{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,3]],"date-time":"2026-07-03T08:36:12Z","timestamp":1783067772129,"version":"3.54.6"},"reference-count":23,"publisher":"SAGE Publications","issue":"3","license":[{"start":{"date-parts":[[2002,9,1]],"date-time":"2002-09-01T00:00:00Z","timestamp":1030838400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Interv Neuroradiol"],"published-print":{"date-parts":[[2002,9]]},"abstract":"<jats:p>Bonnet-Dechaume-Blanc or Wyburn-Mason disease has been considered a rare condition and mysterious disease for the last century. It was recently introduced as a spectrum of disease expression of cerebrofacial vascular structures related by the same neural crest origin, named \u201cCerebrofacial Arteriovenous Malformations Syndrome\u201d (CAMS) by JJ Bhattacharya. We illustrate the special observations of reported cases in the literature and our three demonstrative cases of CAMS in terms of natural history including progressive appearance of the AVMs, clinical presentation, angioarchitecture, clinical risk of retinal AVMs, AVMs along the optic pathways, intracranial AVMs and proper investigation in the suspicious case.<\/jats:p>","DOI":"10.1177\/159101990200800305","type":"journal-article","created":{"date-parts":[[2017,1,10]],"date-time":"2017-01-10T23:53:09Z","timestamp":1484092389000},"page":"251-264","source":"Crossref","is-referenced-by-count":18,"title":["Clinical Course and Angioarchitecture of Cerebrofacial Arteriovenous Metameric Syndromes"],"prefix":"10.1177","volume":"8","author":[{"given":"P.","family":"Jiarakongmun","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Alvarez","sequence":"additional","affiliation":[{"name":"Neuroradiology Diagnostique et Therapeutique, H\u00f4pital de Bic\u00eatre, Le Kremlin Bic\u00eatre-Cedex; France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Rodesch","sequence":"additional","affiliation":[{"name":"Neuroradiology Diagnostique et Therapeutique, H\u00f4pital de Bic\u00eatre, Le Kremlin Bic\u00eatre-Cedex; France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"P.","family":"Lasjaunias","sequence":"additional","affiliation":[{"name":"Neuroradiology Diagnostique et Therapeutique, H\u00f4pital de Bic\u00eatre, Le Kremlin Bic\u00eatre-Cedex; France"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2002,9,1]]},"reference":[{"key":"bibr1-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1177\/159101990100700101"},{"key":"bibr2-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1177\/159101999700300401"},{"key":"bibr3-159101990200800305","first-page":"165","volume":"18","author":"Bonnet P","year":"1937","journal-title":"Le Journal Medical de Lyon"},{"key":"bibr4-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/66.3.163"},{"key":"bibr5-159101990200800305","first-page":"95","volume":"5","author":"Effron L","year":"1985","journal-title":"J Clin Neuroophthalmol"},{"key":"bibr6-159101990200800305","first-page":"91","volume":"4","author":"Danis R","year":"1984","journal-title":"J Clin Neuroophthalmol"},{"key":"bibr7-159101990200800305","first-page":"53","volume":"3","author":"Hopen G","year":"1983","journal-title":"Concomitant chiasmal and fundus vascular malformations"},{"key":"bibr8-159101990200800305","doi-asserted-by":"publisher","DOI":"10.3171\/jns.2001.95.2.0346"},{"key":"bibr9-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1055\/s-2008-1035181"},{"key":"bibr10-159101990200800305","first-page":"1039","volume":"29","author":"Fujita H","year":"1989","journal-title":"Rinsho Shinkei gaku"},{"key":"bibr11-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1016\/0149-936X(88)90063-X"},{"key":"bibr12-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1007\/BF00589113"},{"key":"bibr13-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1016\/0090-3019(89)90329-7"},{"key":"bibr14-159101990200800305","first-page":"279","volume":"67","author":"Meinhold JR","year":"1996","journal-title":"J Am Ophthal Assoc"},{"key":"bibr15-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1016\/S0002-9394(98)00300-6"},{"key":"bibr16-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1080\/02688699844718"},{"key":"bibr17-159101990200800305","doi-asserted-by":"publisher","DOI":"10.1016\/S0002-9394(14)71738-6"},{"key":"bibr18-159101990200800305","first-page":"65","volume":"24","author":"Maeda H","year":"1992","journal-title":"No To Hattatsu"},{"key":"bibr19-159101990200800305","first-page":"91","volume":"4","author":"Daenis R","year":"1984","journal-title":"J Clin Neuro ophthalmol"},{"key":"bibr20-159101990200800305","first-page":"53","volume":"3","author":"Hopen G","year":"1983","journal-title":"J Clin Neuro ophthalmol"},{"key":"bibr21-159101990200800305","first-page":"788","volume":"168","author":"Schlieter F","year":"1976","journal-title":"Klin Monatsbl Augenheikd"},{"key":"bibr22-159101990200800305","first-page":"47","volume":"14","author":"Lalonde G","year":"1979","journal-title":"Can J Opthalmol"},{"key":"bibr23-159101990200800305","first-page":"1039","volume":"29","author":"Fujita H","year":"1989","journal-title":"Rinsho Shinkei gaku"}],"container-title":["Interventional Neuroradiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/159101990200800305","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/159101990200800305","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,4,29]],"date-time":"2026-04-29T10:58:01Z","timestamp":1777460281000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/159101990200800305"}},"subtitle":["Three Demonstrative Cases and Literature Review"],"short-title":[],"issued":{"date-parts":[[2002,9]]},"references-count":23,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2002,9]]}},"alternative-id":["10.1177\/159101990200800305"],"URL":"https:\/\/doi.org\/10.1177\/159101990200800305","relation":{},"ISSN":["1591-0199","2385-2011"],"issn-type":[{"value":"1591-0199","type":"print"},{"value":"2385-2011","type":"electronic"}],"subject":[],"published":{"date-parts":[[2002,9]]}}}