{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,27]],"date-time":"2026-05-27T20:00:06Z","timestamp":1779912006847,"version":"3.53.1"},"reference-count":42,"publisher":"SAGE Publications","issue":"4","license":[{"start":{"date-parts":[[2015,10,1]],"date-time":"2015-10-01T00:00:00Z","timestamp":1443657600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["World J Pediatr Congenit Heart Surg"],"published-print":{"date-parts":[[2015,10]]},"abstract":"<jats:p>Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA\/VSD\/MAPCAs) is a rare and complex congenital cardiac lesion that has historically carried a poor prognosis. With advancements in surgical management, we have seen an improvement in the outcomes for children affected by this disease. However, this population continues to present challenges due to the complex anatomy and physiology associated with PA\/VSD\/MAPCA. This summary of material presented during one of the nursing sessions of the 2014 Meeting of the Pediatric Cardiac Intensive Care Society provides an overview for those in cardiac intensive care units who do not have a large experience with this lesion. We will review the anatomy, physiology, surgical approach, postoperative management strategies, and cardiac catheter intervention options for PA\/VSD\/MAPCAs. We will also discuss recent innovations that may lead to continued improvement in outcomes for this challenging patient population.<\/jats:p>","DOI":"10.1177\/2150135115598559","type":"journal-article","created":{"date-parts":[[2015,10,14]],"date-time":"2015-10-14T12:28:44Z","timestamp":1444825724000},"page":"630-639","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":30,"title":["An Overview of Pulmonary Atresia and Major Aortopulmonary Collateral Arteries"],"prefix":"10.1177","volume":"6","author":[{"given":"Laura B.","family":"Presnell","sequence":"first","affiliation":[{"name":"Pediatric Cardiac Intensive Care Unit, Lucile Packard Children\u2019s Hospital, Palo Alto, CA, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Angela","family":"Blankenship","sequence":"additional","affiliation":[{"name":"The Heart Center, Nationwide Children\u2019s Hospital, Columbus, OH, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sharon L.","family":"Cheatham","sequence":"additional","affiliation":[{"name":"The Heart Center, Nationwide Children\u2019s Hospital, Columbus, OH, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gabe E.","family":"Owens","sequence":"additional","affiliation":[{"name":"C.S. Mott Children\u2019s Hospital, University of Michigan Congenital Heart Center, Hospital Drive, Ann Arbor, MI, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandra L.","family":"Staveski","sequence":"additional","affiliation":[{"name":"Research in Patient Services and Heart Institute, Cincinnati Children\u2019s Hospital Medical Center, Cincinnati, OH, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2015,10,14]]},"reference":[{"key":"bibr1-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1136\/heart.84.5.499"},{"key":"bibr2-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1016\/0735-1097(94)00364-V"},{"key":"bibr3-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1161\/01.CIR.89.1.243"},{"key":"bibr4-2150135115598559","first-page":"879","volume-title":"Moss and Adams\u2019 Heart Disease in Infants, Children, and Adolescents including the Fetus and Young Adult","author":"O\u2019Leary PW","year":"2008","edition":"7"},{"key":"bibr5-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1016\/S0735-1097(85)80223-0"},{"key":"bibr6-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1016\/j.ejcts.2005.12.054"},{"key":"bibr7-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.44.1.14"},{"key":"bibr8-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1016\/B978-032301281-2.50037-0"},{"key":"bibr9-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1053\/j.pcsu.2009.01.017"},{"key":"bibr10-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1161\/01.CIR.0000023624.33478.18"},{"key":"bibr11-2150135115598559","doi-asserted-by":"publisher","DOI":"10.1007\/s00431-011-1621-4"},{"key":"bibr12-2150135115598559","unstructured":"Asija R, Perry S. 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