{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,2,25]],"date-time":"2025-02-25T05:09:09Z","timestamp":1740460149386,"version":"3.37.3"},"reference-count":13,"publisher":"European Respiratory Society (ERS)","issue":"2","license":[{"start":{"date-parts":[[2021,3,26]],"date-time":"2021-03-26T00:00:00Z","timestamp":1616716800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":["publications.ersnet.org"],"crossmark-restriction":true},"short-container-title":["ERJ Open Res"],"accepted":{"date-parts":[[2021,3,20]]},"published-print":{"date-parts":[[2021,4]]},"DOI":"10.1183\/23120541.00758-2020","type":"journal-article","created":{"date-parts":[[2021,3,26]],"date-time":"2021-03-26T18:50:14Z","timestamp":1616784614000},"page":"00758-2020","update-policy":"https:\/\/doi.org\/10.1183\/ers-crossmark-policy","source":"Crossref","is-referenced-by-count":3,"title":["Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor"],"prefix":"10.1183","volume":"7","author":[{"given":"Jochen G.","family":"Mainz","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nina","family":"Erdmann","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Franziska","family":"Duckstein","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Carlos","family":"Zagoya","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"81","published-online":{"date-parts":[[2021,3,26]]},"reference":[{"key":"2024101711080234000_7.2.00758-2020.1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa0909825"},{"key":"2024101711080234000_7.2.00758-2020.2","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201301-0153OC"},{"key":"2024101711080234000_7.2.00758-2020.3","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa1105185"},{"key":"2024101711080234000_7.2.00758-2020.4","doi-asserted-by":"publisher","DOI":"10.1086\/376525"},{"key":"2024101711080234000_7.2.00758-2020.5","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0904709106"},{"key":"2024101711080234000_7.2.00758-2020.6","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra043184"},{"key":"2024101711080234000_7.2.00758-2020.7","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa1908639"},{"key":"2024101711080234000_7.2.00758-2020.8","doi-asserted-by":"crossref","first-page":"232","DOI":"10.1016\/j.arbres.2017.09.012","article-title":"Effects of ivacaftor in three pediatric siblings with cystic fibrosis carrying the mutations G551D and F508del","volume":"54","author":"Mainz","year":"2018","journal-title":"Arch Bronconeumol"},{"key":"2024101711080234000_7.2.00758-2020.9","doi-asserted-by":"publisher","DOI":"10.1111\/j.1439-0507.2011.02130.x"},{"key":"2024101711080234000_7.2.00758-2020.10","doi-asserted-by":"publisher","DOI":"10.1136\/thx.2010.145862"},{"key":"2024101711080234000_7.2.00758-2020.11","doi-asserted-by":"publisher","DOI":"10.1002\/jgm.1119"},{"key":"2024101711080234000_7.2.00758-2020.12","doi-asserted-by":"publisher","DOI":"10.4049\/jimmunol.177.8.5186"},{"key":"2024101711080234000_7.2.00758-2020.13","doi-asserted-by":"crossref","first-page":"372","DOI":"10.3389\/fcimb.2020.00372","article-title":"CFTR modulators dampen aspergillus-induced reactive oxygen species production by cystic fibrosis phagocytes","volume":"10","author":"Currie","year":"2020","journal-title":"Front Cell Infect Microbiol"}],"container-title":["ERJ Open Research"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1183\/23120541.00758-2020","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,2,24]],"date-time":"2025-02-24T05:07:32Z","timestamp":1740373652000},"score":1,"resource":{"primary":{"URL":"https:\/\/publications.ersnet.org\/lookup\/doi\/10.1183\/23120541.00758-2020"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,3,26]]},"references-count":13,"journal-issue":{"issue":"2","published-online":{"date-parts":[[2021,5,24]]},"published-print":{"date-parts":[[2021,4]]}},"alternative-id":["10.1183\/23120541.00758-2020"],"URL":"https:\/\/doi.org\/10.1183\/23120541.00758-2020","relation":{},"ISSN":["2312-0541"],"issn-type":[{"type":"electronic","value":"2312-0541"}],"subject":[],"published":{"date-parts":[[2021,3,26]]}}}