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Typical histopathological, clinical, and radiologic features are necessary for the diagnosis of Erdheim\u2013Chester disease. Prognosis depends on the extent of the systemic involvement, and central nervous system involvement has a poorer outcome. We present a 30-year-old Moroccan woman with diabetes insipidus, bone marrow, and asymmetrical axial osteolytic bone lesions. Biopsies were consistent with Erdheim\u2013Chester disease. Despite no treatment, the patient has demonstrated clinical improvement. <\/jats:p>","DOI":"10.1177\/2050313x19845217","type":"journal-article","created":{"date-parts":[[2019,5,6]],"date-time":"2019-05-06T13:29:05Z","timestamp":1557149345000},"update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":6,"title":["Case of Erdheim\u2013Chester presenting with xanthelasma-like eruption and osteolytic bone lesions: A case report"],"prefix":"10.1177","volume":"7","author":[{"given":"Evelyn Alarcon","family":"Chinchilla","sequence":"first","affiliation":[{"name":"Faculty of Medicine, CHU de Qu\u00e9bec-Universit\u00e9 Laval, Qu\u00e9bec, QC, Canada"},{"name":"Division of Dermatology, Department of Medicine, H\u00f4pital du Saint-Sacrement, CHU de Qu\u00e9bec-Universit\u00e9 Laval, Qu\u00e9bec, QC, 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