{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,6]],"date-time":"2026-02-06T00:58:07Z","timestamp":1770339487677,"version":"3.49.0"},"reference-count":30,"publisher":"European Respiratory Society (ERS)","issue":"2","funder":[{"DOI":"10.13039\/501100004963","name":"Seventh Framework Programme","doi-asserted-by":"publisher","award":["35404 BESTCILIA"],"award-info":[{"award-number":["35404 BESTCILIA"]}],"id":[{"id":"10.13039\/501100004963","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100000921","name":"European Cooperation in Science and Technology","doi-asserted-by":"publisher","award":["COST Action BEAT-PCD: Better Experimental Approach"],"award-info":[{"award-number":["COST Action BEAT-PCD: Better Experimental Approach"]}],"id":[{"id":"10.13039\/501100000921","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100001711","name":"Schweizerischer Nationalfonds zur F\u00f6rderung der Wissenschaftlichen Forschung","doi-asserted-by":"publisher","award":["32003B_162820"],"award-info":[{"award-number":["32003B_162820"]}],"id":[{"id":"10.13039\/501100001711","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["publications.ersnet.org"],"crossmark-restriction":true},"short-container-title":["Eur Respir J"],"accepted":{"date-parts":[[2016,12,22]]},"published-print":{"date-parts":[[2017,2]]},"DOI":"10.1183\/13993003.02514-2016","type":"journal-article","created":{"date-parts":[[2017,2,24]],"date-time":"2017-02-24T02:13:17Z","timestamp":1487902397000},"page":"1602514","update-policy":"https:\/\/doi.org\/10.1183\/ers-crossmark-policy","source":"Crossref","is-referenced-by-count":24,"title":["Hypertonic saline in patients with primary ciliary dyskinesia: on the road to evidence-based treatment for a rare lung disease"],"prefix":"10.1183","volume":"49","author":[{"given":"Claudia E.","family":"Kuehni","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Myrofora","family":"Goutaki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Helene E.","family":"Kobbernagel","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"81","published-online":{"date-parts":[[2017,2,23]]},"reference":[{"key":"2024101903421336000_49.2.1602514.1","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01770-2016"},{"key":"2024101903421336000_49.2.1602514.2","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00176608"},{"key":"2024101903421336000_49.2.1602514.3","doi-asserted-by":"crossref","unstructured":"Lucas JS , Walker WT , Kuehni CE , et\u00a0al. Primary Ciliary Dyskinesia. In: Cordier J-F , ed. Orphan Lung diseases (European Respiratory Monograph). Sheffield, European Respiratory Society, 2011; pp. 201\u2013217.","DOI":"10.1183\/1025448x.10008310"},{"key":"2024101903421336000_49.2.1602514.4","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01090-2016"},{"key":"2024101903421336000_49.2.1602514.5","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.00736-2016"},{"key":"2024101903421336000_49.2.1602514.6","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00001010"},{"key":"2024101903421336000_49.2.1602514.7","doi-asserted-by":"publisher","DOI":"10.1136\/adc.2009.158493"},{"key":"2024101903421336000_49.2.1602514.8","doi-asserted-by":"publisher","DOI":"10.1016\/j.rmed.2011.12.021"},{"key":"2024101903421336000_49.2.1602514.9","doi-asserted-by":"publisher","DOI":"10.1126\/science.1173869"},{"key":"2024101903421336000_49.2.1602514.10","doi-asserted-by":"publisher","DOI":"10.1038\/nm.2237"},{"key":"2024101903421336000_49.2.1602514.11","doi-asserted-by":"publisher","DOI":"10.1186\/1471-2466-3-4"},{"key":"2024101903421336000_49.2.1602514.12","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00216214"},{"key":"2024101903421336000_49.2.1602514.13","first-page":"1726","article-title":"Primary ciliary dyskinesia: first health-related quality-of-life measures for pediatric patients","volume":"13","author":"Dell","year":"2016","journal-title":"Ann Am Thorac Soc"},{"key":"2024101903421336000_49.2.1602514.14","doi-asserted-by":"publisher","DOI":"10.1136\/thoraxjnl-2014-206578"},{"key":"2024101903421336000_49.2.1602514.15","doi-asserted-by":"publisher","DOI":"10.1136\/thoraxjnl-2011-200726"},{"key":"2024101903421336000_49.2.1602514.16","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.00466-2016"},{"key":"2024101903421336000_49.2.1602514.17","doi-asserted-by":"crossref","first-page":"S23","DOI":"10.1016\/j.jcf.2014.03.010","article-title":"European Cystic Fibrosis Society standards of care: best practice guidelines","volume":"13","author":"Smyth","year":"2014","journal-title":"J Cyst Fibros"},{"key":"2024101903421336000_49.2.1602514.18","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcf.2009.01.004"},{"key":"2024101903421336000_49.2.1602514.19","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcf.2014.03.009"},{"key":"2024101903421336000_49.2.1602514.20","doi-asserted-by":"publisher","DOI":"10.1378\/chest.128.4.2347"},{"key":"2024101903421336000_49.2.1602514.21","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcf.2007.02.001"},{"key":"2024101903421336000_49.2.1602514.22","doi-asserted-by":"crossref","first-page":"2519","DOI":"10.1016\/S0140-6736(16)00576-6","article-title":"Cystic fibrosis","volume":"388","author":"Elborn","year":"2016","journal-title":"Lancet"},{"key":"2024101903421336000_49.2.1602514.23","doi-asserted-by":"publisher","DOI":"10.1016\/S1470-2045(13)70010-X"},{"key":"2024101903421336000_49.2.1602514.24","doi-asserted-by":"publisher","DOI":"10.1016\/S1470-2045(08)70101-3"},{"key":"2024101903421336000_49.2.1602514.25","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa043900"},{"key":"2024101903421336000_49.2.1602514.26","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1186\/s12919-016-0067-0","article-title":"BEAT-PCD. Proceedings of the COST action BM1407 inaugural conference BEAT-PCD: translational research in primary ciliary dyskinesia \u2013 bench, bedside, and population perspectives","volume":"10","author":"Rubbo","year":"2016","journal-title":"BMC Proc"},{"key":"2024101903421336000_49.2.1602514.27","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01181-2016"},{"key":"2024101903421336000_49.2.1602514.28","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.00776-2015"},{"key":"2024101903421336000_49.2.1602514.29","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1186\/s12890-016-0261-x","article-title":"Study protocol, rationale and recruitment in a European multi-centre randomized controlled trial to determine the efficacy and safety of azithromycin maintenance therapy for 6 months in primary ciliary dyskinesia","volume":"16","author":"Kobbernagel","year":"2016","journal-title":"BMC Pulm Med"},{"key":"2024101903421336000_49.2.1602514.30","unstructured":"European standards of care for children with cancer. Warsaw, European Society of Paediatric Oncology, 2009. www.siope.eu\/wp-content\/uploads\/2013\/09\/European_Standards_final_2011.pdf Date last updated: October 14, 2009."}],"container-title":["European Respiratory Journal"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1183\/13993003.02514-2016","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,2,24]],"date-time":"2025-02-24T06:38:28Z","timestamp":1740379108000},"score":1,"resource":{"primary":{"URL":"https:\/\/publications.ersnet.org\/lookup\/doi\/10.1183\/13993003.02514-2016"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,2]]},"references-count":30,"journal-issue":{"issue":"2","published-online":{"date-parts":[[2017,2,23]]},"published-print":{"date-parts":[[2017,2]]}},"alternative-id":["10.1183\/13993003.02514-2016"],"URL":"https:\/\/doi.org\/10.1183\/13993003.02514-2016","relation":{},"ISSN":["0903-1936","1399-3003"],"issn-type":[{"value":"0903-1936","type":"print"},{"value":"1399-3003","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,2]]}}}