{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T13:05:46Z","timestamp":1777899946910,"version":"3.51.4"},"reference-count":25,"publisher":"SAGE Publications","issue":"1","license":[{"start":{"date-parts":[[2019,12,30]],"date-time":"2019-12-30T00:00:00Z","timestamp":1577664000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["Scott Med J"],"published-print":{"date-parts":[[2020,2]]},"abstract":"<jats:p>The clinical triad of peripheral cutaneous erythematous nodules, oligo or polyarthritis with intraosseous fat necrosis in the setting of pancreatic disease defines a rare entity called pancreatitis-panniculitis-polyarthritis syndrome. The early recognition of this triad is critical due to its high mortality rate and the rapid onset of osseous and articular disabilities. We describe the clinical course of a 54-year-old patient with complaints of weight loss and fever who presented to our hospital with signs of polyarthritis and appendicular erythematous cutaneous nodules. Clinical investigation revealed high inflammatory and pancreatic enzymes levels. Cutaneous biopsy and articular MRI showed evidence of peripheral necrosis. After a thorough investigation, a diagnosis of panniculitis-polyarthritis-pancreatitis syndrome was established. Treatment was initiated, and a slow but steady improvement was observed. Further complications of the disease process were observed. This case highlights the importance of recognising the association between panniculitis and polyarthritis with pancreatic disease in order to improve outcomes.<\/jats:p>","DOI":"10.1177\/0036933019897373","type":"journal-article","created":{"date-parts":[[2019,12,30]],"date-time":"2019-12-30T10:30:44Z","timestamp":1577701844000},"page":"19-23","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":5,"title":["A case report of pancreatitis-panniculitis-polyarthritis syndrome \u2013 an unusual but serious presentation of pancreatic disease"],"prefix":"10.1177","volume":"65","author":[{"given":"Jo\u00e3o Paulo","family":"Castro","sequence":"first","affiliation":[{"name":"Medical Doctor, Physical and Rehabilitation Medicine, Centro Hospitalar Vila Nova de Gaia\/Espinho, Portugal"},{"name":"Medical Doctor, Department of Biomedicine, Unit of Anatomy, Faculty of Medicine, University of Porto, Portugal"}]},{"given":"Gabriel","family":"Atan\u00e1sio","sequence":"additional","affiliation":[{"name":"Medical Doctor, Internal Medicine, Centro Hospitalar de Vila Nova de Gaia\/Espinho, Portugal"}]},{"given":"Maria Ana","family":"Canelas","sequence":"additional","affiliation":[{"name":"Medical Doctor, Internal Medicine, Centro Hospitalar de Vila Nova de Gaia\/Espinho, Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8577-5128","authenticated-orcid":false,"given":"Andr\u00e9","family":"Ferreira","sequence":"additional","affiliation":[{"name":"Medical Doctor, Department of Biomedicine, Unit of Anatomy, Faculty of Medicine, University of Porto, Portugal"}]},{"given":"Ana Rita","family":"Barbosa","sequence":"additional","affiliation":[{"name":"Medical Doctor, Internal Medicine, Centro Hospitalar de Vila Nova de Gaia\/Espinho, Portugal"}]},{"given":"Marta","family":"Barbedo","sequence":"additional","affiliation":[{"name":"Medical Doctor, Internal Medicine, Centro Hospitalar de Vila Nova de Gaia\/Espinho, Portugal"}]},{"given":"Regina","family":"Abreu","sequence":"additional","affiliation":[{"name":"Medical Doctor, Internal Medicine, Centro Hospitalar de Vila Nova de Gaia\/Espinho, Portugal"}]}],"member":"179","published-online":{"date-parts":[[2019,12,30]]},"reference":[{"key":"bibr1-0036933019897373","doi-asserted-by":"publisher","DOI":"10.1016\/j.ijscr.2017.01.037"},{"key":"bibr2-0036933019897373","doi-asserted-by":"publisher","DOI":"10.1159\/000066758"},{"key":"bibr3-0036933019897373","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjmed.2017.04.037"},{"key":"bibr4-0036933019897373","doi-asserted-by":"publisher","DOI":"10.1007\/s00383-003-1041-2"},{"key":"bibr5-0036933019897373","unstructured":"Graham P and, Altman D. A man with painful lower extremity nodules, pancreatitis, and polyarthritis. 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