{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T17:35:27Z","timestamp":1777656927231,"version":"3.51.4"},"reference-count":19,"publisher":"SAGE Publications","license":[{"start":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T00:00:00Z","timestamp":1772150400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"},{"start":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T00:00:00Z","timestamp":1772150400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["Sage Open Pediatrics"],"published-print":{"date-parts":[[2026,3]]},"abstract":"<jats:p>Solid-pseudopapillary tumor (SPT) of the pancreas is an extremely rare neoplasm in children, with an unknown origin. It accounts for 8% to 12% of primary pancreatic tumors and predominantly affects young females (91%), with very few cases reported in males. Malignant potential is minimal, particularly in adolescents. We report a 12-year-old child presenting with abdominal distension, nausea, vomiting, appetite loss, weight loss, pruritus, jaundice, dark urine, and back pain. Examination revealed a distended abdomen moving with respiration and a firm, tender 15\u2009cm\u2009\u00d7\u200920\u2009cm mass in the right upper quadrant. CT imaging demonstrated a large heterogeneously enhancing mass arising from the pancreatic head, consistent with SPT. Surgical therapy remains the treatment of choice, with partial duodenopancreatectomy or distal pancreatectomy (spleen-preserving when possible) recommended for complete excision. Although the body and tail are more commonly affected, complete resection (R0) offers excellent prognosis, even with local invasion or metastasis.<\/jats:p>","DOI":"10.1177\/30502225261419179","type":"journal-article","created":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T10:16:11Z","timestamp":1772187371000},"update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":0,"title":["Solid-Pseudo papillary Tumor of the Pancreas (Frantz Tumor): Case Report of a Rare Pancreatic Tumor in Ethiopia"],"prefix":"10.1177","volume":"13","author":[{"given":"Workye Tigabe","family":"Mola","sequence":"first","affiliation":[{"name":"Saint Peter\u2019s Specialized Hospital, Addis Ababa, Ethiopia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0004-6191-4102","authenticated-orcid":false,"given":"Mustofa Hassen","family":"Yesuf","sequence":"additional","affiliation":[{"name":"Saint Peter\u2019s Specialized Hospital, Addis Ababa, Ethiopia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Dagamawi","family":"Dagne","sequence":"additional","affiliation":[{"name":"Addis Ababa University, Ethiopia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yoseph","family":"Bedore","sequence":"additional","affiliation":[{"name":"Addis Ababa University, Ethiopia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0003-2335-1508","authenticated-orcid":false,"given":"Abdurehman Seid","family":"Mohammed","sequence":"additional","affiliation":[{"name":"Saint Peter\u2019s Specialized Hospital, Addis Ababa, Ethiopia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2026,2,27]]},"reference":[{"key":"e_1_3_3_2_2","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.29975"},{"key":"e_1_3_3_3_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2559.1983.tb02277.x"},{"key":"e_1_3_3_4_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0039-6060(05)80271-5"},{"key":"e_1_3_3_5_2","first-page":"2587","article-title":"Papillary cystic tumors of the pancreas: assessment of malignant potential by analysis of progesterone receptor, flow cytometry, and ras oncogene mutation","volume":"17","author":"Lee WY","year":"1997","unstructured":"Lee WY, Tzeng CC, Chen RM, Tsao CJ, Tseng JY, Jin YT. Papillary cystic tumors of the pancreas: assessment of malignant potential by analysis of progesterone receptor, flow cytometry, and ras oncogene mutation. Anticancer Res. 1997;17(4A):2587-2591.","journal-title":"Anticancer Res"},{"key":"e_1_3_3_6_2","doi-asserted-by":"publisher","DOI":"10.1007\/s002689900621"},{"key":"e_1_3_3_7_2","volume-title":"Atlas of Tumor Pathology","author":"Frantz VK","year":"1959","unstructured":"Frantz VK (ed.). Tumors of the pancreas. In: Atlas of Tumor Pathology. Section VII, Fascicles 27 and 28. Armed Forces Institute of Pathology; 1959, pp. 32-33."},{"key":"e_1_3_3_8_2","doi-asserted-by":"publisher","DOI":"10.1002\/1097-0142(19930101)71:1<82::AID-CNCR2820710114>3.0.CO;2-Y"},{"key":"e_1_3_3_9_2","doi-asserted-by":"publisher","DOI":"10.1007\/s004280050475"},{"key":"e_1_3_3_10_2","doi-asserted-by":"publisher","DOI":"10.1097\/JS9.0000000000000373"},{"key":"e_1_3_3_11_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF01600295"},{"key":"e_1_3_3_12_2","doi-asserted-by":"publisher","DOI":"10.1016\/0022-3468(95)90701-7"},{"key":"e_1_3_3_13_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF02924165"},{"issue":"12","key":"e_1_3_3_14_2","first-page":"2298","article-title":"Chromosome abnormality in solid and cystic tumor of the pancreas","volume":"92","author":"Matsubara K","year":"1997","unstructured":"Matsubara K, Nigami H, Harigaya H, Baba K. Chromosome abnormality in solid and cystic tumor of the pancreas. Am J Gastroenterol. 1997;92(12):2298-2300.","journal-title":"Am J Gastroenterol"},{"key":"e_1_3_3_15_2","doi-asserted-by":"publisher","DOI":"10.1093\/ajcp\/98.5.478"},{"key":"e_1_3_3_16_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.modpat.2023.100141"},{"key":"e_1_3_3_17_2","doi-asserted-by":"publisher","DOI":"10.1155\/2020\/2829647"},{"key":"e_1_3_3_18_2","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.27114"},{"issue":"18","key":"e_1_3_3_19_2","article-title":"Response to mammalian target of rapamycin-based therapy and Incidental finding of Lynch syndrome in a patient with solid pseudopapillary neoplasm of the pancreas with AKT1_E17K mutation","volume":"2","author":"Cuglievan B","year":"2018","unstructured":"Cuglievan B, Subbiah V, Wang H, et al. Response to mammalian target of rapamycin-based therapy and Incidental finding of Lynch syndrome in a patient with solid pseudopapillary neoplasm of the pancreas with AKT1_E17K mutation. JCO Precis Oncol. 2018;2(18):00182.","journal-title":"JCO Precis Oncol"},{"issue":"12","key":"e_1_3_3_20_2","first-page":"2030","article-title":"Adjuvant chemotherapy for pediatric solid pseudopapillary tumor of the pancreas","volume":"51","author":"Hong SM","year":"2016","unstructured":"Hong SM, Jung MJ, Ki MH, Kim HJ, Lee JW. Adjuvant chemotherapy for pediatric solid pseudopapillary tumor of the pancreas. J Pediatr Surg. 2016;51(12):2030-2034.","journal-title":"J Pediatr Surg"}],"container-title":["Sage Open Pediatrics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/30502225261419179","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.1177\/30502225261419179","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.1177\/30502225261419179","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,4,29]],"date-time":"2026-04-29T07:07:39Z","timestamp":1777446459000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.1177\/30502225261419179"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,2,27]]},"references-count":19,"alternative-id":["10.1177\/30502225261419179"],"URL":"https:\/\/doi.org\/10.1177\/30502225261419179","relation":{},"ISSN":["3050-2225","3050-2225"],"issn-type":[{"value":"3050-2225","type":"print"},{"value":"3050-2225","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,2,27]]},"article-number":"30502225261419179"}}