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Batten disease, or neuronal ceroid lipofuscinosis, and Sanfilippo syndrome, or mucopolysaccharidosis type III, are two of the more common forms of childhood dementia disorders worldwide. While psychosocial interventions are the best available therapeutic approach for BPSD management in adult-onset dementia, there is very limited literature or clinical experience in the context of childhood dementia. To address this gap, we conducted a descriptive case analysis of BPSD profiles, associated contributing factors and targeted psychosocial interventions in two cases with childhood dementia disorders (Sanfilippo syndrome and CLN3 (juvenile onset) Batten disease) who were referred to Dementia Support Australia, a national dementia behaviour support service in Australia. Primary BPSD identified in these disorders included physical and verbal aggression and irritability\/lability. In these cases, contributing factors to the development of BPSD were not monolithic, encompassing pain, caregiver\u2019s approach and over or under-stimulation. Improvement in BPSD were observed using the Neuropsychiatric Inventory-Quesionnaire and globally noted as per the qualitative feedback reported by family and caregivers. Person-centred, multimodal psychosocial interventions were recognised as effective therapies in resolving BPSD in these cases. In conclusion, the case studies described the nature and presentation of BPSD in two common forms of childhood dementia and demonstrated the potential benefits of person-centred psychosocial interventions (delivered through national dementia-specific support programs) in alleviating BPSD such as irritability and aggression in these disorders.<\/jats:p>","DOI":"10.1177\/26323524241273492","type":"journal-article","created":{"date-parts":[[2024,9,7]],"date-time":"2024-09-07T00:58:16Z","timestamp":1725670696000},"update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":5,"title":["Behaviours and psychological symptoms of childhood dementia: two cases of psychosocial interventions"],"prefix":"10.1177","volume":"18","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0837-3245","authenticated-orcid":false,"given":"Mustafa","family":"Atee","sequence":"first","affiliation":[{"name":"The Dementia Centre, HammondCare, Level 2, 302 Selby Street Nth, Osborne Park, WA 6017, Australia"},{"name":"Sydney Pharmacy School, Faculty of Medicine and Health, The University of Sydney, Sydney, NSW, Australia"},{"name":"Curtin Medical School, Faculty of Health Sciences, Curtin University, Bentley, WA, Australia"},{"name":"Centre for Research in Aged Care, School of Nursing and Midwifery, Edith Cowan University, Joondalup, WA, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ineka","family":"Whiteman","sequence":"additional","affiliation":[{"name":"Batten Disease Support &amp; Research Association (BDSRA) Australia, Brisbane, QLD, Australia"},{"name":"BDSRA Foundation, Columbus, OH, USA"},{"name":"Beyond Batten Disease Foundation, Austin, TX, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2018-1908","authenticated-orcid":false,"given":"Rebecca","family":"Lloyd","sequence":"additional","affiliation":[{"name":"The Dementia Centre, HammondCare, Osborne Park, WA, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3627-6095","authenticated-orcid":false,"given":"Thomas","family":"Morris","sequence":"additional","affiliation":[{"name":"The Dementia Centre, HammondCare, St Leonards, NSW, Australia"},{"name":"Sydney School of Public Health, Faculty of Medicine and Health, The University of Sydney, Sydney, NSW, Australia"},{"name":"Thomas Morris is also affiliated with Faculty of Health, University of Canberra, Bruce, ACT, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","published-online":{"date-parts":[[2024,9,6]]},"reference":[{"key":"e_1_3_4_2_2","doi-asserted-by":"publisher","DOI":"10.1007\/s007870200012"},{"key":"e_1_3_4_3_2","first-page":"75","volume-title":"Juvenile neuronal ceroid lipofuscinosis, childhood dementia and education: intervention, education and learning strategies in a lifetime perspective","author":"Haugen PK","year":"2019","unstructured":"Haugen PK, von Tetzchner S, Oxley JD, et al. 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