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These complications were managed conservatively. Unfortunately the patient died of a pulmonary infection and a multi-organ failure syndrome several days after her admission. <\/jats:p>","DOI":"10.1177\/096721090201000622","type":"journal-article","created":{"date-parts":[[2022,9,13]],"date-time":"2022-09-13T13:06:22Z","timestamp":1663074382000},"page":"640-643","source":"Crossref","is-referenced-by-count":0,"title":["Fatal Cardiovascular Complications in a Patient with Ehlers-Danlos Syndrome Type IV and Dextrocardia"],"prefix":"10.1177","volume":"10","author":[{"given":"S.","family":"Jazayeri","sequence":"first","affiliation":[{"name":"Service de Chirurgie Cardio-vasculaire, 2 Bd Marechal de Lattre de Tassigny, BP 1542. 21034 Dijon Cedex, France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M. 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