{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T07:12:37Z","timestamp":1777878757666,"version":"3.51.4"},"reference-count":8,"publisher":"SAGE Publications","issue":"3","license":[{"start":{"date-parts":[[2025,2,6]],"date-time":"2025-02-06T00:00:00Z","timestamp":1738800000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["World J Pediatr Congenit Heart Surg"],"published-print":{"date-parts":[[2025,5]]},"abstract":"<jats:p>We present a unique case of progressive neoaortic root and neoascending aortic dilatation, with poly-valvar regurgitation in a patient with Marfan syndrome and hypoplastic left heart syndrome palliated to Fontan procedure. This progressive dilation and valvar dysfunction necessitated a modified Bentall procedure and tricuspid valve repair. Our case highlights the impact of both a primary and secondary aortopathy complicating the Fontan procedure and the need for mechanical aortic valve replacement.<\/jats:p>","DOI":"10.1177\/21501351241313314","type":"journal-article","created":{"date-parts":[[2025,2,6]],"date-time":"2025-02-06T04:14:48Z","timestamp":1738815288000},"page":"424-426","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["Neoaortic Dilation and Polyvalvar Dysfunction: The Coexistence of Marfan Syndrome with Hypoplastic Left Heart Syndrome"],"prefix":"10.1177","volume":"16","author":[{"given":"Sruti","family":"Rao","sequence":"first","affiliation":[{"name":"Department of Pediatric Cardiology, Cleveland Clinic Children\u2019s Hospital, Cleveland, OH, USA"},{"name":"Department of Pediatric Cardiology, Johns Hopkins University, Baltimore, MD, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4516-3770","authenticated-orcid":false,"given":"Rukmini","family":"Komarlu","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiology, Cleveland Clinic Children\u2019s Hospital, Cleveland, OH, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hani K.","family":"Najm","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiothoracic and Vascular Surgery, Cleveland Clinic Children's Hospital, Cleveland, OH, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Brittany","family":"Hansen","sequence":"additional","affiliation":[{"name":"Genomic Medical Institute, Cleveland Clinic, Cleveland, OH, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rene E.","family":"Rodriguez","sequence":"additional","affiliation":[{"name":"Department of Pathology, Cleveland Clinic, Cleveland, OH, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kenneth G.","family":"Zahka","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiology, Cleveland Clinic Children\u2019s Hospital, Cleveland, OH, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2025,2,6]]},"reference":[{"key":"e_1_3_2_2_2","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.2009.183871"},{"key":"e_1_3_2_3_2","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9149(84)90418-1"},{"key":"e_1_3_2_4_2","doi-asserted-by":"publisher","DOI":"10.4070\/kcj.2013.43.4.215"},{"key":"e_1_3_2_5_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0735-1097(03)00715-0"},{"key":"e_1_3_2_6_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2012.07.005"},{"key":"e_1_3_2_7_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2010.07.076"},{"key":"e_1_3_2_8_2","first-page":"1","article-title":"Novel SMAD3 mutation in a patient with hypoplastic left heart syndrome with significant aortic aneurysm","author":"Fitzgerald KK","year":"2014","unstructured":"Fitzgerald KK, Bhat AM, Conard K, Hyland J, Pizarro C. 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