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We reported an 18-year-old woman who presented with 3 years history of sole involvement of attacking erythema, pain and warmth over her face and ears without any other associations. The frequency and severity of the flares progressed gradually during the course. Cutaneous examination revealed erythema, increased temperature and tenderness on the face and ears during the flare. The symptoms could be relieved rapidly by cooling. Dermatoscope showed that vessels inside the erythema were more dilated during the episode than after application of ice. The lesion is considered a rare variant of erythermalgia with sole involvement of face and ears. The symptoms had mild response to oral antihistamines, topical steroids and tacrolimus, but had excellent response to the combinative therapy of aspirin and paroxetins.<\/jats:p>","DOI":"10.1186\/1129-2377-15-18","type":"journal-article","created":{"date-parts":[[2014,3,26]],"date-time":"2014-03-26T16:09:10Z","timestamp":1395850150000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":13,"title":["Erythema associated with pain and warmth on face and ears: a variant of erythermalgia or red ear syndrome?"],"prefix":"10.1186","volume":"15","author":[{"given":"Ming-Chun","family":"Chen","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Qing-Fang","family":"Xu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Di-Qing","family":"Luo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xiang","family":"Li","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ding-Yang","family":"He","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2014,3,26]]},"reference":[{"issue":"3","key":"602_CR1","doi-asserted-by":"publisher","first-page":"330","DOI":"10.1001\/archderm.136.3.330","volume":"136","author":"MD Davis","year":"2000","unstructured":"Davis MD, O\u2019Fallon WM, Rogers RS 3rd, Rooke TW: Natural history of erythromelalgia: presentation and out-come in 168 patients. 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