{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,13]],"date-time":"2026-11-13T11:09:21Z","timestamp":1794568161117,"version":"4.9.1"},"reference-count":143,"publisher":"Springer Science and Business Media LLC","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Orphanet J Rare Dis","Orphanet Journal of Rare Diseases"],"published-print":{"date-parts":[[2011]]},"DOI":"10.1186\/1750-1172-6-60","type":"journal-article","created":{"date-parts":[[2011,9,8]],"date-time":"2011-09-08T19:54:17Z","timestamp":1315511657000},"page":"60","source":"Crossref","is-referenced-by-count":537,"title":["Atypical hemolytic uremic syndrome"],"prefix":"10.1186","volume":"6","author":[{"given":"Chantal","family":"Loirat","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V\u00e9ronique","family":"Fr\u00e9meaux-Bacchi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","reference":[{"key":"10.1186\/1750-1172-6-60-B2","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2004100861"},{"key":"10.1186\/1750-1172-6-60-B3","doi-asserted-by":"publisher","DOI":"10.1007\/s00431-008-0745-7"},{"key":"10.1186\/1750-1172-6-60-B4","doi-asserted-by":"publisher","DOI":"10.1007\/s00431-009-1039-4"},{"key":"10.1186\/1750-1172-6-60-B5","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1637-4"},{"key":"10.1186\/1750-1172-6-60-B6","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1690-z"},{"key":"-","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2005.01047.x"},{"key":"10.1186\/1750-1172-6-60-B8","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2009-03-207563"},{"key":"10.1186\/1750-1172-6-60-B10","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa0707330"},{"key":"10.1186\/1750-1172-6-60-B13","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.10499"},{"key":"10.1186\/1750-1172-6-60-B15","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM197505222922102"},{"key":"10.1186\/1750-1172-6-60-B16","doi-asserted-by":"publisher","DOI":"10.1038\/ncpneph0670"},{"key":"10.1186\/1750-1172-6-60-B17","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2006080811"},{"key":"10.1186\/1750-1172-6-60-B18","doi-asserted-by":"publisher","DOI":"10.2215\/CJN.02210310"},{"key":"10.1186\/1750-1172-6-60-B19","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2004.02.010"},{"key":"10.1186\/1750-1172-6-60-B20","doi-asserted-by":"publisher","DOI":"10.1111\/j.1469-1809.2009.00554.x"},{"key":"10.1186\/1750-1172-6-60-B21","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2005-10-007252"},{"key":"10.1186\/1750-1172-6-60-B22","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfq010"},{"key":"10.1186\/1750-1172-6-60-B23","doi-asserted-by":"publisher","DOI":"10.1002\/humu.21256"},{"key":"10.1186\/1750-1172-6-60-B24","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0010208"},{"key":"10.1186\/1750-1172-6-60-B25","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2009-09-243790"},{"key":"10.1186\/1750-1172-6-60-B26","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddi066"},{"key":"10.1186\/1750-1172-6-60-B27","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.2008.064766"},{"key":"10.1186\/1750-1172-6-60-B29","doi-asserted-by":"publisher","DOI":"10.1136\/adc.65.7.716"},{"key":"10.1186\/1750-1172-6-60-B31","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-008-0872-4"},{"key":"10.1186\/1750-1172-6-60-B32","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfp166"},{"key":"10.1186\/1750-1172-6-60-B33","doi-asserted-by":"publisher","DOI":"10.3109\/0886022X.2010.486491"},{"key":"10.1186\/1750-1172-6-60-B34","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1636-5"},{"key":"10.1186\/1750-1172-6-60-B35","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1649-0"},{"key":"10.1186\/1750-1172-6-60-B37","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2010030315"},{"key":"10.1186\/1750-1172-6-60-B38","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra0902814"},{"key":"10.1186\/1750-1172-6-60-B40","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1606-y"},{"key":"10.1186\/1750-1172-6-60-B41","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfq160"},{"key":"10.1186\/1750-1172-6-60-B42","doi-asserted-by":"publisher","DOI":"10.1007\/s004670050058"},{"key":"10.1186\/1750-1172-6-60-B44","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM200104053441406"},{"key":"10.1186\/1750-1172-6-60-B45","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa0810739"},{"key":"10.1186\/1750-1172-6-60-B47","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.1017087108"},{"key":"10.1186\/1750-1172-6-60-B48","doi-asserted-by":"publisher","DOI":"10.1038\/nsmb.2018"},{"key":"10.1186\/1750-1172-6-60-B49","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.med.59.060106.185110"},{"key":"10.1186\/1750-1172-6-60-B50","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1555-5"},{"key":"10.1186\/1750-1172-6-60-B51","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.2010.08295.x"},{"key":"10.1186\/1750-1172-6-60-B52","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2007-08-106153"},{"key":"10.1186\/1750-1172-6-60-B53","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2009-03-205096"},{"key":"10.1186\/1750-1172-6-60-B54","doi-asserted-by":"publisher","DOI":"10.1084\/jem.20070301"},{"key":"10.1186\/1750-1172-6-60-B55","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2010050451"},{"key":"10.1186\/1750-1172-6-60-B57","doi-asserted-by":"publisher","DOI":"10.1111\/j.1523-1755.1998.00824.x"},{"key":"10.1186\/1750-1172-6-60-B58","doi-asserted-by":"publisher","DOI":"10.1002\/humu.20435"},{"key":"-","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M900814200"},{"key":"10.1186\/1750-1172-6-60-B61","doi-asserted-by":"publisher","DOI":"10.1016\/j.jim.2010.12.020"},{"key":"10.1186\/1750-1172-6-60-B63","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pmed.0030431"},{"key":"10.1186\/1750-1172-6-60-B64","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.40.9.676"},{"key":"10.1186\/1750-1172-6-60-B65","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2004050380"},{"key":"10.1186\/1750-1172-6-60-B66","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2007-02-071472"},{"key":"10.1186\/1750-1172-6-60-B68","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfp388"},{"key":"10.1186\/1750-1172-6-60-B69","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pgen.0030041"},{"key":"10.1186\/1750-1172-6-60-B72","doi-asserted-by":"publisher","DOI":"10.1203\/PDR.0b013e3181b1bd4a"},{"key":"10.1186\/1750-1172-6-60-B73","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.2135497100"},{"key":"10.1186\/1750-1172-6-60-B74","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(03)14742-3"},{"key":"10.1186\/1750-1172-6-60-B75","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2005101051"},{"key":"10.1186\/1750-1172-6-60-B76","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.2004.019083"},{"key":"10.1186\/1750-1172-6-60-B77","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2005010103"},{"key":"10.1186\/1750-1172-6-60-B78","doi-asserted-by":"publisher","DOI":"10.1016\/j.molimm.2007.05.004"},{"key":"10.1186\/1750-1172-6-60-B80","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0603420103"},{"key":"10.1186\/1750-1172-6-60-B82","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-009-1415-3"},{"key":"10.1186\/1750-1172-6-60-B83","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2008-01-133702"},{"key":"10.1186\/1750-1172-6-60-B84","doi-asserted-by":"publisher","DOI":"10.2215\/CJN.06281208"},{"key":"10.1186\/1750-1172-6-60-B85","doi-asserted-by":"publisher","DOI":"10.1016\/j.molimm.2005.11.008"},{"key":"10.1186\/1750-1172-6-60-B86","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.2005.030783"},{"key":"10.1186\/1750-1172-6-60-B87","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddg363"},{"key":"10.1186\/1750-1172-6-60-B88","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2009-05-223834"},{"key":"10.1186\/1750-1172-6-60-B90","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-008-0964-1"},{"key":"10.1186\/1750-1172-6-60-B91","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.2009.07916.x"},{"key":"10.1186\/1750-1172-6-60-B92","doi-asserted-by":"publisher","DOI":"10.1097\/01.inf.0000223494.83542.ad"},{"key":"10.1186\/1750-1172-6-60-B93","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2007.03.055"},{"key":"10.1186\/1750-1172-6-60-B94","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-007-0518-y"},{"key":"10.1186\/1750-1172-6-60-B95","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-008-0863-5"},{"key":"10.1186\/1750-1172-6-60-B96","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2005010086"},{"key":"10.1186\/1750-1172-6-60-B97","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.2005.05420.x"},{"key":"10.1186\/1750-1172-6-60-B98","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1609-8"},{"key":"10.1186\/1750-1172-6-60-B99","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2004.12.004"},{"key":"10.1186\/1750-1172-6-60-B100","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2008-03-144691"},{"key":"10.1186\/1750-1172-6-60-B101","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2008.02297.x"},{"key":"10.1186\/1750-1172-6-60-B102","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pmed.1001013"},{"key":"10.1186\/1750-1172-6-60-B103","doi-asserted-by":"publisher","DOI":"10.1055\/s-0030-1262890"},{"key":"10.1186\/1750-1172-6-60-B105","doi-asserted-by":"publisher","DOI":"10.1067\/mpd.2001.112649"},{"key":"10.1186\/1750-1172-6-60-B106","doi-asserted-by":"publisher","DOI":"10.1007\/s004670100609"},{"key":"10.1186\/1750-1172-6-60-B107","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-006-0237-9"},{"key":"10.1186\/1750-1172-6-60-B108","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2004.10.018"},{"key":"10.1186\/1750-1172-6-60-B109","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-007-0438-x"},{"key":"10.1186\/1750-1172-6-60-B110","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/17.4.684"},{"key":"10.1186\/1750-1172-6-60-B111","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-003-1192-3"},{"key":"10.1186\/1750-1172-6-60-B113","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-008-0833-y"},{"key":"10.1186\/1750-1172-6-60-B115","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-009-1306-7"},{"key":"10.1186\/1750-1172-6-60-B116","doi-asserted-by":"publisher","DOI":"10.1007\/s004670050515"},{"key":"10.1186\/1750-1172-6-60-B117","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2008.01.026"},{"key":"10.1186\/1750-1172-6-60-B118","doi-asserted-by":"publisher","DOI":"10.1007\/s10157-009-0205-3"},{"key":"10.1186\/1750-1172-6-60-B119","doi-asserted-by":"publisher","DOI":"10.1016\/j.molimm.2006.10.005"},{"key":"10.1186\/1750-1172-6-60-B120","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-009-1188-8"},{"key":"10.1186\/1750-1172-6-60-B122","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfn063"},{"key":"-","doi-asserted-by":"publisher","DOI":"10.1093\/ndtplus\/sfp109"},{"key":"10.1186\/1750-1172-6-60-B124","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2009.12.026"},{"key":"10.1186\/1750-1172-6-60-B125","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2008080906"},{"key":"10.1186\/1750-1172-6-60-B126","doi-asserted-by":"publisher","DOI":"10.1111\/j.1537-2995.2007.01405.x"},{"key":"10.1186\/1750-1172-6-60-B127","doi-asserted-by":"publisher","DOI":"10.1016\/j.transci.2008.09.001"},{"key":"-","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-3046.2008.00910.x"},{"key":"10.1186\/1750-1172-6-60-B130","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2010.03156.x"},{"key":"10.1186\/1750-1172-6-60-B131","doi-asserted-by":"publisher","DOI":"10.1038\/nrneph.2010.155"},{"key":"10.1186\/1750-1172-6-60-B132","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2008.06.027"},{"key":"10.1186\/1750-1172-6-60-B133","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2009.02586.x"},{"key":"10.1186\/1750-1172-6-60-B134","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2009.02870.x"},{"key":"10.1186\/1750-1172-6-60-B135","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2005.01184.x"},{"key":"10.1186\/1750-1172-6-60-B136","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfp377"},{"key":"10.1186\/1750-1172-6-60-B137","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2009.08.011"},{"key":"10.1186\/1750-1172-6-60-B138","doi-asserted-by":"publisher","DOI":"10.1016\/j.transproceed.2010.03.048"},{"key":"10.1186\/1750-1172-6-60-B139","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2009.02647.x"},{"key":"10.1186\/1750-1172-6-60-B140","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(02)08560-4"},{"key":"10.1186\/1750-1172-6-60-B141","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2005.00783.x"},{"key":"10.1186\/1750-1172-6-60-B142","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-003-1371-2"},{"key":"10.1186\/1750-1172-6-60-B145","doi-asserted-by":"publisher","DOI":"10.2215\/CJN.02170508"},{"key":"10.1186\/1750-1172-6-60-B146","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2010.03228.x"},{"key":"10.1186\/1750-1172-6-60-B147","doi-asserted-by":"publisher","DOI":"10.1053\/j.ajkd.2011.04.008"},{"key":"10.1186\/1750-1172-6-60-B148","doi-asserted-by":"publisher","DOI":"10.1681\/ASN.2010111145"},{"key":"10.1186\/1750-1172-6-60-B149","doi-asserted-by":"publisher","DOI":"10.1016\/j.blre.2007.10.002"},{"key":"10.1186\/1750-1172-6-60-B151","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2011-02-333997"},{"key":"10.1186\/1750-1172-6-60-B152","doi-asserted-by":"publisher","DOI":"10.1038\/nrneph.2010.98"},{"key":"10.1186\/1750-1172-6-60-B153","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1556-4"},{"key":"10.1186\/1750-1172-6-60-B154","doi-asserted-by":"publisher","DOI":"10.1128\/CMR.00048-09"},{"key":"10.1186\/1750-1172-6-60-B155","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMc0809959"},{"key":"10.1186\/1750-1172-6-60-B157","doi-asserted-by":"publisher","DOI":"10.2215\/CJN.01090209"},{"key":"10.1186\/1750-1172-6-60-B158","doi-asserted-by":"publisher","DOI":"10.1055\/s-0030-1262889"},{"key":"10.1186\/1750-1172-6-60-B159","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1719-3"},{"key":"10.1186\/1750-1172-6-60-B162","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMc0808527"},{"key":"10.1186\/1750-1172-6-60-B163","doi-asserted-by":"publisher","DOI":"10.1016\/j.transproceed.2010.09.125"},{"key":"10.1186\/1750-1172-6-60-B165","doi-asserted-by":"publisher","DOI":"10.1097\/TP.0b013e3181ccd80d"},{"key":"10.1186\/1750-1172-6-60-B166","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1708-6"},{"key":"10.1186\/1750-1172-6-60-B167","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMc1001060"},{"key":"10.1186\/1750-1172-6-60-B168","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-011-1879-9"},{"key":"10.1186\/1750-1172-6-60-B169","doi-asserted-by":"publisher","DOI":"10.2215\/CJN.10181110"},{"key":"10.1186\/1750-1172-6-60-B173","doi-asserted-by":"publisher","DOI":"10.1055\/s-0030-1262888"},{"key":"10.1186\/1750-1172-6-60-B174","doi-asserted-by":"publisher","DOI":"10.1038\/ki.2010.132"},{"key":"10.1186\/1750-1172-6-60-B175","doi-asserted-by":"publisher","DOI":"10.1016\/j.pep.2010.12.002"},{"key":"10.1186\/1750-1172-6-60-B176","doi-asserted-by":"publisher","DOI":"10.1111\/j.1467-7652.2010.00552.x"},{"key":"10.1186\/1750-1172-6-60-B177","doi-asserted-by":"publisher","DOI":"10.1093\/ndt\/gfq319"},{"key":"10.1186\/1750-1172-6-60-B178","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1608-9"}],"container-title":["Orphanet Journal of Rare Diseases"],"original-title":[],"language":"en","deposited":{"date-parts":[[2016,5,16]],"date-time":"2016-05-16T17:12:16Z","timestamp":1463418736000},"score":1,"resource":{"primary":{"URL":"http:\/\/ojrd.biomedcentral.com\/articles\/10.1186\/1750-1172-6-60"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011]]},"references-count":143,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2011]]}},"alternative-id":["1750-1172-6-60"],"URL":"https:\/\/doi.org\/10.1186\/1750-1172-6-60","relation":{},"ISSN":["1750-1172"],"issn-type":[{"value":"1750-1172","type":"print"}],"subject":[],"published":{"date-parts":[[2011]]}}}