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The optimal screening tools and methodology are, as yet, unknown, and this is confounded by a lack of consensus over which patients to screen. Current practice favours annual screening of all SSc patients using Doppler echocardiography to detect elevated right heart pressures. This will typically identify most patients with the various forms of pulmonary hypertension found in SSc. The optimum thresholds for Doppler echocardiography are still subject to investigation, especially for patients with mild pulmonary hypertension, and this technique may, therefore, yield a significant number of false-positives and a currently unknown number of false-negatives. Confirmatory right heart catheterisation remains necessary in all suspected cases. Further research is needed to identify the optimal tools and the screening approach with greatest specificity and selectivity.<\/jats:p>","DOI":"10.1183\/09059180.00003209","type":"journal-article","created":{"date-parts":[[2009,8,31]],"date-time":"2009-08-31T17:23:01Z","timestamp":1251739381000},"page":"162-169","source":"Crossref","is-referenced-by-count":45,"title":["Screening for pulmonary arterial hypertension in systemic sclerosis"],"prefix":"10.1183","volume":"18","author":[{"given":"J-L.","family":"Vachi\u00e9ry","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Coghlan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"81","published-online":{"date-parts":[[2009,8,31]]},"reference":[{"key":"2024102402472320000_18.113.162.1","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjmed.2004.04.031"},{"key":"2024102402472320000_18.113.162.2","first-page":"S85","volume":"26","year":"2008","journal-title":"Clin Exp Rheumatol"},{"key":"2024102402472320000_18.113.162.3","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200806-953OC"},{"key":"2024102402472320000_18.113.162.4","doi-asserted-by":"publisher","DOI":"10.1136\/ard.2006.066068"},{"key":"2024102402472320000_18.113.162.5","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.200510-1668OC"},{"key":"2024102402472320000_18.113.162.6","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00138706"},{"key":"2024102402472320000_18.113.162.7","doi-asserted-by":"publisher","DOI":"10.1016\/j.ehj.2004.09.014"},{"key":"2024102402472320000_18.113.162.8","doi-asserted-by":"publisher","DOI":"10.1136\/ard.2003.017673"},{"key":"2024102402472320000_18.113.162.9","unstructured":"The Criteria Committee of the New York Heart Association. 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