{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,6]],"date-time":"2026-07-06T09:24:17Z","timestamp":1783329857069,"version":"3.54.6"},"reference-count":29,"publisher":"SAGE Publications","license":[{"start":{"date-parts":[[2026,7,6]],"date-time":"2026-07-06T00:00:00Z","timestamp":1783296000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"},{"start":{"date-parts":[[2026,7,6]],"date-time":"2026-07-06T00:00:00Z","timestamp":1783296000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"funder":[{"DOI":"10.13039\/100008666","name":"Fundaci\u00f3 la Marat\u00f3 de TV3","doi-asserted-by":"publisher","award":["202023-30"],"award-info":[{"award-number":["202023-30"]}],"id":[{"id":"10.13039\/100008666","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100008666","name":"Fundaci\u00f3 la Marat\u00f3 de TV3","doi-asserted-by":"publisher","award":["202023-31"],"award-info":[{"award-number":["202023-31"]}],"id":[{"id":"10.13039\/100008666","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100008666","name":"Fundaci\u00f3 la Marat\u00f3 de TV3","doi-asserted-by":"publisher","award":["202023-32"],"award-info":[{"award-number":["202023-32"]}],"id":[{"id":"10.13039\/100008666","id-type":"DOI","asserted-by":"publisher"}]},{"name":"Miguel Servet program from Instituto de Salud Carlos III, Spain","award":["CP22\/00141"],"award-info":[{"award-number":["CP22\/00141"]}]}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["Journal of Neuromuscular Diseases"],"abstract":"<jats:sec>\n                    <jats:title>Aim<\/jats:title>\n                    <jats:p>To evaluate the longitudinal performance of inertial measurement unit (IMU)-based workspace metrics as a complementary tool to standard clinical scales for monitoring upper limb function in Duchenne muscular dystrophy (DMD) and spinal muscular atrophy (SMA).<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>Eighteen children and adolescents (10 DMD, 8 SMA) previously assessed at baseline underwent a one-year follow-up evaluation. Functional status was measured using disease-specific clinical scales (Performance of Upper Limb [PUL] for DMD; Revised Upper Limb Module [RULM] for SMA) combined with IMU-based kinematic analysis. Longitudinal changes in IMU-derived variables were compared with the evolution of clinical scores.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>Overall, IMU-based metrics showed longitudinal trends broadly comparable to those observed with clinical scales, with most participants remaining stable over 12 months. Minor individual discrepancies occurred in a few cases, and only two individuals exhibited a clear divergence between IMU-derived measures and clinical scale scores.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Interpretation<\/jats:title>\n                    <jats:p>IMU-based workspace analysis is feasible and showed meaningful associations with established functional assessments in pediatric neuromuscular disorders. These findings support its further evaluation as a complementary tool for longitudinal monitoring and highlight its potential future role in both clinical trials and routine follow-up.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1177\/22143602261464735","type":"journal-article","created":{"date-parts":[[2026,7,6]],"date-time":"2026-07-06T08:56:33Z","timestamp":1783328193000},"update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["IMU-based workspace area as a promising complementary tool to assess upper limb function in Neuromuscular diseases: A one-year follow-up"],"prefix":"10.1177","author":[{"given":"Alessandra","family":"Favata","sequence":"first","affiliation":[{"name":"Universitat Polit\u00e8cnica de Catalunya - BarcelonaTech (UPC)"},{"name":"Medical Technologies: Biomechanics, Institut de Recerca Sant Joan de D\u00e9u"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jesica","family":"Exp\u00f3sito-Escudero","sequence":"additional","affiliation":[{"name":"Hospital Sant Joan de D\u00e9u"},{"name":"Institut de Recerca Sant Joan de D\u00e9u"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Roger","family":"Gallart-Agut","sequence":"additional","affiliation":[{"name":"Medical Technologies: Biomechanics, Institut de Rob\u00f2tica i Inform\u00e0tica Industrial, CSIC-UPC"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Julita","family":"Medina-Cantillo","sequence":"additional","affiliation":[{"name":"Institut de Recerca Sant Joan de D\u00e9u"},{"name":"Hospital Sant Joan de D\u00e9u"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2933-398X","authenticated-orcid":false,"given":"Carme","family":"Torras","sequence":"additional","affiliation":[{"name":"Medical Technologies: Biomechanics, Institut de Rob\u00f2tica i Inform\u00e0tica Industrial, CSIC-UPC"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Josep M.","family":"Font-Llagunes","sequence":"additional","affiliation":[{"name":"Universitat Polit\u00e8cnica de Catalunya - BarcelonaTech (UPC)"},{"name":"Medical Technologies: Biomechanics, Institut de Recerca Sant Joan de D\u00e9u"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rosa","family":"P\u00e0mies-Vil\u00e0","sequence":"additional","affiliation":[{"name":"Universitat Polit\u00e8cnica de Catalunya - BarcelonaTech (UPC)"},{"name":"Medical Technologies: Biomechanics, Institut de Recerca Sant Joan de D\u00e9u"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7764-2085","authenticated-orcid":false,"given":"Daniel","family":"Natera-de Benito","sequence":"additional","affiliation":[{"name":"Hospital Sant Joan de D\u00e9u"},{"name":"Institut de Recerca Sant Joan de D\u00e9u"},{"name":"Instituto de Salud Carlos III"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2026,7,6]]},"reference":[{"key":"e_1_3_9_2_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.molmed.2024.12.006"},{"key":"e_1_3_9_3_2","doi-asserted-by":"publisher","DOI":"10.1038\/s41572-021-00248-3"},{"key":"e_1_3_9_4_2","doi-asserted-by":"publisher","DOI":"10.3233\/JND-230220"},{"key":"e_1_3_9_5_2","doi-asserted-by":"publisher","DOI":"10.1038\/s41572-022-00380-8"},{"key":"e_1_3_9_6_2","doi-asserted-by":"publisher","DOI":"10.1212\/CON.0000000000001338"},{"key":"e_1_3_9_7_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.braindev.2025.104397"},{"key":"e_1_3_9_8_2","doi-asserted-by":"publisher","DOI":"10.1111\/dmcn.16239"},{"key":"e_1_3_9_9_2","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0156696"},{"key":"e_1_3_9_10_2","doi-asserted-by":"publisher","DOI":"10.1186\/s12984-017-0259-5"},{"key":"e_1_3_9_11_2","doi-asserted-by":"publisher","DOI":"10.1186\/s12984-020-00757-4"},{"key":"e_1_3_9_12_2","doi-asserted-by":"publisher","DOI":"10.1038\/s41591-022-02045-1"},{"key":"e_1_3_9_13_2","doi-asserted-by":"publisher","DOI":"10.1186\/s12984-025-01602-2"},{"key":"e_1_3_9_14_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.clinbiomech.2020.105101"},{"key":"e_1_3_9_15_2","doi-asserted-by":"publisher","DOI":"10.1186\/1743-0003-10-65"},{"key":"e_1_3_9_16_2","doi-asserted-by":"publisher","DOI":"10.3389\/fbioe.2018.00027"},{"key":"e_1_3_9_17_2","doi-asserted-by":"publisher","DOI":"10.1186\/s12984-017-0315-1"},{"key":"e_1_3_9_18_2","doi-asserted-by":"publisher","DOI":"10.1038\/s41598-024-80177-9"},{"key":"e_1_3_9_19_2","doi-asserted-by":"publisher","DOI":"10.3233\/JND-230188"},{"key":"e_1_3_9_20_2","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0334177"},{"key":"e_1_3_9_21_2","doi-asserted-by":"publisher","DOI":"10.1111\/dmcn.14361"},{"key":"e_1_3_9_22_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.25430"},{"key":"e_1_3_9_23_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880040304"},{"key":"e_1_3_9_24_2","doi-asserted-by":"publisher","DOI":"10.1038\/s41598-019-50759-z"},{"key":"e_1_3_9_25_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jbiomech.2004.05.042"},{"key":"e_1_3_9_26_2","doi-asserted-by":"publisher","DOI":"10.1002\/acn3.51281"},{"key":"e_1_3_9_27_2","volume-title":"Clinical application of a wearable system for assessing upper limb motor function in children with Duchenne muscular dystrophy and spinal muscular atrophy","author":"Favata A","year":"2025","unstructured":"Favata A. Clinical application of a wearable system for assessing upper limb motor function in children with Duchenne muscular dystrophy and spinal muscular atrophy. Universitat Polit\u00e8cnica de Catalunya, 2025. https:\/\/doi.org\/10.5821\/dissertation-2117-443821"},{"key":"e_1_3_9_28_2","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0239064"},{"key":"e_1_3_9_29_2","first-page":"20250001","article-title":"Calculation of the Minimal Clinically Important Difference in Upper and Lower Limb Motor Assessment in Spinal Muscular Atrophy","volume":"10","author":"Hara T","year":"2025","unstructured":"Hara T, Miyazaki Y, Shimizu-Motohashi Y, et al. Calculation of the Minimal Clinically Important Difference in Upper and Lower Limb Motor Assessment in Spinal Muscular Atrophy. Prog Rehabil Med 2025; 10: 20250001. https:\/\/doi.org\/10.2490\/prm.20250001","journal-title":"Prog Rehabil Med"},{"key":"e_1_3_9_30_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.nmd.2025.105544"}],"container-title":["Journal of Neuromuscular Diseases"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/22143602261464735","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.1177\/22143602261464735","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/22143602261464735","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,7,6]],"date-time":"2026-07-06T08:56:35Z","timestamp":1783328195000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/22143602261464735"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,7,6]]},"references-count":29,"alternative-id":["10.1177\/22143602261464735"],"URL":"https:\/\/doi.org\/10.1177\/22143602261464735","relation":{},"ISSN":["2214-3599","2214-3602"],"issn-type":[{"value":"2214-3599","type":"print"},{"value":"2214-3602","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,7,6]]},"article-number":"22143602261464735"}}