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Vulvar tumors represent only 4% of all gynecological neoplasms, and they are fourth in frequency after tumors of the cervix, uterus, and ovary. Ninety-eight percent of all vulvar tumors are benign and only 2% are malignant. Sarcomas of the vulva comprise approximately 1\u20133% of all vulvar cancers. They are characterized by rapid growth, high metastatic potential, frequent recurrences, aggressive behavior, and high mortality rate. In Part 1 of this paper, we presented the most common forms of sarcoma of the vulva: leiomyosarcoma, epithelioid sarcoma, malignant rhabdoid tumor, and rhabdomyosarcoma. The second part of this review will focus mainly on the rarest variants of vulvar sarcoma: low-grade fibromyxoid sarcoma, synovial sarcoma, monophasic synovial sarcoma, carcinosarcoma, Ewing sarcoma, myeloid sarcoma, dermatofibrosarcoma protuberans, malignant fibrous histiocytoma, angiomatoid fibrous histiocytoma, liposarcoma, malignant peripheral nerve sheath tumor, and malignant mesothelioma.<\/jats:p>","DOI":"10.1177\/0394632015575977","type":"journal-article","created":{"date-parts":[[2015,3,27]],"date-time":"2015-03-27T15:16:51Z","timestamp":1427469411000},"page":"178-186","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":18,"title":["Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2"],"prefix":"10.1177","volume":"28","author":[{"given":"AA","family":"Chokoeva","sequence":"first","affiliation":[{"name":"Onkoderma-Policlinic for Dermatology and Dermatologic Surgery, Sofia, Bulgaria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"G","family":"Tchernev","sequence":"additional","affiliation":[{"name":"Policlinic for Dermatology and Venereology, University Hospital Lozenetz, Sofia, Bulgaria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"JC","family":"Cardoso","sequence":"additional","affiliation":[{"name":"Department of Dermatology, University Hospital of Coimbra, Coimbra, Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"JW","family":"Patterson","sequence":"additional","affiliation":[{"name":"Department of Dermatology, University of Virginia Health System, Charlottesville, VA, USA"},{"name":"Department of Pathology, University of Virginia Health System, Charlottesville, VA, 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