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Urgent surgical intervention is critical for survival because of hemodynamic compromise. We review our experience with surgical management of neonates with Ebstein\u2019s anomaly associated with circular shunt and review the literature for similar reported cases. The underlying pathophysiology and different options of treatment are discussed.<\/jats:p>","DOI":"10.1177\/2150135117704615","type":"journal-article","created":{"date-parts":[[2017,10,3]],"date-time":"2017-10-03T21:22:09Z","timestamp":1507065729000},"page":"116-120","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":14,"title":["Surgical Management of Neonatal Ebstein\u2019s Anomaly Associated With Circular Shunt"],"prefix":"10.1177","volume":"10","author":[{"given":"Chawki","family":"Elzein","sequence":"first","affiliation":[{"name":"Advocate Children\u2019s Heart Institute, Advocate Children\u2019s Hospital, Oak Lawn, IL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sujata","family":"Subramanian","sequence":"additional","affiliation":[{"name":"Advocate Children\u2019s Heart Institute, Advocate Children\u2019s Hospital, Oak Lawn, IL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michel","family":"Ilbawi","sequence":"additional","affiliation":[{"name":"Advocate Children\u2019s Heart Institute, Advocate Children\u2019s Hospital, Oak Lawn, IL, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2017,10,3]]},"reference":[{"key":"bibr1-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2011.01.029"},{"key":"bibr2-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjcard.2005.05.035"},{"key":"bibr3-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.athoracsur.2015.11.029"},{"key":"bibr4-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1007\/s00246-007-9106-y"},{"key":"bibr5-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1093\/icvts\/ivs061"},{"key":"bibr6-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.arcped.2010.08.023"},{"key":"bibr7-2150135117704615","volume-title":"Data Analyses of the Society of Thoracic Surgeons Congenital Heart Surgery Database","author":"Jacobs JP","year":"2015"},{"key":"bibr8-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1093\/ejcts\/ezt465"},{"key":"bibr9-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1007\/s00246-012-0355-z"},{"key":"bibr10-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjcard.2007.11.049"},{"key":"bibr11-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/0735-1097(94)90516-9"},{"key":"bibr12-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjcard.2005.04.024"},{"key":"bibr13-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/0002-8703(62)90041-8"},{"key":"bibr14-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1136\/thx.21.1.83"},{"key":"bibr15-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.2006.105262"},{"key":"bibr16-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1016\/j.cjca.2016.03.008"},{"key":"bibr17-2150135117704615","doi-asserted-by":"publisher","DOI":"10.4103\/0974-2069.149527"},{"issue":"4","key":"bibr18-2150135117704615","first-page":"73","volume":"9","author":"Hakim K","year":"2013","journal-title":"Cardiol Tunis"},{"key":"bibr19-2150135117704615","doi-asserted-by":"publisher","DOI":"10.1007\/s00246-011-0124-4"}],"container-title":["World Journal for Pediatric and Congenital Heart Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/2150135117704615","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.1177\/2150135117704615","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/2150135117704615","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,4,30]],"date-time":"2026-04-30T23:20:46Z","timestamp":1777591246000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/2150135117704615"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,10,3]]},"references-count":19,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2019,1]]}},"alternative-id":["10.1177\/2150135117704615"],"URL":"https:\/\/doi.org\/10.1177\/2150135117704615","relation":{},"ISSN":["2150-1351","2150-136X"],"issn-type":[{"value":"2150-1351","type":"print"},{"value":"2150-136X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,10,3]]}}}