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In addition, there was improvement in the myoclonic jerks, sleep pattern, and developmental progress. Corticosteroids appeared to have a broad benefit on the epileptic encephalopathy. We believe that these cases pose a challenge to the conventional management of intractable epilepsy in Angelman syndrome.<\/jats:p>","DOI":"10.1177\/0883073808331344","type":"journal-article","created":{"date-parts":[[2009,8,7]],"date-time":"2009-08-07T18:34:01Z","timestamp":1249670041000},"page":"952-958","source":"Crossref","is-referenced-by-count":17,"title":["Benefit of Corticosteroid Therapy in Angelman Syndrome"],"prefix":"10.1177","volume":"24","author":[{"given":"Katharine M. L.","family":"Forrest","sequence":"first","affiliation":[{"name":"Evelina Children's Hospital, Westminster Bridge Road, London, United Kingdom,"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Helen","family":"Young","sequence":"additional","affiliation":[{"name":"T.Y. 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