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Their radiological presentation is less distinctive, and definitive diagnosis may require the use of transbronchial or surgical lung biopsy. Corticosteroid therapy is the mainstay of ILD treatment in Sj\u00f6gren's syndrome, but the use of other immunosuppressive drugs needs to be determined. ILD is a significant cause of death in Sj\u00f6gren's syndrome. Tracheobronchial disease is common in Sj\u00f6gren's syndrome, characterised by diffuse lymphocytic infiltration of the airway. It is sometimes responsible for a crippling chronic cough. It can also present in the form of bronchial hyperresponsiveness, bronchiectasis, bronchiolitis or recurrent respiratory infections. The management of these manifestations may require treatment for dryness and\/or inflammation of the airways. Airway disease has little effect on respiratory function and is rarely the cause of death in Sj\u00f6gren's syndrome patients. 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