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We present a unique case of Hurler-Scheie syndrome with multisuture craniosynostosis and elevated ICP, without ventriculomegaly, where elevated ICP was successfully treated with extensive cranial vault expansion and shunt placement was avoided. Patients with MPS should be evaluated for craniosynostosis, and calvarial vault expansion may be considered as a viable treatment alternative to CSF shunting for elevated ICP in select patients.<\/jats:p>","DOI":"10.1177\/1055665618777906","type":"journal-article","created":{"date-parts":[[2018,5,23]],"date-time":"2018-05-23T14:48:50Z","timestamp":1527086930000},"page":"395-399","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["Markedly Elevated Intracranial Pressure Treated With Cranial Vault Expansion, Instead of CSF Shunting, in a Child With Hurler-Scheie Syndrome and Multiple Suture Craniosynostosis"],"prefix":"10.1177","volume":"56","author":[{"given":"Jessica A.","family":"Ching","sequence":"first","affiliation":[{"name":"Division of Plastic Surgery, Department of Surgery, University of Florida, Gainesville, FL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jared S.","family":"Troy","sequence":"additional","affiliation":[{"name":"Division of Plastic Surgery, Department of Surgery, University of South Florida Morsani College of Medicine, Tampa, FL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ernesto J.","family":"Ruas","sequence":"additional","affiliation":[{"name":"Division of Plastic Surgery, Department of Surgery, University of South Florida Morsani College of Medicine, Tampa, FL, USA"},{"name":"Division of Plastic Surgery, Johns Hopkins Medicine, All Children\u2019s Hospital, St Petersburg, FL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Joshua M.","family":"Beckman","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery and Brain Repair, University of South Florida Morsani College of Medicine, Tampa, FL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gerald F.","family":"Tuite","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery and Brain Repair, University of South Florida Morsani College of Medicine, Tampa, FL, USA"},{"name":"Institute for Brain Protection Sciences, Johns Hopkins Medicine, All Children\u2019s Hospital, St Petersburg, FL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2018,5,23]]},"reference":[{"key":"e_1_3_2_2_1","doi-asserted-by":"publisher","DOI":"10.1227\/NEU.0b013e3181f8c11d"},{"key":"e_1_3_2_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/0039-6257(82)90111-4"},{"key":"e_1_3_2_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2008.12.024"},{"key":"e_1_3_2_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.survophthal.2005.11.007"},{"key":"e_1_3_2_6_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-005-0112-z"},{"key":"e_1_3_2_7_1","volume-title":"Anesthesia for Genetic, Metabolic, and Dysmorphic Syndromes of Childhood","author":"Baum VC","year":"2007","unstructured":"Baum VC, O\u2019Flaherty JE. 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