{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T07:09:23Z","timestamp":1777878563798,"version":"3.51.4"},"reference-count":5,"publisher":"SAGE Publications","issue":"3","license":[{"start":{"date-parts":[[2020,4,15]],"date-time":"2020-04-15T00:00:00Z","timestamp":1586908800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["World J Pediatr Congenit Heart Surg"],"published-print":{"date-parts":[[2020,5]]},"abstract":"<jats:p>Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.<\/jats:p>","DOI":"10.1177\/2150135119894292","type":"journal-article","created":{"date-parts":[[2020,4,15]],"date-time":"2020-04-15T12:13:37Z","timestamp":1586952817000},"page":"358-360","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle"],"prefix":"10.1177","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-6201-2547","authenticated-orcid":false,"given":"Irene","family":"Raso","sequence":"first","affiliation":[{"name":"Department of Cardiology, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrea","family":"Quarti","sequence":"additional","affiliation":[{"name":"Department of Congenital Cardiac Surgery, Azienda 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