the ear include lop ear, preauricular skin tags, ossicular abnormalities, and a mixed hearing loss. The hearing loss in Townes\u2010Brocks syndrome is predominantly sensorineural, affects high\u2010frequency thresholds more than low\u2010frequency thresholds, and has a variable (usually small) conductive component. The sensorineural component of the hearing loss is slowly progressive. It is typically in the mild range (20 to 40\u00a0dB hearing level) during early childhood and progresses to the moderate hearing loss range (40 to 60\u00a0dB hearing level) by early adulthood. We present a description of the otologic manifestations and an analysis of audiologic findings in six members of a family With Townes\u2010Brocks syndrome.<\/jats:p>","DOI":"10.1177\/01945998941113p103","type":"journal-article","created":{"date-parts":[[2015,11,25]],"date-time":"2015-11-25T06:54:07Z","timestamp":1448434447000},"page":"175-180","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":13,"title":["Hearing Loss in Townes\u2010Brocks Syndrome"],"prefix":"10.1002","volume":"111","author":[{"given":"David R.","family":"Rossmiller","sequence":"first","affiliation":[{"name":"Division of Otolaryngology\u2010Head and Neck Surgery University of Wisconsin Madison Wisconsin"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas R.","family":"Pasic","sequence":"additional","affiliation":[{"name":"School of Medicine University of Wisconsin Madison 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