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This case series explores paediatric SCSTs, presenting clinical, gross, histologic, and immunohistochemical findings, with a focus on limited information available about these tumours in African children. This retrospective study includes 9 cases of ovarian and testicular SCSTs (8 female and 1 male) in patients below 16\u2009years of age. Female patients presented with various SCST subtypes, including juvenile granulosa cell tumours (JGCTs), fibroma, and mixed tumours. Precocious puberty was a common presentation. The male patient had a Leydig cell tumour. Tumour sizes varied, with the smallest in the testis and the largest in a 3-year-old girl. Histologically, most cases exhibited characteristic features of their respective subtypes. Paediatric SCSTs are rare but important considerations in children with gonadal masses. Their incidence in African children is largely unknown. JGCTs are the most prevalent ovarian subtype. Leydig cell tumours are rare in children and can present with virilisation. Mixed SCST-germ cell tumours, though extremely rare, warrant careful consideration and immunohistochemistry for accurate diagnosis.<\/jats:p>","DOI":"10.1177\/10935266251414780","type":"journal-article","created":{"date-parts":[[2026,1,31]],"date-time":"2026-01-31T03:40:40Z","timestamp":1769830840000},"page":"200-209","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["Sex Cord-Stromal Tumours in Children: A Case Series"],"prefix":"10.1177","volume":"29","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6060-3979","authenticated-orcid":false,"given":"Patricia","family":"Okiro","sequence":"first","affiliation":[{"name":"Department of Pathology, Aga Khan University Hospital, Nairobi, Kenya"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marc","family":"Hendricks","sequence":"additional","affiliation":[{"name":"Haematology Oncology Service, Department of Paediatrics and Child Health, Faculty of Health Sciences, University of Cape Town, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Komala","family":"Pillay","sequence":"additional","affiliation":[{"name":"Department of Pathology, University of Cape Town\/National Health Laboratory Services, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2026,1,30]]},"reference":[{"key":"e_1_3_3_2_2","unstructured":"Reyes-Mugica M. 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