{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,6]],"date-time":"2026-01-06T02:06:39Z","timestamp":1767665199387,"version":"3.38.0"},"reference-count":8,"publisher":"SAGE Publications","issue":"1","license":[{"start":{"date-parts":[[2000,1,1]],"date-time":"2000-01-01T00:00:00Z","timestamp":946684800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiovascular Surgery"],"published-print":{"date-parts":[[2000,1]]},"abstract":"<jats:p> Ehlers\u2014Danlos syndrome type IV is a distinctive syndrome in which thin and fragile skin, premature ageing, bruising and scarring are combined with lethal or life-threatening arterial weakness Aortic rupture either at the aortic root and arch, or sometimes lower down the artery, are Darticularly characteristic. Even quite minor injury can produce dangerous vascular tearing and damage Technical difficulties encountered in arterial repair or venous ligature are particularly worrvinq The authors report the treatment of a ruptured type A aortic dissection associated with Ehlers\u2014Danlos syndrome where the extreme fragility of the tissues and tendency to bleed posed a difficult task for the surgeon. <\/jats:p>","DOI":"10.1177\/096721090000800112","type":"journal-article","created":{"date-parts":[[2024,9,22]],"date-time":"2024-09-22T10:05:26Z","timestamp":1726999526000},"page":"75-78","source":"Crossref","is-referenced-by-count":3,"title":["Emergency Repair of Type a Aortic Dissection in Type IV Ehlers\u2014Danlos Syndrome"],"prefix":"10.1177","volume":"8","author":[{"given":"R.","family":"Ascione","sequence":"first","affiliation":[{"name":"Bristol Heart Institute, Bristol Royal Infirmary, Bristol BS2 8HW, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"W.J.","family":"Gomes","sequence":"additional","affiliation":[{"name":"Bristol Heart Institute, Bristol Royal Infirmary, Bristol BS2 8HW, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.","family":"Bates","sequence":"additional","affiliation":[{"name":"Bristol Heart Institute, Bristol Royal Infirmary, Bristol BS2 8HW, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J.L.","family":"Shannon","sequence":"additional","affiliation":[{"name":"Department of Histopathology, Bristol Royal Infirmary, Bristol, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"F.M.","family":"Pope","sequence":"additional","affiliation":[{"name":"Institute of Medical Genetics, Cardiff, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"G.D.","family":"Angelini","sequence":"additional","affiliation":[{"name":"Bristol Heart Institute, Bristol Royal Infirmary, Bristol BS2 8HW, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2000,1,1]]},"reference":[{"key":"bibr1-096721090000800112","doi-asserted-by":"publisher","DOI":"10.1055\/s-0038-1650281"},{"key":"bibr2-096721090000800112","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2230.1988.tb00709.x"},{"key":"bibr3-096721090000800112","first-page":"351","volume-title":"Connective Tissue and its Heritable Disorders. Molecular, Genetic and Medical Aspects","author":"Steinmann B.","year":"1993"},{"key":"bibr4-096721090000800112","first-page":"163","volume":"162","author":"Bergqvist D.","year":"1996","journal-title":"European Journal of Surgery"},{"key":"bibr5-096721090000800112","first-page":"530","volume":"29","author":"Serry C.","year":"1988","journal-title":"Journal of Cardiovascular Surgery"},{"key":"bibr6-096721090000800112","first-page":"647","volume":"29","author":"Raman J.","year":"1988","journal-title":"Journal of Cardiovascular Surgery"},{"key":"bibr7-096721090000800112","doi-asserted-by":"publisher","DOI":"10.1016\/S0950-821X(05)80766-2"},{"key":"bibr8-096721090000800112","first-page":"827","volume":"60","author":"Mattar S. G.","year":"1994","journal-title":"American Surgery"}],"container-title":["Cardiovascular Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/096721090000800112","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/096721090000800112","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,3,1]],"date-time":"2025-03-01T22:25:22Z","timestamp":1740867922000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/096721090000800112"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2000,1]]},"references-count":8,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2000,1]]}},"alternative-id":["10.1177\/096721090000800112"],"URL":"https:\/\/doi.org\/10.1177\/096721090000800112","relation":{},"ISSN":["0967-2109"],"issn-type":[{"type":"print","value":"0967-2109"}],"subject":[],"published":{"date-parts":[[2000,1]]}}}