{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,22]],"date-time":"2026-10-22T04:34:35Z","timestamp":1792643675210,"version":"4.5.0"},"reference-count":71,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2010,12,1]],"date-time":"2010-12-01T00:00:00Z","timestamp":1291161600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/2.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Orphanet J Rare Dis"],"published-print":{"date-parts":[[2010,12]]},"DOI":"10.1186\/1750-1172-5-38","type":"journal-article","created":{"date-parts":[[2010,12,8]],"date-time":"2010-12-08T19:15:19Z","timestamp":1291835719000},"source":"Crossref","is-referenced-by-count":149,"title":["The Schnitzler syndrome"],"prefix":"10.1186","volume":"5","author":[{"given":"Dan","family":"Lipsker","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2010,12,8]]},"reference":[{"issue":"10","key":"201_CR1","doi-asserted-by":"publisher","first-page":"3759","DOI":"10.1182\/blood-2003-03-0801","volume":"102","author":"RA Kyle","year":"2003","unstructured":"Kyle RA, Therneau TM, Rajkumar SV, Remstein ED, Offord JR, Larson DR, Plevak MF, Melton LJ: Long-term follow-up of IgM monoclonal gammopathy of undetermined significance. Blood. 2003, 102 (10): 3759-64. 10.1182\/blood-2003-03-0801.","journal-title":"Blood"},{"issue":"1","key":"201_CR2","first-page":"182","volume":"158","author":"K Claes","year":"2008","unstructured":"Claes K, Bammens B, Delforge M, Evenepoel P, Kuypers D, Vanrenterghem Y: Another devastating complication of the Schnitzler syndrome: AA amyloidosis. Br J Dermatol. 2008, 158 (1): 182-4.","journal-title":"Br J Dermatol"},{"issue":"3","key":"201_CR3","doi-asserted-by":"publisher","first-page":"137","DOI":"10.1016\/j.semarthrit.2007.04.001","volume":"37","author":"HD de Koning","year":"2007","unstructured":"de Koning HD, Bodar EJ, van der Meer JW, Simon A, Schnitzler Syndrome Study Group: Schnitzler syndrome: beyond the case reports: review and follow-up of 94 patients with an emphasis on prognosis and treatment. Semin Arthritis Rheum. 2007, 37 (3): 137-48. 10.1016\/j.semarthrit.2007.04.001.","journal-title":"Semin Arthritis Rheum"},{"key":"201_CR4","volume-title":"Journ\u00e9e Dermatologique d'Angers","author":"L Schnitzler","year":"1972","unstructured":"Schnitzler L: L\u00e9sions urticariennes chroniques permanentes (\u00e9ryth\u00e8me p\u00e9talo\u00efde ?) Cas cliniques, n\u00b0 46 B. Journ\u00e9e Dermatologique d'Angers. 1972"},{"key":"201_CR5","first-page":"363","volume":"81","author":"L Schnitzler","year":"1974","unstructured":"Schnitzler L, Schubert B, Boasson M, Gardais J, Tourmen A: Urticaire chronique, l\u00e9sions osseuses, macroglobulin\u00e9mie IgM: maladie de Waldenstr\u00f6m ? 2\u00e8me pr\u00e9sentation. Bull Soc Fr Dermatol Syphil. 1974, 81: 363-","journal-title":"Bull Soc Fr Dermatol Syphil"},{"issue":"1","key":"201_CR6","doi-asserted-by":"publisher","first-page":"37","DOI":"10.1097\/00005792-200101000-00004","volume":"80","author":"D Lipsker","year":"2001","unstructured":"Lipsker D, Veran Y, Grunenberger F, Cribier B, Heid E, Grosshans E: The Schnitzler syndrome. Four new cases and review of the literature. Medicine (Baltimore). 2001, 80 (1): 37-44. 10.1097\/00005792-200101000-00004.","journal-title":"Medicine (Baltimore)"},{"key":"201_CR7","doi-asserted-by":"publisher","first-page":"212","DOI":"10.1186\/ar2579","volume":"11","author":"HJ Lachmann","year":"2009","unstructured":"Lachmann HJ, Hawkins PN: Developments in the scientific and clinical understanding of autoinflammatory disorders. Arthritis Res Ther. 2009, 11: 212-10.1186\/ar2579.","journal-title":"Arthritis Res Ther"},{"key":"201_CR8","doi-asserted-by":"publisher","first-page":"484","DOI":"10.1016\/S0248-8663(05)81474-2","volume":"15","author":"M Soubrier","year":"1994","unstructured":"Soubrier M, Dubost JJ, Jouanel P, Tridon A, Flori B, Leguille C, Ristori JM, Bussi\u00e8re JL: Multiples complications d'une IgM monoclonale. Rev Med Interne. 1994, 15: 484-6. 10.1016\/S0248-8663(05)81474-2.","journal-title":"Rev Med Interne"},{"issue":"1","key":"201_CR9","doi-asserted-by":"publisher","first-page":"23","DOI":"10.1097\/MD.0b013e3181943f5e","volume":"88","author":"C Kieffer","year":"2009","unstructured":"Kieffer C, Cribier B, Lipsker D: Neutrophilic urticarial dermatosis: a variant of neutrophilic urticaria strongly associated with systemic disease. Report of 9 new cases and review of the literature. Medicine (Baltimore). 2009, 88 (1): 23-31. 10.1097\/MD.0b013e3181943f5e.","journal-title":"Medicine (Baltimore)"},{"key":"201_CR10","doi-asserted-by":"publisher","first-page":"348","DOI":"10.1016\/0090-1229(82)90199-4","volume":"25","author":"JP Clauvel","year":"1982","unstructured":"Clauvel JP, Brouet JC, Danon F, Leibowitch M, Seligmann M: Chronic urticaria with monoclonal IgM: a report of five cases. Clin Immunol Immunopathol. 1982, 25: 348-53. 10.1016\/0090-1229(82)90199-4.","journal-title":"Clin Immunol Immunopathol"},{"issue":"1","key":"201_CR11","first-page":"41","volume":"10","author":"G S\u00e1nchez","year":"2000","unstructured":"S\u00e1nchez G, A\u00f1\u00f3 M, Garc\u00eda-Avil\u00e9s C, Di\u00e9guez I: Schnitzler syndrome: a case study. J Investig Allergol Clin Immunol. 2000, 10 (1): 41-3.","journal-title":"J Investig Allergol Clin Immunol"},{"issue":"2","key":"201_CR12","doi-asserted-by":"publisher","first-page":"94","DOI":"10.1159\/000246220","volume":"193","author":"FR de Castro","year":"1996","unstructured":"de Castro FR, Masouy\u00e9 I, Winkelmann RK, Saurat JH: Urticarial pathology in Schnitzler's (hyper-IgM) syndrome. Dermatology. 1996, 193 (2): 94-9. 10.1159\/000246220.","journal-title":"Dermatology"},{"issue":"12","key":"201_CR13","doi-asserted-by":"publisher","first-page":"1432","DOI":"10.1007\/s00108-007-1956-0","volume":"48","author":"O Tanneberger","year":"2007","unstructured":"Tanneberger O, Buechner S, Zimmerli LU: Schnitzler-Syndrome mit Urtikaria-Vaskulitis. Internist (Berl). 2007, 48 (12): 1432-5. 10.1007\/s00108-007-1956-0.","journal-title":"Internist (Berl)"},{"key":"201_CR14","first-page":"71","volume":"3","author":"P Altmeyer","year":"1977","unstructured":"Altmeyer P, Welke S: Makroglobulin\u00e4mie Waldenstr\u00f6m, assoziiert mit einem chronisch rezidivierenden urtikariellen Exanthem. Akt Dermatol. 1977, 3: 71-6.","journal-title":"Akt Dermatol"},{"key":"201_CR15","doi-asserted-by":"publisher","first-page":"849","DOI":"10.1016\/0091-6749(91)90132-8","volume":"87","author":"SS Berdy","year":"1991","unstructured":"Berdy SS, Bloch KJ: Schnitzler's syndrome: a broader clinical spectrum. J Allergy Clin Immunol. 1991, 87: 849-54. 10.1016\/0091-6749(91)90132-8.","journal-title":"J Allergy Clin Immunol"},{"key":"201_CR16","doi-asserted-by":"publisher","first-page":"113","DOI":"10.1111\/j.1365-2133.1990.tb01831.x","volume":"123","author":"L Borradori","year":"1990","unstructured":"Borradori L, Rybojad M, Puissant A, Dallot A, Verola O, Morel P: Urticarial vasculitis associated with a monoclonal IgM gammopathy: Schnitzler's syndrome. Br J Dermatol. 1990, 123: 113-8. 10.1111\/j.1365-2133.1990.tb01831.x.","journal-title":"Br J Dermatol"},{"key":"201_CR17","first-page":"51","volume":"140","author":"R Carlioz","year":"1989","unstructured":"Carlioz R, Haas C, Jaubert F, Allouche C, Lowenstein W, Le Jeunne C, Durand H: Maladie de Waldenstr\u00f6m avec lymphome diffus \u00e0 grandes cellules immunoblastiques et urticaire chronique. Ann Med Interne. 1989, 140: 51-78.","journal-title":"Ann Med Interne"},{"key":"201_CR18","doi-asserted-by":"publisher","first-page":"32","DOI":"10.1111\/j.1346-8138.1995.tb03337.x","volume":"22","author":"A Morita","year":"1995","unstructured":"Morita A, Sakakibara S, Yokota M, Tsuji T: A case of urticarial vasculitis associated with macroglobulinemia (Schnitzler's syndrome). J Dermatol. 1995, 22: 32-5.","journal-title":"J Dermatol"},{"key":"201_CR19","doi-asserted-by":"publisher","first-page":"206","DOI":"10.1016\/S0190-9622(89)70023-2","volume":"20","author":"M Janier","year":"1989","unstructured":"Janier M, Bonvalet D, Blanc MF, Lemarchand F, Cavelier B, Ribrioux A, Aguenier B, Civatte J: Chronic urticaria and macroglobulinemia (Schnitzler's syndrome): report of two cases. J Am Acad Dermatol. 1989, 20: 206-11. 10.1016\/S0190-9622(89)70023-2.","journal-title":"J Am Acad Dermatol"},{"key":"201_CR20","doi-asserted-by":"publisher","first-page":"379","DOI":"10.1111\/j.0954-6820.1980.tb09742.x","volume":"207","author":"E Olsen","year":"1980","unstructured":"Olsen E, Forre O, Lea T, Langeland T: Unique antigenic determinants (idiotypes) used as markers in a patient with macroglobulinemia urticaria: similar idiotypes demonstrated in the skin and on peripheral blood lymphocytes. Acta Med Scan. 1980, 207: 379-84. 10.1111\/j.0954-6820.1980.tb09742.x.","journal-title":"Acta Med Scan"},{"key":"201_CR21","first-page":"91","volume":"15","author":"P Puddu","year":"1997","unstructured":"Puddu P, Cianchini G, Girardelli CR, Colonna l, Gatti S, De Pita O: Schnitzler's syndrome: report of a new case and review of the literature. Clin Exp Rheumatol. 1997, 15: 91-5.","journal-title":"Clin Exp Rheumatol"},{"key":"201_CR22","doi-asserted-by":"publisher","first-page":"954","DOI":"10.1046\/j.1365-2133.2000.03477.x","volume":"142","author":"D Lipsker","year":"2000","unstructured":"Lipsker D, Spehner D, Drillien R, Schmitt P, Cribier B, Heid E, Humbel RL, Grosshans E: Schnitzler syndrome: heteregous immunopathologic findings involving IgM-skin interactions. Br J Dermatol. 2000, 142: 954-9. 10.1046\/j.1365-2133.2000.03477.x.","journal-title":"Br J Dermatol"},{"key":"201_CR23","doi-asserted-by":"publisher","first-page":"567","DOI":"10.1007\/s10067-010-1375-9","volume":"29","author":"E Besada","year":"2010","unstructured":"Besada E, Nossent H: Dramatic response to IL1-RA treatment in longstanding multidrug resistant Schnitzler's syndrome: a case report and literature review. Clin Rheumatol. 2010, 29: 567-71. 10.1007\/s10067-010-1375-9.","journal-title":"Clin Rheumatol"},{"key":"201_CR24","doi-asserted-by":"publisher","first-page":"294","DOI":"10.1007\/s002560050385","volume":"27","author":"M Lecompte","year":"1998","unstructured":"Lecompte M, Blais G, Bisson G, Maynard B: Schnitzler's syndrome. Skeletal radiol. 1998, 27: 294-6. 10.1007\/s002560050385.","journal-title":"Skeletal radiol"},{"key":"201_CR25","doi-asserted-by":"publisher","first-page":"1325","DOI":"10.2214\/ajr.175.5.1751325","volume":"175","author":"S De Waele","year":"2000","unstructured":"De Waele S, Lecouvet FE, Malghem J, et al: Schnitzler's syndrome: an unusual cause of bone pain with suggestive imaging features. AJR. 2000, 175: 1325-1327.","journal-title":"AJR"},{"key":"201_CR26","first-page":"203","volume":"4","author":"FJ Ferrando","year":"1994","unstructured":"Ferrando FJ, Pujol J, Hortells JL, Navarro M, Pinol J, Carapeto FJ: Schnitzler's syndrome: report of a case with bone osteolysis. J Invest Allergol Clin Immunol. 1994, 4: 203-5.","journal-title":"J Invest Allergol Clin Immunol"},{"key":"201_CR27","first-page":"1948","volume":"11","author":"D Lambert","year":"1982","unstructured":"Lambert D, Legoux A, Chapuis JL, Benoit JP, Putelat R: Urticaire chronique et macroglobulin\u00e9mie. Nouv Presse Med. 1982, 11: 1948-","journal-title":"Nouv Presse Med"},{"key":"201_CR28","doi-asserted-by":"publisher","first-page":"285","DOI":"10.1016\/S0248-8663(00)80049-1","volume":"21","author":"P Germain","year":"2000","unstructured":"Germain P, Fach J, Bui N, Traissac T, Delbrel X, Bras ML, Longy-Boursier M: Syndrome de Schnitzler: une cause rare d'urticaire syst\u00e9mique. Rev Med Interne. 2000, 21: 285-9. 10.1016\/S0248-8663(00)80049-1.","journal-title":"Rev Med Interne"},{"key":"201_CR29","doi-asserted-by":"publisher","first-page":"860","DOI":"10.1055\/s-2008-1043079","volume":"121","author":"G Winckelmann","year":"1996","unstructured":"Winckelmann G, Nagel HG, Maier R, Reuther G: Schnitzler-Syndrom als Ursache eines rezidivierenden Fiebers unbekannter Ursache. Dtsch Med Wschr. 1996, 121: 860-4. 10.1055\/s-2008-1043079.","journal-title":"Dtsch Med Wschr"},{"key":"201_CR30","doi-asserted-by":"publisher","first-page":"107","DOI":"10.1007\/s10067-007-0758-z","volume":"27","author":"AF Fl\u00f3rez","year":"2008","unstructured":"Fl\u00f3rez AF, Gallardo Agromayor E, Garc\u00eda-Barredo R, Landeras Alvaro RM, Gorri\u00f1o Angulo M, Mart\u00ednez-Taboada VM, Fern\u00e1ndez Echevarr\u00eda MA: Radiological aid to clinical diagnosis of Schnitzler's syndrome: multimodality imaging approach. Clin Rheumatol. 2008, 27: 107-10.","journal-title":"Clin Rheumatol"},{"key":"201_CR31","doi-asserted-by":"publisher","first-page":"225","DOI":"10.1148\/radiology.220.1.r01jl24225","volume":"220","author":"K Chanchairujira","year":"2001","unstructured":"Chanchairujira K, Chung CB, Lai YM, et al: Intramedullary osteosclerosis: imaging features in nine patients. Radiology. 2001, 220: 225-230.","journal-title":"Radiology"},{"key":"201_CR32","first-page":"413","volume":"58","author":"MS Doutre","year":"1987","unstructured":"Doutre MS, Beylot C, Bioulac P, Bezian JH: Monoclonal IgM and chronic urticaria: two cases. Ann Allergy. 1987, 58: 413-4.","journal-title":"Ann Allergy"},{"key":"201_CR33","doi-asserted-by":"publisher","first-page":"201","DOI":"10.1046\/j.1440-0960.1999.00361.x","volume":"40","author":"B Welsh","year":"1999","unstructured":"Welsh B, Tate B: Schnitzler's syndrome: report of a case with progression to Waldenstrom's macroglobulinaemia. Australas J Dermatol. 1999, 40: 201-3. 10.1046\/j.1440-0960.1999.00361.x.","journal-title":"Australas J Dermatol"},{"key":"201_CR34","first-page":"221","volume":"52","author":"H Barri\u00e8re","year":"1976","unstructured":"Barri\u00e8re H, Schnitzler L, Moulin G, Grolleau Y: L\u00e9sions urticariennes chroniques et macroglobulin\u00e9mie. A propos de cinq observations. Sem H\u00f4p Paris. 1976, 52: 221-7.","journal-title":"A propos de cinq observations. Sem H\u00f4p Paris"},{"key":"201_CR35","doi-asserted-by":"publisher","first-page":"348","DOI":"10.1016\/0090-1229(82)90199-4","volume":"25","author":"JP Clauvel","year":"1982","unstructured":"Clauvel JP, Brouet JC, Danon F, Leibowitch M, Seligmann M: Chronic urticaria with monoclonal IgM: a report of five cases. Clin Immunol Immunopathol. 1982, 25: 348-53. 10.1016\/0090-1229(82)90199-4.","journal-title":"Clin Immunol Immunopathol"},{"key":"201_CR36","first-page":"95","volume":"13","author":"P Goupille","year":"1995","unstructured":"Goupille P, Pizzuti P, Diot E, Jattiot F, Guilmot JL, Valat JP: Schnitzler's syndrome (urticaria with macroglobulinemia) dramatically improved with corticosteroids. Clin Exp Rheumatol. 1995, 13: 95-8.","journal-title":"Clin Exp Rheumatol"},{"key":"201_CR37","doi-asserted-by":"crossref","first-page":"22","DOI":"10.2340\/00015555722224","volume":"72","author":"L Machet","year":"1991","unstructured":"Machet L, Vaillant L, Machet MC, Esteve E, De Muret A, Khallouf R, Arbeille B, Muller C, Lorette G: Schnitzler's syndrome (urticaria and macroglobulinemia) associated with pseudoxanthoma elasticum. Acta Derm Venereol (Stockh). 1991, 72: 22-4.","journal-title":"Acta Derm Venereol (Stockh)"},{"key":"201_CR38","first-page":"1758","volume":"21","author":"P Paulin","year":"1992","unstructured":"Paulin P, Cusset C, Jaquelin L, Pages JM, Chapalain JC: Syndrome de Schnitzler: une nouvelle observation. Presse Med. 1992, 21: 1758-61.","journal-title":"Presse Med"},{"key":"201_CR39","doi-asserted-by":"crossref","first-page":"284","DOI":"10.1177\/112070001002000225","volume":"20","author":"E Romanini","year":"2010","unstructured":"Romanini E, Magaletti M, D'Aviera L, Antonelli S: Severe heterotopic ossification after total hip arthroplasty in Schnitzler syndrome. Hip Int. 2010, 20: 284-6.","journal-title":"Hip Int"},{"key":"201_CR40","doi-asserted-by":"publisher","first-page":"132","DOI":"10.1111\/j.1365-2133.1995.tb02507.x","volume":"133","author":"D Nashan","year":"1995","unstructured":"Nashan D, Sunderk\u00f6tter C, Bonsmann G, Luger T, Goerdt S: chronic urticaria, arthralgia, raised eythrocyte sedimentation rate and IgG paraproteinaemia: a variant of Schnitzler's syndrome ?. Br J Dermatol. 1995, 133: 132-4. 10.1111\/j.1365-2133.1995.tb02507.x.","journal-title":"Br J Dermatol"},{"key":"201_CR41","doi-asserted-by":"crossref","first-page":"280","DOI":"10.2340\/00015555-0233","volume":"87","author":"R Treudler","year":"2007","unstructured":"Treudler R, Kauer F, Simon JC: Striking effect of the IL-1 receptor antagonist Anakinra in chronic urticarial rash with polyclonal increase in IgA and IgG. Acta Derm Venereol (Stockh). 2007, 87: 280-1.","journal-title":"Acta Derm Venereol (Stockh)"},{"key":"201_CR42","first-page":"783","volume":"120","author":"M Rybojad","year":"1993","unstructured":"Rybojad M, Moraillon I, Cordoliani F, Lebb\u00e9 C, Baccard M, Flageul B, Weiss L, Morel P: Syndrome de Schnitzler aved d\u00e9ficit g\u00e9n\u00e9tique en C4: deux observations. Ann Dermatol Venereol. 1993, 120: 783-5.","journal-title":"Ann Dermatol Venereol"},{"key":"201_CR43","first-page":"118","volume":"8","author":"H Tomkova","year":"1998","unstructured":"Tomkova H, Shirafuji Y, Arata J: Schnitzler's syndrome versus adult onset Still's disease. Eur J Dermatol. 1998, 8: 118-21.","journal-title":"Eur J Dermatol"},{"key":"201_CR44","doi-asserted-by":"crossref","first-page":"22","DOI":"10.2340\/00015555722224","volume":"72","author":"L Machet","year":"1991","unstructured":"Machet L, Vaillant L, Machet MC, Esteve E, De Muret A, Khallouf R, Arbeille B, Muller C, Lorette G: Schnitzler's syndrome (urticaria and macroglobulinemia) associated with pseudoxanthoma elasticum. Acta Derm Venereol (Stockh). 1991, 72: 22-4.","journal-title":"Acta Derm Venereol (Stockh)"},{"key":"201_CR45","volume-title":"3rd Congress of EADV, 26-30 Sept","author":"ML Wilhelmi","year":"1993","unstructured":"Wilhelmi ML, Ocana Wilhelmi J, Ocana Sierra J: Schnitzler's syndrome and pseudoxanthoma elasticum. 3rd Congress of EADV, 26-30 Sept. 1993, Copenhagen, Abst FC20, 159"},{"key":"201_CR46","doi-asserted-by":"publisher","first-page":"316","DOI":"10.1016\/S0190-9622(94)70031-1","volume":"30","author":"C Lebbe","year":"1994","unstructured":"Lebbe C, Rybojad M, Klein F, Oksenhendler E, Catala M, Danon F, Morel P: Schnitzler's syndrome associated with sensorimotor neuropathy. J Am Acad Dermatol. 1994, 30: 316-8. 10.1016\/S0190-9622(94)70031-1.","journal-title":"J Am Acad Dermatol"},{"key":"201_CR47","first-page":"281","volume":"66","author":"A Lauwers","year":"1999","unstructured":"Lauwers A, Chouvy V, Mosnier JF, Misery L, Alexandre C: A case of Schnitzler's syndrome with nodular regenerative hyperplasia of the liver. Rev Rhum Engl Ed. 1999, 66: 281-3.","journal-title":"Rev Rhum Engl Ed"},{"key":"201_CR48","first-page":"660","volume":"19","author":"TH Westhoff","year":"2006","unstructured":"Westhoff TH, Zidek W, Uharek L, Steinhoff-Georgieva J, van der Giet M: Impairment of renal function in Schnitzler's syndrome. J Nephrol. 2006, 19: 660-3.","journal-title":"J Nephrol"},{"issue":"3","key":"201_CR49","first-page":"366","volume":"21","author":"G Famularo","year":"2003","unstructured":"Famularo G, Barracchini A, Minisola G: Severe thrombophilia with antiphospholipid syndrome and hyperhomocysteinemia in a patient with Schnitzler's syndrome. Clin Exp Rheumatol. 2003, 21 (3): 366-8.","journal-title":"Clin Exp Rheumatol"},{"key":"201_CR50","first-page":"459","volume":"120","author":"JL Verret","year":"1993","unstructured":"Verret JL, Leclech C, Rousselet MC, Hurez D, Schnitzler L: Syndrome de Schnitzler et maladie de Waldenstr\u00f6m. Evolution terminale du cas princeps. Ann Dermatol Venereol. 1993, 120: 459-60.","journal-title":"Evolution terminale du cas princeps. Ann Dermatol Venereol"},{"key":"201_CR51","first-page":"71","volume":"3","author":"P Altmeyer","year":"1977","unstructured":"Altmeyer P, Welke S: Makroglobulin\u00e4mie Waldenstr\u00f6m, assoziiert mit einem chronisch rezidivierenden urtikariellen Exanthem. Akt Dermatol. 1977, 3: 71-6.","journal-title":"Akt Dermatol"},{"key":"201_CR52","first-page":"780","volume":"14","author":"S Govindaraju","year":"1993","unstructured":"Govindaraju S, Brochot P, Ringot AC, Paternotte L, Morrone A, Eschard JP, Etienne JC: Urticaire chronique-macroglobulin\u00e9mie (syndrome de Schnitzler): \u00e9volution vers un my\u00e9lome \u00e0 IgM. A propos d'un cas. Rev Med Interne. 1993, 14: 780-3.","journal-title":"A propos d'un cas. Rev Med Interne"},{"key":"201_CR53","doi-asserted-by":"crossref","first-page":"413","DOI":"10.2340\/0001555576413413","volume":"76","author":"L Machet","year":"1996","unstructured":"Machet L, Vaillant L, Machet MC, Reisenleiter M, Goupille P, Lorette G: Schnitzler's syndrome (urticaria and macroglobulinemia): evolution to Waldenstr\u00f6m's disease is not uncommon. Acta Derm Venereol (Stockh). 1996, 76: 413-","journal-title":"Acta Derm Venereol (Stockh)"},{"key":"201_CR54","doi-asserted-by":"publisher","first-page":"855","DOI":"10.1016\/S0190-9622(89)80127-6","volume":"20","author":"RM Pujol","year":"1989","unstructured":"Pujol RM, Barnadas MA, Brunet S, de Moragas JM: Urticarial dermatosis associated with Waldenstr\u00f6m's macroglobulinemia. J Am Acad Dermatol. 1989, 20: 855-7. 10.1016\/S0190-9622(89)80127-6.","journal-title":"J Am Acad Dermatol"},{"key":"201_CR55","doi-asserted-by":"publisher","first-page":"201","DOI":"10.1046\/j.1440-0960.1999.00361.x","volume":"40","author":"B Welsh","year":"1999","unstructured":"Welsh B, Tate B: Schnitzler's syndrome: report of a case with progression to Waldenstrom's macroglobulinaemia. Australas J Dermatol. 1999, 40: 201-3. 10.1046\/j.1440-0960.1999.00361.x.","journal-title":"Australas J Dermatol"},{"issue":"4","key":"201_CR56","doi-asserted-by":"publisher","first-page":"827","DOI":"10.1111\/j.1365-2133.2006.07417.x","volume":"155","author":"S Dalle","year":"2006","unstructured":"Dalle S, Balme B, Sebban C, Pariset C, Berger F, Thomas L: Schnitzler syndrome associated with systemic marginal zone B-cell lymphoma. Br J Dermatol. 2006, 155 (4): 827-9. 10.1111\/j.1365-2133.2006.07417.x.","journal-title":"Br J Dermatol"},{"key":"201_CR57","first-page":"931","volume":"25","author":"M Gilson","year":"2007","unstructured":"Gilson M, Abad S, Larroche C, Dhote R: Treatment of Schnitzler syndrome with anakinra. Clin Exp Rheumatol. 2007, 25: 931-","journal-title":"Clin Exp Rheumatol"},{"key":"201_CR58","doi-asserted-by":"publisher","first-page":"244","DOI":"10.1016\/0091-6749(91)90335-L","volume":"88","author":"JH Saurat","year":"1991","unstructured":"Saurat JH, Schifferli J, Steiger G, Dayer JM, Didierjean L: Anti-interleukin-1 alpha autoantibodies in humans: characterization, isotype distribution, and receptor-binding inhibition--higher frequency in Schnitzler's syndrome (urticaria and macroglobulinemia). J Allergy Clin Immunol. 1991, 88: 244-56. 10.1016\/0091-6749(91)90335-L.","journal-title":"J Allergy Clin Immunol"},{"key":"201_CR59","first-page":"362","volume":"14","author":"P Modiano","year":"1995","unstructured":"Modiano P, Barbaud A, Laveine E, Cabut S, Weber M, Schmutz JL: Efficacit\u00e9 de la PUVAth\u00e9rapie dans un syndrome de Schnitzler. Nouv Dermatol. 1995, 14: 362-3.","journal-title":"Nouv Dermatol"},{"issue":"6","key":"201_CR60","doi-asserted-by":"publisher","first-page":"1070","DOI":"10.1016\/j.jaad.2008.12.040","volume":"61","author":"H Murota","year":"2009","unstructured":"Murota H, Shoda Y, Ishibashi T, Sugahara H, Matsumura I, Katayama I: Improvement of recurrent urticaria in a patient with Schnitzler syndrome associated with B-cell lymphoma with combination rituximab and radiotherapy. J Am Acad Dermatol. 2009, 61 (6): 1070-5. 10.1016\/j.jaad.2008.12.040.","journal-title":"J Am Acad Dermatol"},{"issue":"1","key":"201_CR61","doi-asserted-by":"publisher","first-page":"260","DOI":"10.1016\/j.jaci.2007.09.021","volume":"121","author":"JG Ryan","year":"2008","unstructured":"Ryan JG, de Koning HD, Beck LA, Booty MG, Kastner DL, Simon A: IL-1 blockade in Schnitzler syndrome: ex vivo findings correlate with clinical remission. J Allergy Clin Immunol. 2008, 121 (1): 260-2. 10.1016\/j.jaci.2007.09.021.","journal-title":"J Allergy Clin Immunol"},{"issue":"10","key":"201_CR62","doi-asserted-by":"publisher","first-page":"1304","DOI":"10.1093\/rheumatology\/kep222","volume":"48","author":"C Pizzirani","year":"2009","unstructured":"Pizzirani C, Falzoni S, Govoni M, La Corte R, Donadei S, Di Virgilio F, Trotta F, Lo Monaco A: Dysfunctional inflammasome in Schnitzler's syndrome. Rheumatology (Oxford). 2009, 48 (10): 1304-8. 10.1093\/rheumatology\/kep222.","journal-title":"Rheumatology (Oxford)"},{"key":"201_CR63","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1684\/ecn.2009.0164","volume":"20","author":"P Migliorini","year":"2009","unstructured":"Migliorini P, Del Corso I, Tommasi C, Boraschi D: Free circulating interleukin-18 is increased in the Schnitzler syndrome: a new auto-inflammatory disease. Eur Cytokine Netw. 2009, 20: 108-11.","journal-title":"Eur Cytokine Netw"},{"issue":"2","key":"201_CR64","doi-asserted-by":"publisher","first-page":"500","DOI":"10.1016\/j.jaci.2009.10.066","volume":"125","author":"J Loock","year":"2010","unstructured":"Loock J, Lamprecht P, Timmann C, Mrowietz U, Csernok E, Gross WL: Genetic predisposition (NLRP3 V198 M mutation) for IL-1-mediated inflammation in a patient with Schnitzler syndrome. J Allergy Clin Immunol. 2010, 125 (2): 500-2. 10.1016\/j.jaci.2009.10.066.","journal-title":"J Allergy Clin Immunol"},{"key":"201_CR65","doi-asserted-by":"publisher","first-page":"1190","DOI":"10.1111\/j.1365-4632.2009.04151.x","volume":"48","author":"C Schuster","year":"2009","unstructured":"Schuster C, Kr\u00e4nke B, Aberer E, Arbab E, Sturm G, Aberer W: Schnitzler syndrome: response to anakinra in two cases and review of the literature. Int J Dermatol. 2009, 48: 1190-4. 10.1111\/j.1365-4632.2009.04151.x.","journal-title":"Int J Dermatol"},{"issue":"8","key":"201_CR66","doi-asserted-by":"publisher","first-page":"1046","DOI":"10.1001\/archderm.143.8.1046","volume":"143","author":"B Asli","year":"2007","unstructured":"Asli B, Bienvenu B, Cordoliani F, Brouet JC, Uzunhan Y, Arnulf B, Malphettes M, Rybojad M, Fermand JP: Chronic urticaria and monoclonal IgM gammopathy (Schnitzler syndrome): report of 11 cases treated with pefloxacin. Arch Dermatol. 2007, 143 (8): 1046-50. 10.1001\/archderm.143.8.1046.","journal-title":"Arch Dermatol"},{"issue":"6","key":"201_CR67","doi-asserted-by":"publisher","first-page":"359","DOI":"10.3816\/CLM.2008.n.053","volume":"8","author":"E Kastritis","year":"2008","unstructured":"Kastritis E, Katoulis A, Terpos E, Panayiotides I, Gavriatopoulopu M, Dimopopoulos MA: Schnitzler's syndrome: increased levels of bone formation and angiogenesis factors are reduced after successful pefloxacin treatment. Clin Lymphoma Myeloma. 2008, 8 (6): 359-62. 10.3816\/CLM.2008.n.053.","journal-title":"Clin Lymphoma Myeloma"},{"issue":"7","key":"201_CR68","doi-asserted-by":"publisher","first-page":"2226","DOI":"10.1002\/art.21101","volume":"52","author":"VM Martinez-Taboada","year":"2005","unstructured":"Martinez-Taboada VM, Fontalba A, Blanco R, Fern\u00e1ndez-Luna JL: Successful treatment of refractory Schnitzler syndrome with anakinra: comment on the article by Hawkins et al. Arthritis Rheum. 2005, 52 (7): 2226-7. 10.1002\/art.21101.","journal-title":"Arthritis Rheum"},{"issue":"2","key":"201_CR69","doi-asserted-by":"crossref","first-page":"633","DOI":"10.1177\/039463201002300226","volume":"23","author":"N Cascavilla","year":"2010","unstructured":"Cascavilla N, Bisceglia M, D'Arena G: Successful treatment of Schnitzler's syndrome with anakinra after failure of rituximab trial. Int J Immunopathol Pharmacol. 2010, 23 (2): 633-6.","journal-title":"Int J Immunopathol Pharmacol"},{"issue":"6","key":"201_CR70","doi-asserted-by":"publisher","first-page":"617","DOI":"10.1016\/S1081-1206(10)60064-6","volume":"100","author":"PA Frischmeyer-Guerrerio","year":"2008","unstructured":"Frischmeyer-Guerrerio PA, Rachamalla R, Saini SS: Remission of Schnitzler syndrome after treatment with anakinra. Ann Allergy Asthma Immunol. 2008, 100 (6): 617-9. 10.1016\/S1081-1206(10)60064-6.","journal-title":"Ann Allergy Asthma Immunol"},{"key":"201_CR71","doi-asserted-by":"publisher","first-page":"621","DOI":"10.1146\/annurev.immunol.25.022106.141627","volume":"27","author":"SL Masters","year":"2009","unstructured":"Masters SL, Simon A, Aksentijevich I, Kastner DL: Horror autoinflammaticus: the molecular pathophysiology of autoinflammatory disease. Annu Rev Immunol. 2009, 27: 621-68. 10.1146\/annurev.immunol.25.022106.141627.","journal-title":"Annu Rev Immunol"}],"container-title":["Orphanet Journal of Rare Diseases"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/1750-1172-5-38.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1186\/1750-1172-5-38\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/1750-1172-5-38.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T22:14:44Z","timestamp":1712009684000},"score":1,"resource":{"primary":{"URL":"https:\/\/ojrd.biomedcentral.com\/articles\/10.1186\/1750-1172-5-38"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,12]]},"references-count":71,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2010,12]]}},"alternative-id":["201"],"URL":"https:\/\/doi.org\/10.1186\/1750-1172-5-38","relation":{},"ISSN":["1750-1172"],"issn-type":[{"value":"1750-1172","type":"electronic"}],"subject":[],"published":{"date-parts":[[2010,12]]},"article-number":"38"}}