{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,23]],"date-time":"2026-07-23T01:30:30Z","timestamp":1784770230217,"version":"3.55.0"},"reference-count":5,"publisher":"SAGE Publications","issue":"2","license":[{"start":{"date-parts":[[2025,2,6]],"date-time":"2025-02-06T00:00:00Z","timestamp":1738800000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["World J Pediatr Congenit Heart Surg"],"published-print":{"date-parts":[[2025,3]]},"abstract":"<jats:p>\n                    This manuscript will provide information about pulmonary atresia\u2009+\u2009ventricular septal defect, including definitions, nomenclature, and classification, based on the 2021\n                    <jats:italic>International Paediatric and Congenital Cardiac Code<\/jats:italic>\n                    (IPCCC) and the\n                    <jats:italic>Eleventh Revision of the International Classification of Diseases<\/jats:italic>\n                    (\n                    <jats:italic>ICD-11<\/jats:italic>\n                    ). The 2021 IPCCC and\n                    <jats:italic>ICD-11<\/jats:italic>\n                    provide the following definition for Tetralogy of Fallot with pulmonary atresia: Tetralogy of Fallot with pulmonary atresia is defined as \u201cA congenital cardiovascular malformation that is a variant of tetralogy of Fallot in which there is no direct communication between the right ventricle and the pulmonary arterial tree.\u201d The 2021 IPCCC and\n                    <jats:italic>ICD-11<\/jats:italic>\n                    provide the following definition for Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral arteries: Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral arteries is defined as \u201cA congenital cardiovascular malformation that is a variant of tetralogy of Fallot in which there is no direct communication between the right ventricle and the pulmonary arterial tree and there are collateral blood vessels between the systemic and pulmonary arteries.\u201d \u201cTetralogy of Fallot\u2009+\u2009pulmonary atresia\u201d is a specific type of \u201cpulmonary atresia\u2009+\u2009ventricular septal defect\u201d where the intracardiac malformation is more accurately defined. The presence or absence of major aortopulmonary collateral arteries (MAPCA[s]) does not change these definitions. Therefore, \u201ctetralogy of Fallot\u2009+\u2009pulmonary atresia\u2009+\u2009MAPCA(s)\u201d is a specific type of \u201cpulmonary atresia\u2009+\u2009ventricular septal defect\u2009+\u2009MAPCA(s)\u201d where the intracardiac malformation is more accurately defined. In the universe of patients with pulmonary atresia\u2009+\u2009ventricular septal defect, the anatomy and morphology of the pulmonary circulation to a large extent determines the surgical approach and overall outcome, with the intracardiac anatomy playing a secondary role. Based on the characterization of the pulmonary circulation, patients with pulmonary atresia\u2009+\u2009ventricular septal defect can be classified into three groups: In type A, pulmonary blood flow is provided by native pulmonary arteries (NPAs). In type B, pulmonary blood flow is provided by both NPA and MAPCA(s). In type C, pulmonary blood flow is provided only by MAPCA(s).\n                  <\/jats:p>","DOI":"10.1177\/21501351241311878","type":"journal-article","created":{"date-parts":[[2025,2,6]],"date-time":"2025-02-06T05:12:21Z","timestamp":1738818741000},"page":"173-176","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":3,"title":["Pulmonary Atresia and Ventricular Septal Defect: Definitions, Nomenclature, and Classification"],"prefix":"10.1177","volume":"16","author":[{"given":"Christo I.","family":"Tchervenkov","sequence":"first","affiliation":[{"name":"Division of Cardiovascular Surgery, The Montreal Children's Hospital, McGill University Health Centre, Montreal, Quebec, Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Richard","family":"Tang","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Surgery, The Montreal Children's Hospital, McGill University Health Centre, Montreal, Quebec, Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Giles J.","family":"Peek","sequence":"additional","affiliation":[{"name":"Congenital Heart Center, Division of Cardiovascular Surgery, Departments of Surgery and Pediatrics, University of Florida, Gainesville, Florida, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mark S.","family":"Bleiweis","sequence":"additional","affiliation":[{"name":"Congenital Heart Center, Division of Cardiovascular Surgery, Departments of Surgery and Pediatrics, University of Florida, Gainesville, Florida, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9916-929X","authenticated-orcid":false,"given":"Jeffrey P.","family":"Jacobs","sequence":"additional","affiliation":[{"name":"Congenital Heart Center, Division of Cardiovascular Surgery, Departments of Surgery and Pediatrics, University of Florida, Gainesville, Florida, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2025,2,6]]},"reference":[{"issue":"4","key":"e_1_3_2_2_2","article-title":"Congenital Heart Surgery and Nomenclature and Database Project: pulmonary atresia-ventricular septal defect","volume":"69","author":"Tchervenkov CI","year":"2000","unstructured":"Tchervenkov CI, Roy N. Congenital Heart Surgery and Nomenclature and Database Project: pulmonary atresia-ventricular septal defect. Ann Thorac Surg. 2000;69(4 Suppl):S97-S105. doi: https:\/\/doi.org\/10.1016\/s0003-4975 (99) 01285-0.","journal-title":"Ann Thorac Surg"},{"key":"e_1_3_2_3_2","doi-asserted-by":"crossref","DOI":"10.1016\/S0003-4975(99)01321-1","article-title":"The international congenital heart surgery nomenclature and database project","volume":"69","author":"Mavroudis C","year":"2000","unstructured":"Mavroudis C, Jacobs JP. The international congenital heart surgery nomenclature and database project. Ann Thorac Surg. 2000;69(4 Suppl):S1\u2013372. doi:https:\/\/doi.org\/10.1016\/S0003-4975(99)01278-3","journal-title":"Ann Thorac Surg."},{"key":"e_1_3_2_4_2","doi-asserted-by":"publisher","DOI":"10.1017\/S1047951117002244"},{"key":"e_1_3_2_5_2","article-title":"Nomenclature for pediatric and congenital cardiac care: Unification of clinical and administrative nomenclature - The 2021 international paediatric and congenital cardiac code (IPCCC) and the eleventh revision of the international classification of diseases (ICD-11)","author":"Jacobs JP","unstructured":"Jacobs JP, Franklin RCG, B\u00e9land MJ, et al. Nomenclature for pediatric and congenital cardiac care: Unification of clinical and administrative nomenclature - The 2021 international paediatric and congenital cardiac code (IPCCC) and the eleventh revision of the international classification of diseases (ICD-11). Cardiol Young. 2021;31(7):1057\u20131188. doi:https:\/\/doi.org\/10.1017\/S104795112100281X","journal-title":"Cardiol Young"},{"key":"e_1_3_2_6_2","article-title":"Nomenclature for pediatric and congenital cardiac care: unification of clinical and administrative nomenclature - The 2021 international paediatric and congenital cardiac code (IPCCC) and the eleventh revision of the international classification of diseases (ICD-11)","author":"Jacobs JP","unstructured":"Jacobs JP, Franklin RCG, B\u00e9land MJ, et al. Nomenclature for pediatric and congenital cardiac care: unification of clinical and administrative nomenclature - The 2021 international paediatric and congenital cardiac code (IPCCC) and the eleventh revision of the international classification of diseases (ICD-11). World J Pediatr Congenit Heart Surg. 2021;12(5):E1\u2013E18. doi: https:\/\/doi.org\/10.1177\/21501351211032919","journal-title":"World J Pediatr Congenit Heart Surg"}],"container-title":["World Journal for Pediatric and Congenital Heart Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/21501351241311878","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.1177\/21501351241311878","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/21501351241311878","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,4,30]],"date-time":"2026-04-30T23:27:14Z","timestamp":1777591634000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/21501351241311878"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,2,6]]},"references-count":5,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2025,3]]}},"alternative-id":["10.1177\/21501351241311878"],"URL":"https:\/\/doi.org\/10.1177\/21501351241311878","relation":{},"ISSN":["2150-1351","2150-136X"],"issn-type":[{"value":"2150-1351","type":"print"},{"value":"2150-136X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2025,2,6]]}}}