{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,5]],"date-time":"2026-05-05T00:54:41Z","timestamp":1777942481181,"version":"3.51.4"},"reference-count":10,"publisher":"SAGE Publications","issue":"3","license":[{"start":{"date-parts":[[2016,3,13]],"date-time":"2016-03-13T00:00:00Z","timestamp":1457827200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["Vasc Endovascular Surg"],"published-print":{"date-parts":[[2016,4]]},"abstract":"<jats:p>Ehlers-Danlos syndrome (EDS) encompasses a group of rare genetic connective tissue disorders. The vascular type (type IV) poses the most serious risk to patients. Diagnosis is usually difficult, especially if patients lack a family history. Life-threatening vascular emergency such as dissection or rupture can be the first presenting symptom. Management of the disease can pose a clinical challenge due to the emergency of presentation, tissue friability, and lack of clear management recommendations. We report a unique case of a 40-year-old man who presented with a ruptured celiac artery and a strong family history of EDS. This case highlights the difficulties and complications associated with treating this uncommon and serious disease.<\/jats:p>","DOI":"10.1177\/1538574416627697","type":"journal-article","created":{"date-parts":[[2016,3,14]],"date-time":"2016-03-14T20:08:13Z","timestamp":1457986093000},"page":"156-159","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":3,"title":["Ehlers-Danlos Syndrome Type IV"],"prefix":"10.1177","volume":"50","author":[{"given":"Sarah","family":"Soo-Hoo","sequence":"first","affiliation":[{"name":"Department of Vascular Medicine, Minneapolis Heart Institute, Minneapolis, MN, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Brandon R.","family":"Porten","sequence":"additional","affiliation":[{"name":"Department of Vascular Medicine, Minneapolis Heart Institute, Minneapolis, MN, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bjorn I.","family":"Engstrom","sequence":"additional","affiliation":[{"name":"Department of Vascular and Interventional Radiology, Abbott Northwestern Hospital, Minneapolis, MN, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nedaa","family":"Skeik","sequence":"additional","affiliation":[{"name":"Department of Vascular Medicine, Minneapolis Heart Institute, Minneapolis, MN, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2016,3,13]]},"reference":[{"key":"bibr1-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1016\/j.jvs.2009.08.019"},{"key":"bibr2-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19980428)77:1<31::AID-AJMG8>3.0.CO;2-O"},{"key":"bibr3-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1097\/SLA.0b013e31829c7a59"},{"key":"bibr4-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1007\/978-94-007-7893-1_9"},{"key":"bibr5-1538574416627697","first-page":"1993","volume-title":"GeneReviews\u00ae","author":"Pepin MG","year":"1999"},{"key":"bibr6-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM200003093421001"},{"key":"bibr7-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1016\/j.jvs.2005.03.053"},{"key":"bibr8-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1583\/07-2286.1"},{"key":"bibr9-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(10)60960-9"},{"key":"bibr10-1538574416627697","doi-asserted-by":"publisher","DOI":"10.1258\/vasc.2011.cr0318"}],"container-title":["Vascular and Endovascular Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/1538574416627697","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.1177\/1538574416627697","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/1538574416627697","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,5,2]],"date-time":"2026-05-02T06:57:23Z","timestamp":1777705043000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/1538574416627697"}},"subtitle":["A Case Report"],"short-title":[],"issued":{"date-parts":[[2016,3,13]]},"references-count":10,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2016,4]]}},"alternative-id":["10.1177\/1538574416627697"],"URL":"https:\/\/doi.org\/10.1177\/1538574416627697","relation":{},"ISSN":["1538-5744","1938-9116"],"issn-type":[{"value":"1538-5744","type":"print"},{"value":"1938-9116","type":"electronic"}],"subject":[],"published":{"date-parts":[[2016,3,13]]}}}